Sickle cell disease in Brazil;A doença falciforme no Brasil

Revista Brasileira de Hematologia e Hemoterapia

Volumn 29, Issue 3, 2007, Pages 204-206

  Cançado, Rodolfo Delfini ^a,b,c   Jesus, Joice A ^b  

^a UNIVERSITY OF SÃO PAULO   (Brazil)

^b MINISTÉRIO DA SAÚDE   (Brazil)

^c Hemocentro da Santa Casa   (Brazil)

Author keywords

[No Author keywords available]

Indexed keywords

EID: 38049158354     PISSN: 15168484     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Editorial

References (9)

1. Portaria no 1.391/GM de 16 de Agosto de 2005. Art. 1° Instituir, no âmbito do Sistema Único de Saúde - SUS, como diretrizes para a Política Nacional de Atenção Integral às Pessoas com Doença Falciforme e outras Hemoglobinopatias. http://dtr2001.saude. gov.br/sas/gab05/gabago05.htm
2. Zago MA. Considerações gerais sobre as doenças falciformes. In: Manual de Diagnóstico e Tratamento das Doenças Falciformes (Agência Nacional de Vigilância Sanitária, org.), 2002; pp. 9-11, Brasília: Ministério da Saúde.
3. Steinberg MH, Barton F, Castro O et al. Effect of hydroxyurea on mortality and morbidity in adult sickle cell anemia: risks and benefits up to 9 years of treatment. JAMA. 2003;289:1645.
4. Adams RJ, McKie VC, Hsu L, Files B, Vichinsky E, Pegelow C et al. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med. 1998;339(1):5-11
5. Adams RJ, Brambilla D. Optimizing primary stroke prevention in Sickle Cell Anemia (STOP 2) Trial Investigators. Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease. N Engl J Med. 2005;353(26):2769-78.
6. Styles LA, Vichinsky E. Effects of a long-term transfusion regimen on sickle cell-related illnesses. J Pediatr. 1994;125(6):909-11.
7. Miller ST, Wright E, Abboud M, Berman B, Files B, Scher CD et al. STOP Investigators. Impact of chronic transfusion on incidence of pain and acute chest syndrome during the Stroke Prevention Trial (STOP) in sickle-cell anemia. J Pediatr. 2001;139(6):785-9.
8. Harmatz P, Butensky E, Quirolo K, Williams R, Ferrell L, Moyer T et al. Severity of iron overload in patients with sickle cell disease receiving chronic red blood cell transfusion therapy. Blood. 2000; 96(1):76-9.
9. Ballas SK. Iron overload is a determinant of morbidity and mortality in adult patients with sickle cell disease. Semin Hematol 2001; 38(Suppl 1):30-6.