G6PD deficiency and absence of α-thalassemia increase the risk for cerebral vasculopathy in children with sickle cell anemia

European Journal of Haematology

Volumn 96, Issue 4, 2016, Pages 404-408

  Joly, Philippe ^a,b   Garnier, Nathalie ^c   Kebaili, Kamila ^c   Renoux, Céline ^a,b   Dony, Arthur ^c   Cheikh, Nathalie ^c   Renard, Cécile ^c   Ceraulo, Antony ^c   Cuzzubbo, Daniela ^c   Pondarré, Corinne ^c,d   Martin, Cyril ^b   Pialoux, Vincent ^b,e   Francina, Alain ^a   Bertrand, Yves ^c   Connes, Philippe ^b,e  

^a EDOUARD HERRIOT HOSPITAL   (France)

^b UNIVERSITÉ LYON 1   (France)

^c HOSPICES CIVILS DE LYON   (France)

^d CENTRE HOSPITALIER INTERCOMMUNAL DE CRÉTEIL   (France)

^e INSTITUT UNIVERSITAIRE DE FRANCE   (France)

Author keywords

Hemolysis; Sickle cell disease; Stroke; Vasculopathy

Indexed keywords

HEMOGLOBIN;

ALPHA THALASSEMIA; ARTICLE; BRAIN INFARCTION; CEREBROVASCULAR ACCIDENT; CEREBROVASCULAR DISEASE; CHILD; CONTROLLED STUDY; DISEASE ASSOCIATION; DOPPLER ECHOGRAPHY; FEMALE; FOLLOW UP; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY; HAPLOTYPE; HEMATOLOGICAL PARAMETERS; HUMAN; HUMAN CELL; LONG TERM CARE; MAJOR CLINICAL STUDY; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RETICULOCYTE; RISK; SICKLE CELL ANEMIA; STEADY STATE; TRANSCRANIAL DOPPLER; ALPHA-THALASSEMIA; ANEMIA, SICKLE CELL; BLOOD; CEREBROVASCULAR DISORDERS; COMPLICATION; GLUCOSEPHOSPHATE DEHYDROGENASE DEFICIENCY; METABOLISM; PATHOLOGY; PRESCHOOL CHILD; RETICULOCYTE COUNT; RISK FACTOR; TRANSCRANIAL DOPPLER ULTRASONOGRAPHY;

ALPHA-THALASSEMIA; ANEMIA, SICKLE CELL; CEREBROVASCULAR DISORDERS; CHILD; CHILD, PRESCHOOL; FEMALE; GLUCOSEPHOSPHATE DEHYDROGENASE DEFICIENCY; HEMOGLOBINS; HUMANS; MALE; RETICULOCYTE COUNT; RETICULOCYTES; RISK FACTORS; ULTRASONOGRAPHY, DOPPLER, TRANSCRANIAL;

EID: 84934782986     PISSN: 09024441     EISSN: 16000609     Source Type: Journal    
DOI: 10.1111/ejh.12607     Document Type: Article

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