Good Syndrome: An Adult-Onset Immunodeficiency Remarkable for Its High Incidence of Invasive Infections and Autoimmune Complications

Clinical Infectious Diseases

Volumn 61, Issue 2, 2015, Pages e13-e19

  Malphettes, Marion ^a   Gérard, Laurence ^a,b   Galicier, Lionel ^a,b   Boutboul, David ^a   Asli, Bouchra ^a   Szalat, Raphael ^a   Perlat, Antoinette ^c   Masseau, Agathe ^d   Schleinitz, Nicolas ^e   Le Guenno, Guillaume ^f   Viallard, Jean François ^g   Bonnotte, Bernard ^h   Thiercelin Legrand, Marie Françoise ⁱ   Sanhes, Laurence ^j   Borie, Raphael ^k   Georgin Lavialle, Sophie ^l   Fieschi, Claire ^a   Oksenhendler, Eric ^a,b  

^a SAINT LOUIS HOSPITAL   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c SERVICE DE RHUMATOLOGIE   (France)

^d NANTES UNIVERSITY HOSPITAL   (France)

^e HÔPITAL DE LA CONCEPTION   (France)

^f UNIVERSITY HOSPITAL OF CLERMONT FERRAND   (France)

^g HAUT LÉVÊQUE HOSPITAL   (France)

^h HÔPITAL DU BOCAGE   (France)

ⁱ CHU PURPAN   (France)

^j Service d'Hématologie   (France)

^k BICHAT HOSPITAL   (France)

^l HÔPITAL TENON   (France)

more..

Author keywords

autoimmunity; CVID; Good syndrome; infection; thymoma

Indexed keywords

IMMUNOGLOBULIN;

ADULT; AGED; ARTICLE; AUTOIMMUNE DISEASE; AUTOIMMUNITY; B LYMPHOCYTE; BACTEREMIA; BACTERIAL INFECTION; BACTERIAL SINUSITIS; BLOOD SAMPLING; BRONCHITIS; CD4 LYMPHOCYTE COUNT; CLINICAL FEATURE; COMMON VARIABLE IMMUNODEFICIENCY; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE DURATION; FEMALE; GOOD SYNDROME; GRAFT VERSUS HOST REACTION; HISTOPATHOLOGY; HUMAN; IMMUNOGLOBULIN DEFICIENCY; IMMUNOTHERAPY; INCIDENCE; INFECTION; INFECTIOUS COMPLICATION; LICHEN PLANUS; LYMPHOCYTIC COLITIS; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; MULTICENTER STUDY; OPPORTUNISTIC INFECTION; OVERALL SURVIVAL; PRIORITY JOURNAL; PURE RED CELL ANEMIA; STREPTOCOCCUS PNEUMONIA; THYMECTOMY; THYMOMA; AGAMMAGLOBULINEMIA; AGE; BACTERIAL INFECTIONS; COLITIS; COMPLICATION; GRAFT VS HOST DISEASE; IMMUNE DEFICIENCY; IMMUNOLOGY; LICHEN PLANUS, ORAL; MICROBIOLOGY; OPPORTUNISTIC INFECTIONS; RED-CELL APLASIA, PURE; T LYMPHOCYTE;

ADULT; AGAMMAGLOBULINEMIA; AGE FACTORS; AGED; AUTOIMMUNITY; B-LYMPHOCYTES; BACTERIAL INFECTIONS; COLITIS; COMMON VARIABLE IMMUNODEFICIENCY; FEMALE; GRAFT VS HOST DISEASE; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INCIDENCE; LICHEN PLANUS, ORAL; MALE; MIDDLE AGED; OPPORTUNISTIC INFECTIONS; RED-CELL APLASIA, PURE; T-LYMPHOCYTES; THYMOMA;

EID: 84936773247     PISSN: 10584838     EISSN: 15376591     Source Type: Journal    
DOI: 10.1093/cid/civ269     Document Type: Article

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