CANDLE Syndrome: A Recently Described Autoinflammatory Syndrome

Journal of Pediatric Hematology/Oncology

Volumn 37, Issue 4, 2015, Pages 296-299

  Tüfekçi, Özlem ^a   Bengoa, Şebnemyilmaz ^a   Karapinar, Tuba Hilkay ^a   Ataseven, Eda Büke ^a   Irken, Gülersu ^a   Ören, Hale ^a  

^a DOKUZ EYLUL UNIVERSITY   (Turkey)

Author keywords

autoimmune hemolytic anemia; CANDLE syndrome; fever; lipodystrophy

Indexed keywords

C REACTIVE PROTEIN; CD123 ANTIGEN; CD163 ANTIGEN; CD20 ANTIGEN; CD3 ANTIGEN; CD68 ANTIGEN; FIBRINOGEN; HEMOGLOBIN; IBUPROFEN; LACTATE DEHYDROGENASE; MYELOPEROXIDASE; PREDNISOLONE; STEM CELL FACTOR; TRYPTASE; LMP7 PROTEIN; PROTEASOME;

ABDOMINAL DISEASE; ACUTE FEBRILE NEUTROPHILIC DERMATOSIS; ANAMNESIS; ARTICLE; AUTOIMMUNE HEMOLYTIC ANEMIA; AUTOINFLAMMATORY DISEASE; AXILLARY LYMPH NODE; BEHCET DISEASE; BLOOD ANALYSIS; BODY HEIGHT; BODY WEIGHT; BONE MARROW BIOPSY; CANDLE SYNDROME; CASE REPORT; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELL INFILTRATION; CHILD; COMPUTER ASSISTED TOMOGRAPHY; COOMBS TEST; CROHN DISEASE; CUTANEOUS MASTOCYTOSIS; DIFFERENTIAL DIAGNOSIS; DRUG DOSE REDUCTION; DRUG RESPONSE; ERYTHEMA; ERYTHROCYTE SEDIMENTATION RATE; EYELID EDEMA; FACE DISORDER; FEVER; FOLLOW UP; HEPATOSPLENOMEGALY; HUMAN; HUMAN CELL; HUMAN TISSUE; HYPERTRANSAMINASEMIA; HYPERTRIGLYCERIDEMIA; INFANT; JOINT CONTRACTURE; LEUKOCYTE COUNT; LIPODYSTROPHY; LYMPH NODE BIOPSY; LYMPHADENOPATHY; LYMPHOCYTE COUNT; MALE; MAST CELL; MASTOCYTOSIS; MICROCEPHALY; MONONUCLEAR CELL; NORMOCHROMIC NORMOCYTIC ANEMIA; PALLOR; PAPULAR SKIN DISEASE; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTUBERANT ABDOMEN; RECURRENT DISEASE; RETICULOCYTE COUNT; RHEUMATOID ARTHRITIS; SKIN BIOPSY; SKIN EDEMA; THROMBOCYTE COUNT; URTICARIA; GENETICS; INFLAMMATION; MUTATION; NEUTROPHIL; SKIN DISEASES; SYNDROME;

CHILD, PRESCHOOL; FEVER; HUMANS; INFLAMMATION; LIPODYSTROPHY; MALE; MUTATION; NEUTROPHILS; PROTEASOME ENDOPEPTIDASE COMPLEX; RECURRENCE; SKIN DISEASES; SYNDROME;

EID: 84937965682     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0000000000000212     Document Type: Article

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