Clinical features, genetics, and outcome of pediatric patients with hemophagocytic lymphohistiocytosis in Korea: Report of a nationwide survey from Korea Histiocytosis Working Party

European Journal of Haematology

Volumn 94, Issue 1, 2015, Pages 51-59

  Koh, Kyung Nam ^a   Im, Ho Joon ^a   Chung, Nak Gyun ^b   Cho, Bin ^b   Kang, Hyoung Jin ^c   Shin, Hee Young ^c   Lyu, Chuhl Joo ^d   Yoo, Keon Hee ^e   Koo, Hong Hoe ^e   Kim, Hee Jin ^e   Baek, Hee Jo ^f   Kook, Hoon ^f   Yoon, Hoi Soo ^g   Lim, Young Tak ^h   Kim, Heung Sik ⁱ   Ryu, Kyung Ha ^j   Seo, Jong Jin ^a  

^a University of Ulsan College of Medicine   (South Korea)

^b The Catholic University of Korea College of Medicine   (South Korea)

^c Seoul National University College of Medicine   (South Korea)

^d Yonsei University College of Medicine   (South Korea)

^e Sungkyunkwan University School of Medicine   (South Korea)

^f Chonnam National University Medical School   (South Korea)

^g Kyung Hee University Hospital   (South Korea)

^h Pusan National University School of Medicine   (South Korea)

ⁱ Keimyung University   (South Korea)

^j Ewha Womans University School of Medicine   (South Korea)

more..

Author keywords

Allogeneic hematopoietic stem cell transplantation; Genetic mutation; Hemophagocytic lymphohistiocytosis; Prognostic factors; Survival

Indexed keywords

ALANINE AMINOTRANSFERASE; ASPARTATE AMINOTRANSFERASE; BILIRUBIN; BUSULFAN; FERRITIN; FLUDARABINE; IMMUNOGLOBULIN; LACTATE DEHYDROGENASE; METHYLPREDNISOLONE; PRF1 PROTEIN; PROTEIN; STX11 PROTEIN; SYNTAXIN; THYMOCYTE ANTIBODY; UNC13D PROTEIN; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AGE DISTRIBUTION; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; ANEMIA; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; BLOOD CLOTTING DISORDER; CENTRAL NERVOUS SYSTEM DISEASE; CHILD; CHILDHOOD DISEASE; CHOLESTASIS; CLINICAL FEATURE; CLINICAL GENETICS; COHORT ANALYSIS; CONTROLLED STUDY; CORONAVIRUS INFECTION; DISEASE ASSOCIATION; DISEASE SEVERITY; EPSTEIN BARR VIRUS INFECTION; ESCHERICHIA COLI INFECTION; FEMALE; FRAMESHIFT MUTATION; GENE MUTATION; GENETIC ANALYSIS; GENETIC RISK; GRAFT FAILURE; HEALTH CARE SURVEY; HEMOPHAGOCYTIC SYNDROME; HEPATITIS A; HEPATOSPLENOMEGALY; HERPES SIMPLEX; HERPES ZOSTER; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERBILIRUBINEMIA; HYPERTRANSAMINASEMIA; HYPOALBUMINEMIA; IMMUNOSUPPRESSIVE TREATMENT; IMMUNOTHERAPY; INCIDENCE; INFANT; JUVENILE RHEUMATOID ARTHRITIS; LACTATE DEHYDROGENASE BLOOD LEVEL; LIVER DYSFUNCTION; MAJOR CLINICAL STUDY; MALE; METAPNEUMOVIRUS INFECTION; MUCOCUTANEOUS LYMPH NODE SYNDROME; MYCOPLASMOSIS; MYELOABLATIVE CONDITIONING; NEWBORN; NONSENSE MUTATION; OUTCOME ASSESSMENT; OVERALL SURVIVAL; PARAINFLUENZA VIRUS INFECTION; PARVOVIRUS INFECTION; PNEUMOCOCCAL INFECTION; PRIORITY JOURNAL; PROGNOSIS; PSEUDOMONAS INFECTION; Q FEVER; RECURRENT SPLICING MUTATION; REDUCED INTENSITY CONDITIONING; RESPIRATORY SYNCYTIAL VIRUS INFECTION; RETROSPECTIVE STUDY; RHINOVIRUS INFECTION; RICKETTSIACEAE INFECTION; SALMONELLOSIS; SOUTH KOREA; SPLENOMEGALY; STAPHYLOCOCCUS INFECTION; STREPTOCOCCUS INFECTION; SURVIVAL RATE; SYSTEMIC DISEASE; SYSTEMIC LUPUS ERYTHEMATOSUS; THROMBOCYTOPENIA; TREATMENT RESPONSE; ALLOTRANSPLANTATION; GENETICS; HEALTH SURVEY; HEMATOPOIETIC STEM CELL TRANSPLANTATION; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MUTATION; PRESCHOOL CHILD; REGISTER; RISK FACTOR; TREATMENT OUTCOME;

ADOLESCENT; CHILD; CHILD, PRESCHOOL; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; INFANT; INFANT, NEWBORN; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MALE; MUTATION; PATIENT OUTCOME ASSESSMENT; PROGNOSIS; PUBLIC HEALTH SURVEILLANCE; REGISTRIES; REPUBLIC OF KOREA; RETROSPECTIVE STUDIES; RISK FACTORS; TRANSPLANTATION, HOMOLOGOUS; TREATMENT OUTCOME;

EID: 84938942078     PISSN: 09024441     EISSN: 16000609     Source Type: Journal    
DOI: 10.1111/ejh.12399     Document Type: Article

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