Characterization of mortality in children with sickle cell disease diagnosed through the Newborn Screening Program

Jornal de Pediatria

Volumn 91, Issue 3, 2015, Pages 242-247

  Sabarense, Alessandra P ^a   Lima, Gabriella O ^a   Silva, Lívia M L ^a   Viana, Marcos Borato ^a  

^a FEDERAL UNIVERSITY OF MINAS GERAIS   (Brazil)

Author keywords

Acute splenic sequestration; Death rate; Infection; Neonatal screening; Sickle cell anemia

Indexed keywords

ARTICLE; BETA THALASSEMIA; CHILD; CHILD DEATH; CHILDHOOD MORTALITY; DEATH CERTIFICATE; EPIDEMIOLOGICAL DATA; FAMILY; FEMALE; HUMAN; INCOME; INFECTION; INTERVIEW; MAJOR CLINICAL STUDY; MALE; MEDICAL CARE; MEDICAL RECORD; NEWBORN SCREENING; SICKLE CELL ANEMIA; BRAZIL; CAUSE OF DEATH; COMPARATIVE STUDY; EDUCATION; EDUCATIONAL STATUS; EPIDEMIOLOGY; HEALTH SURVEY; INFANT; MORTALITY; NEWBORN; PARENT; POVERTY; PRESCHOOL CHILD; SPLEEN DISEASE; THALASSEMIA;

ANEMIA, SICKLE CELL; BRAZIL; CAUSE OF DEATH; CHILD; CHILD, PRESCHOOL; DEATH CERTIFICATES; EDUCATIONAL STATUS; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; INFECTION; MALE; NEONATAL SCREENING; PARENTS; POPULATION SURVEILLANCE; POVERTY; SPLENIC DISEASES; THALASSEMIA;

EID: 84930470030     PISSN: 00217557     EISSN: 16784782     Source Type: Journal    
DOI: 10.1016/j.jped.2014.08.006     Document Type: Article

References (30)

1. C.L. Lobo, S.K. Ballas, A.C. Domingos, P.G. Moura, E.M. do Nascimento, and G.P. Cardoso Newborn screening program for hemoglobinopathies in Rio de Janeiro Brazil. Pediatr Blood Cancer. 61 2014 34 39
2. S.A. Pereira, S. Brener, C.S. Cardoso, and A.B. Proietti Sickle cell disease: quality of life in patients with hemoglobin SS and SC disorders Rev Bras Hematol Hemoter. 35 2013 325 331
3. A.A. Felix, H.M. Souza, and S.B. Ribeiro Aspectos epidemiológicos e sociais da doença falciforme Rev Bras Hematol Hemoter. 32 2010 203 208
4. C.T. Quinn Sickle cell disease in childhood: from newborn screening through transition to adult medical care Pediatr Clin North Am. 60 2013 1363 1381
5. G.R. Serjeant The natural history of sickle cell disease Cold Spring Harb Perspect Med. 3 2013 a011783
6. J. Hankins Toward high quality medical care for sickle cell disease: are we there yet? J Pediatr (Rio J). 86 2010 256 258
7. P.T. McGann Sickle cell anemia: an underappreciated and unaddressed contributor to global childhood mortality J Pediatr. 165 2014 18 22
8. D. Hamideh, and O. Alvarez Sickle cell disease related mortality in the United States (1999-2009) Pediatr Blood Cancer. 60 2013 1482 1486
9. R.D. Cançado, and J.A. Jesus A doença falciforme no Brasil Rev Bras Hematol Hemoter. 29 2007 204 206
10. A.P. Fernandes, J.N. Januário, C.B. Cangussu, D.L. Macedo, and M.B. Viana Mortality of children with sickle cell disease: a population study J Pediatr (Rio J). 86 2010 279 284
11. S.L. Leikin, D. Gallagher, T.R. Kinney, D. Sloane, P. Klug, and W. Rida Mortality in children and adolescents with sickle cell disease. Cooperative Study of Sickle Cell Disease Pediatrics. 84 1989 500 508
12. S.M. Shankar, P.G. Arbogast, E. Mitchel, W.O. Cooper, W.C. Wang, and M.R. Griffin Medical care utilization and mortality in sickle cell disease: a population-based study Am J Hematol. 80 2005 262 270
13. D.W. Rogers, J.M. Clarke, L. Cupidore, A.M. Ramlal, B.R. Sparke, and G.R. Serjeant Early deaths in Jamaican children with sickle cell disease Br Med J. 1 1978 1515 1516
14. F.M. Gill, L.A. Sleeper, S.J. Weiner, A.K. Brown, R. Bellevue, and R. Grover Clinical events in the first decade in a cohort of infants with sickle cell disease. Cooperative Study of Sickle Cell Disease Blood. 86 1995 776 783
15. E.A. Manci, D.E. Culberson, Y.M. Yang, T.M. Gardner, R. Powell, and J. Haynes Jr. Causes of death in sickle cell disease: an autopsy study Br J Haematol. 123 2003 359 365
16. C.T. Quinn, Z.R. Rogers, and G.R. Buchanan Survival of children with sickle cell disease Blood. 103 2004 4023 4027
17. P. Houston-Yu, S.R. Rana, B. Beyer, and O. Castro Frequent and prolonged hospitalizations: a risk factor for early mortality in sickle cell disease patients Am J Hematol. 72 2003 201 203
18. R.A. Seeler Deaths in children with sickle cell anemia. A clinical analysis of 19 fatal instances in Chicago Clin Pediatr (Phila). 11 1972 634 637
19. A.N. Thomas, C. Pattison, and G.R. Serjeant Causes of death in sickle-cell disease in Jamaica Br Med J (Clin Res Ed). 285 1982 633 635
20. O.S. Platt, D.J. Brambilla, W.F. Rosse, P.F. Milner, O. Castro, and M.H. Steinberg Mortality in sickle cell disease. Life expectancy and risk factors for early death N Engl J Med. 330 1994 1639 1644
21. J. Koko, D. Dufillot, J. M'Ba-Meyo, D. Gahouma, and F. Kani Mortality of children with sickle cell disease in a pediatric department in Central Africa Arch Pediatr. 5 1998 965 969
22. J. Makani, S.E. Cox, D. Soka, A.N. Komba, J. Oruo, and H. Mwamtemi Mortality in sickle cell anemia in Africa: a prospective cohort study in Tanzania PLoS One. 6 2011 e14699
23. M.M. Loureiro Epidemiologia das internações hospitalares e tratamento farmacológico dos eventos agudos em doenças falciformes [thesis] 2006 Escola Nacional de Saúde Pública, Fundação Oswaldo Cruz Rio de Janeiro
24. E. Yanni, S.D. Grosse, Q. Yang, and R.S. Olney Trends in pediatric sickle cell disease-related mortality in the United States, 1983-2002 J Pediatr. 154 2009 541 545
25. J.C. Van-Dunem, J.G. Alves, L. Bernardino, J.N. Figueiroa, C. Braga, M. do Nascimento, and L. de Factors associated with sickle cell disease mortality among hospitalized Angolan children and adolescents West Afr J Med. 26 2007 269 273
26. F.M. Gill, A. Brown, D. Gallagher, S. Diamond, E. Goins, and R. Grover Newborn experience in the Cooperative Study of Sickle Cell Disease Pediatrics. 83 1989 827 829
27. S.T. Miller, L.A. Sleeper, C.H. Pegelow, L.E. Enos, W.C. Wang, and S.J. Weiner Prediction of adverse outcomes in children with sickle cell disease N Engl J Med. 342 2000 83 89
28. A.L. Alves Estudo da mortalidade por anemia falciforme Informe Epidemiológico do SUS. 5 1996 45 53
29. P.V. Rezende, M.B. Viana, M. Murao, A.C. Chaves, and A.C. Ribeiro Acute splenic sequestration in a cohort of children with sickle cell anemia J Pediatr (Rio J). 85 2009 163 169
30. E.L. Bitarães, B.M. Oliveira, and M.B. Viana Compliance with antibiotic prophylaxis in children with sickle cell anemia: a prospective study J Pediatr (Rio J). 84 2008 316 322