-
1
-
-
0141706635
-
American Thoracic Society/European Respiratory Society Statement: Standards for the diagnosis and management of individuals with alpha1-antitrypsin deficiency
-
American Thoracic Society/European Respiratory Society Statement: Standards for the diagnosis and management of individuals with alpha1-antitrypsin deficiency. Am J Respir Crit Care Med 2003, 168:818-900.
-
(2003)
Am J Respir Crit Care Med
, vol.168
, pp. 818-900
-
-
-
3
-
-
33846346558
-
Normativa SEPAR: diagnóstico y tratamiento del déficit de alfa-1-antitripsina
-
Comité del Registro Nacional de Pacientes con Déficit de Alfa-1-Antitripsina
-
Vidal R., Blanco I., Casas F., Jardí R., Miravitlles M. Normativa SEPAR: diagnóstico y tratamiento del déficit de alfa-1-antitripsina. Arch Bronconeumol 2006, 42:645-659. Comité del Registro Nacional de Pacientes con Déficit de Alfa-1-Antitripsina.
-
(2006)
Arch Bronconeumol
, vol.42
, pp. 645-659
-
-
Vidal, R.1
Blanco, I.2
Casas, F.3
Jardí, R.4
Miravitlles, M.5
-
4
-
-
67649407825
-
Exploring the role of CT densitometry: A randomised study of augmentation therapy in alpha1-antitrypsin deficiency
-
Dirksen A., Piitulainen E., Parr D.G., Deng C., Wencker M., Shaker S.B., et al. Exploring the role of CT densitometry: A randomised study of augmentation therapy in alpha1-antitrypsin deficiency. Eur Respir J 2009, 33:1345-1353.
-
(2009)
Eur Respir J
, vol.33
, pp. 1345-1353
-
-
Dirksen, A.1
Piitulainen, E.2
Parr, D.G.3
Deng, C.4
Wencker, M.5
Shaker, S.B.6
-
5
-
-
77957273246
-
Therapeutic efficacy of -1 antitrypsin augmentation therapy on the loss of lung tissue: An integrated analysis of 2 randomised clinical trials using computed tomography densitometry
-
Stockley R.A., Parr D.G., Piitulainen E., Stolk J., Stoel B.C., Dirksen A. Therapeutic efficacy of -1 antitrypsin augmentation therapy on the loss of lung tissue: An integrated analysis of 2 randomised clinical trials using computed tomography densitometry. Respir Res 2010, 11:136-144.
-
(2010)
Respir Res
, vol.11
, pp. 136-144
-
-
Stockley, R.A.1
Parr, D.G.2
Piitulainen, E.3
Stolk, J.4
Stoel, B.C.5
Dirksen, A.6
-
6
-
-
37149030877
-
Prevalence and impact of bronchiectasis in alpha1-antitrypsin deficiency
-
Parr D.G., Guest P.G., Reynolds J.H., Dowson L.J., Stockley R.A. Prevalence and impact of bronchiectasis in alpha1-antitrypsin deficiency. Am J Respir Crit Care Med 2007, 176:1215-1221.
-
(2007)
Am J Respir Crit Care Med
, vol.176
, pp. 1215-1221
-
-
Parr, D.G.1
Guest, P.G.2
Reynolds, J.H.3
Dowson, L.J.4
Stockley, R.A.5
-
7
-
-
35448959593
-
Prevalence of alpha-1 antitrypsin deficiency in poorly controlled asthma -results from the ALA-ACRC low-dose theophylline trial
-
Eden E., Holbrook J.T., Brantly M.L., Turino G.M., Wise R.A. Prevalence of alpha-1 antitrypsin deficiency in poorly controlled asthma -results from the ALA-ACRC low-dose theophylline trial. J Asthma 2007, 44:605-608.
-
(2007)
J Asthma
, vol.44
, pp. 605-608
-
-
Eden, E.1
Holbrook, J.T.2
Brantly, M.L.3
Turino, G.M.4
Wise, R.A.5
-
8
-
-
84856545731
-
Low agreement of visual rating for detailed quantification of pulmonary emphysema in whole-lung CT
-
Mascalchi M., Diciotti S., Sverzellati N., Camiciottoli G., Ciccotosto C., Falaschi F., et al. Low agreement of visual rating for detailed quantification of pulmonary emphysema in whole-lung CT. Acta Radiol 2012, 53:53-60.
-
(2012)
Acta Radiol
, vol.53
, pp. 53-60
-
-
Mascalchi, M.1
Diciotti, S.2
Sverzellati, N.3
Camiciottoli, G.4
Ciccotosto, C.5
Falaschi, F.6
-
9
-
-
42149188192
-
Screening and familial testing of patients for alpha 1-antitrypsin deficiency
-
Hogarth D.K., Rachelefsky G. Screening and familial testing of patients for alpha 1-antitrypsin deficiency. Chest 2008, 133:981-988.
-
(2008)
Chest
, vol.133
, pp. 981-988
-
-
Hogarth, D.K.1
Rachelefsky, G.2
-
10
-
-
77955487511
-
Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease
-
Gøtzsche P.C., Johansen H.K. Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease. Cochrane Database Syst Rev 2010, CD007851. (7).
-
(2010)
Cochrane Database Syst Rev
, Issue.7
, pp. CD007851
-
-
Gøtzsche, P.C.1
Johansen, H.K.2
-
11
-
-
77957659757
-
Intravenous alpha-1 antitrypsin augmentation therapy: Systematic review
-
Gøtzsche P.C., Johansen H.K. Intravenous alpha-1 antitrypsin augmentation therapy: Systematic review. Dan Med Bull 2010, 57:A4175.
-
(2010)
Dan Med Bull
, vol.57
, pp. A4175
-
-
Gøtzsche, P.C.1
Johansen, H.K.2
-
12
-
-
70350450961
-
Augmentation therapy for alpha1 antitrypsin deficiency: A meta-analysis
-
Chapman K.R., Stockley R.A., Dawkins C., Wilkes M.M., Navickis R.J. Augmentation therapy for alpha1 antitrypsin deficiency: A meta-analysis. COPD 2009, 6:177-184.
-
(2009)
COPD
, vol.6
, pp. 177-184
-
-
Chapman, K.R.1
Stockley, R.A.2
Dawkins, C.3
Wilkes, M.M.4
Navickis, R.J.5
-
13
-
-
84861316814
-
Alpha-1 antitrypsin deficiency targeted testing and augmentation therapy: A Canadian Thoracic Society clinical practice guideline
-
Canadian Thoracic Society COPD Clinical Assembly Alpha-1 Antitrypsin Deficiency Expert Working Group
-
Marciniuk D.D., Hernandez P., Balter M., Bourbeau J., Chapman K.R., Ford G.T., et al. Alpha-1 antitrypsin deficiency targeted testing and augmentation therapy: A Canadian Thoracic Society clinical practice guideline. Can Respir J 2012, 19:109-116. Canadian Thoracic Society COPD Clinical Assembly Alpha-1 Antitrypsin Deficiency Expert Working Group.
-
(2012)
Can Respir J
, vol.19
, pp. 109-116
-
-
Marciniuk, D.D.1
Hernandez, P.2
Balter, M.3
Bourbeau, J.4
Chapman, K.R.5
Ford, G.T.6
-
14
-
-
0019787989
-
Replacement therapy of alpha 1-antitrypsin deficiency. Reversal of protease-antiprotease imbalance within the alveolar structures of PiZ subjects
-
Gadek J.E., Klein H.G., Holland P.V., Crystal R.G. Replacement therapy of alpha 1-antitrypsin deficiency. Reversal of protease-antiprotease imbalance within the alveolar structures of PiZ subjects. J Clin Invest 1981, 68:1158-1165.
-
(1981)
J Clin Invest
, vol.68
, pp. 1158-1165
-
-
Gadek, J.E.1
Klein, H.G.2
Holland, P.V.3
Crystal, R.G.4
-
15
-
-
84944363276
-
From the NIH: Intravenous replacement therapy for patients with severe alpha 1-antitrypsin deficiency
-
From the NIH: Intravenous replacement therapy for patients with severe alpha 1-antitrypsin deficiency. JAMA. 1982, 248:1693.
-
(1982)
JAMA.
, vol.248
, pp. 1693
-
-
-
16
-
-
0020680610
-
Experience with replacement therapy in the destructive lung disease associated with severe alpha-1-antitrypsin deficiency
-
Gadek J.E., Crystal R.G. Experience with replacement therapy in the destructive lung disease associated with severe alpha-1-antitrypsin deficiency. Am Rev Respir Dis 1983, 127:S45-S46.
-
(1983)
Am Rev Respir Dis
, vol.127
, pp. S45-S46
-
-
Gadek, J.E.1
Crystal, R.G.2
-
17
-
-
0020663341
-
Alpha 1 antitrypsin deficiency: clinical and physiological features in heterozygotes of Pi type SZ. A survey by the British Thoracic Association
-
Hutchison D.C., Tobin M.J., Cook P.J. Alpha 1 antitrypsin deficiency: clinical and physiological features in heterozygotes of Pi type SZ. A survey by the British Thoracic Association. Br J Dis Chest 1983, 77:28-34.
-
(1983)
Br J Dis Chest
, vol.77
, pp. 28-34
-
-
Hutchison, D.C.1
Tobin, M.J.2
Cook, P.J.3
-
18
-
-
0023148995
-
Replacement therapy for alpha 1-antitrypsin deficiency associated with emphysema
-
Wewers M.D., Casolaro M.A., Sellers S.E., Swayze S.C., McPhaul K.M., Wittes J.T., et al. Replacement therapy for alpha 1-antitrypsin deficiency associated with emphysema. N Engl J Med 1987, 316:1055-1062.
-
(1987)
N Engl J Med
, vol.316
, pp. 1055-1062
-
-
Wewers, M.D.1
Casolaro, M.A.2
Sellers, S.E.3
Swayze, S.C.4
McPhaul, K.M.5
Wittes, J.T.6
-
19
-
-
0023784904
-
Biochemical efficacy and safety of monthly augmentation therapy for alpha 1-antitrypsin deficiency
-
Hubbard R.C., Sellers S., Czerski D., Stephens L., Crystal R.G. Biochemical efficacy and safety of monthly augmentation therapy for alpha 1-antitrypsin deficiency. JAMA 1988, 260:1259-1264.
-
(1988)
JAMA
, vol.260
, pp. 1259-1264
-
-
Hubbard, R.C.1
Sellers, S.2
Czerski, D.3
Stephens, L.4
Crystal, R.G.5
-
20
-
-
0023925114
-
Replacement therapy for alpha-1-protease inhibitor deficiency in PiZ subjects with chronic obstructive lung disease
-
Schmidt E.W., Rasche B., Ulmer W.T., Konietzko N., Becker M., Fallise J.P., et al. Replacement therapy for alpha-1-protease inhibitor deficiency in PiZ subjects with chronic obstructive lung disease. Am J Med 1988, 84:63-69.
-
(1988)
Am J Med
, vol.84
, pp. 63-69
-
-
Schmidt, E.W.1
Rasche, B.2
Ulmer, W.T.3
Konietzko, N.4
Becker, M.5
Fallise, J.P.6
-
21
-
-
0024477218
-
Replacement therapy in alpha 1-antitrypsin deficiency
-
Eriksson S. Replacement therapy in alpha 1-antitrypsin deficiency. J Intern Med 1989, 225:69-72.
-
(1989)
J Intern Med
, vol.225
, pp. 69-72
-
-
Eriksson, S.1
-
22
-
-
0025241020
-
Aspects of treatment in alpha 1-antitrypsin deficiency: Insights derived from a Swedish PiZZ series
-
Eriksson S., Wu M.C. Aspects of treatment in alpha 1-antitrypsin deficiency: Insights derived from a Swedish PiZZ series. Eur Respir J Suppl 1990, 9:39s-43s.
-
(1990)
Eur Respir J Suppl
, vol.9
, pp. 39s-43s
-
-
Eriksson, S.1
Wu, M.C.2
-
23
-
-
0026420242
-
Replacement therapy of emphysema caused by alpha 1-antitrypsin deficiency
-
Vidal R., Miravitlles M., de Gracia X., Gallego B., Morell F. Replacement therapy of emphysema caused by alpha 1-antitrypsin deficiency. Med Clin (Barc) 1991, 96:180-182.
-
(1991)
Med Clin (Barc)
, vol.96
, pp. 180-182
-
-
Vidal, R.1
Miravitlles, M.2
de Gracia, X.3
Gallego, B.4
Morell, F.5
-
24
-
-
0025890293
-
Cost-effectiveness of alpha-1 antitrypsin replacement therapy in treatment of congenital chronic obstructive pulmonary disease
-
Hay J.W., Robin E.D. Cost-effectiveness of alpha-1 antitrypsin replacement therapy in treatment of congenital chronic obstructive pulmonary disease. Am J Public Health 1991, 81:427-433.
-
(1991)
Am J Public Health
, vol.81
, pp. 427-433
-
-
Hay, J.W.1
Robin, E.D.2
-
25
-
-
0026926198
-
Alpha 1-antitrypsin-deficiency-related emphysema
-
Barker A.F. Alpha 1-antitrypsin-deficiency-related emphysema. J Am Board Fam Pract 1992, 5:489-493.
-
(1992)
J Am Board Fam Pract
, vol.5
, pp. 489-493
-
-
Barker, A.F.1
-
26
-
-
0026510873
-
Current status of alpha-1-antitrypsin replacement therapy: Recommendations for the management of patients with severe hereditary deficiency. Ad Hoc Committee on Alpha-1-Antitrypsin Replacement Therapy of the Standards Committee, Canadian Thoracic Society
-
Ad Hoc Committee on alpha-1 antitrypsin replacement therapy of the Standards Committee, Canadian Thoracic Society
-
Current status of alpha-1-antitrypsin replacement therapy: Recommendations for the management of patients with severe hereditary deficiency. Ad Hoc Committee on Alpha-1-Antitrypsin Replacement Therapy of the Standards Committee, Canadian Thoracic Society. CMAJ 1992, 146:841-844. Ad Hoc Committee on alpha-1 antitrypsin replacement therapy of the Standards Committee, Canadian Thoracic Society.
-
(1992)
CMAJ
, vol.146
, pp. 841-844
-
-
-
27
-
-
0026939035
-
Alpha-1-antitrypsin replacement therapy -an early Australian experience
-
Burdon J., Cook L., Holmes P., Janus E., Watts S. Alpha-1-antitrypsin replacement therapy -an early Australian experience. Aust N Z J Med 1992, 22:498-499.
-
(1992)
Aust N Z J Med
, vol.22
, pp. 498-499
-
-
Burdon, J.1
Cook, L.2
Holmes, P.3
Janus, E.4
Watts, S.5
-
28
-
-
0028070026
-
Failure to achieve adequate serum levels with monthly replacement therapy in alpha 1-antitrypsin deficiency
-
Cammarata S.K., Stone C.L., Carey J.L., Eichenhorn M.S. Failure to achieve adequate serum levels with monthly replacement therapy in alpha 1-antitrypsin deficiency. Chest 1994, 106:651-652.
-
(1994)
Chest
, vol.106
, pp. 651-652
-
-
Cammarata, S.K.1
Stone, C.L.2
Carey, J.L.3
Eichenhorn, M.S.4
-
29
-
-
0028603327
-
Evaluation of replacement therapy in emphysema caused by alpha 1-antitrypsin deficiency
-
Miravitlles M., Vidal R., Torrella M., Bofill J.M., Cotrina M., de Gracia J. Evaluation of replacement therapy in emphysema caused by alpha 1-antitrypsin deficiency. Arch Bronconeumol 1994, 30:479-484.
-
(1994)
Arch Bronconeumol
, vol.30
, pp. 479-484
-
-
Miravitlles, M.1
Vidal, R.2
Torrella, M.3
Bofill, J.M.4
Cotrina, M.5
de Gracia, J.6
-
30
-
-
0029155644
-
Clinical trials needed for alpha 1-antitrypsin replacement therapy
-
Bhagat R., Swystun V.A., Cockcroft D.W. Clinical trials needed for alpha 1-antitrypsin replacement therapy. Chest 1995, 108:586-587.
-
(1995)
Chest
, vol.108
, pp. 586-587
-
-
Bhagat, R.1
Swystun, V.A.2
Cockcroft, D.W.3
-
31
-
-
0029349461
-
The evolution of the replacement treatment of emphysema due to alpha 1-antitrypsin deficiency
-
Manresa F. The evolution of the replacement treatment of emphysema due to alpha 1-antitrypsin deficiency. Arch Bronconeumol 1995, 31:371-372.
-
(1995)
Arch Bronconeumol
, vol.31
, pp. 371-372
-
-
Manresa, F.1
-
32
-
-
0030466338
-
Pathogenesis of hereditary emphysema and replacement therapy for alpha 1-antitrypsin deficiency. Insight into the more common forms of emphysema
-
Gadek J.E., Pacht E.R. Pathogenesis of hereditary emphysema and replacement therapy for alpha 1-antitrypsin deficiency. Insight into the more common forms of emphysema. Chest 1996, 110:248s-250s.
-
(1996)
Chest
, vol.110
, pp. 248s-250s
-
-
Gadek, J.E.1
Pacht, E.R.2
-
33
-
-
0029963017
-
Alpha 1-antitrypsin deficiency: evaluation of bronchiectasis with CT
-
King M.A., Stone J.A., Diaz P.T., Mueller C.F., Becker W.J., Gadek J.E. Alpha 1-antitrypsin deficiency: evaluation of bronchiectasis with CT. Radiology 1996, 199:137-141.
-
(1996)
Radiology
, vol.199
, pp. 137-141
-
-
King, M.A.1
Stone, J.A.2
Diaz, P.T.3
Mueller, C.F.4
Becker, W.J.5
Gadek, J.E.6
-
34
-
-
0030446288
-
Clinical features of individuals with PI*SZ phenotype of alpha 1-antitrypsin deficiency
-
Alpha 1-Antitrypsin Deficiency Registry Study Group
-
Turino G.M., Barker A.F., Brantly M.L., Cohen A.B., Connelly R.P., Crystal R.G., et al. Clinical features of individuals with PI*SZ phenotype of alpha 1-antitrypsin deficiency. Am J Respir Crit Care Med 1996, 154:1718-1725. Alpha 1-Antitrypsin Deficiency Registry Study Group.
-
(1996)
Am J Respir Crit Care Med
, vol.154
, pp. 1718-1725
-
-
Turino, G.M.1
Barker, A.F.2
Brantly, M.L.3
Cohen, A.B.4
Connelly, R.P.5
Crystal, R.G.6
-
35
-
-
2642680855
-
Alpha 1-antitrypsin deficiency: Memorandum from a WHO meeting
-
Alpha 1-antitrypsin deficiency: Memorandum from a WHO meeting. Bull World Health Organ 1997, 75:397-415.
-
(1997)
Bull World Health Organ
, vol.75
, pp. 397-415
-
-
-
36
-
-
0030663669
-
Alpha-1-antitrypsin replacement therapy: Will its efficacy ever be proved
-
Hutchison D.C., Hughes M.D. Alpha-1-antitrypsin replacement therapy: Will its efficacy ever be proved. Eur Respir J 1997, 10:2191-2193.
-
(1997)
Eur Respir J
, vol.10
, pp. 2191-2193
-
-
Hutchison, D.C.1
Hughes, M.D.2
-
37
-
-
0031242842
-
Does alpha1-antitrypsin augmentation therapy slow the annual decline in FEV1 in patients with severe hereditary alpha1-antitrypsin deficiency? Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen (WATL) alpha1-AT study group
-
Seersholm N., Wencker M., Banik N., Viskum K., Dirksen A., Kok-Jensen A., et al. Does alpha1-antitrypsin augmentation therapy slow the annual decline in FEV1 in patients with severe hereditary alpha1-antitrypsin deficiency? Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen (WATL) alpha1-AT study group. Eur Respir J 1997, 10:2260-2263.
-
(1997)
Eur Respir J
, vol.10
, pp. 2260-2263
-
-
Seersholm, N.1
Wencker, M.2
Banik, N.3
Viskum, K.4
Dirksen, A.5
Kok-Jensen, A.6
-
38
-
-
0032013907
-
¿ Deberíamos administrar tratamiento sustitutivo a los pacientes con déficit de alfa-1 antitripsina?
-
Miravitlles M. ¿ Deberíamos administrar tratamiento sustitutivo a los pacientes con déficit de alfa-1 antitripsina?. Arch Bronconeumol 1998, 34:109-111.
-
(1998)
Arch Bronconeumol
, vol.34
, pp. 109-111
-
-
Miravitlles, M.1
-
39
-
-
0031756969
-
Usefulness of a national registry of alpha-1-antitrypsin deficiency. The Spanish experience
-
Miravitlles M., Vidal R., Barros-Tizón J.C., Bustamante A., España P.P., Casas F., et al. Usefulness of a national registry of alpha-1-antitrypsin deficiency. The Spanish experience. Respir Med 1998, 92:1181-1187.
-
(1998)
Respir Med
, vol.92
, pp. 1181-1187
-
-
Miravitlles, M.1
Vidal, R.2
Barros-Tizón, J.C.3
Bustamante, A.4
España, P.P.5
Casas, F.6
-
40
-
-
0032110436
-
Survival and FEV1 decline in individuals with severe deficiency of alpha1-antitrypsin
-
The Alpha-1-Antitrypsin Deficiency Registry Study Group
-
Survival and FEV1 decline in individuals with severe deficiency of alpha1-antitrypsin. Am J Respir Crit Care Med 1998, 158:49-59. The Alpha-1-Antitrypsin Deficiency Registry Study Group.
-
(1998)
Am J Respir Crit Care Med
, vol.158
, pp. 49-59
-
-
-
41
-
-
0031884479
-
Long-term treatment of alpha1-antitrypsin deficiency-related pulmonary emphysema with human alpha1-antitrypsin. Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen(WATL)-alpha1-AT-study group
-
Wencker M., Banik N., Buhl R., Seidel R., Konietzko N. Long-term treatment of alpha1-antitrypsin deficiency-related pulmonary emphysema with human alpha1-antitrypsin. Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen(WATL)-alpha1-AT-study group. Eur Respir J 1998, 11:428-433.
-
(1998)
Eur Respir J
, vol.11
, pp. 428-433
-
-
Wencker, M.1
Banik, N.2
Buhl, R.3
Seidel, R.4
Konietzko, N.5
-
42
-
-
84880726176
-
Alpha-1 antitrypsin augmentation therapy and biomarkers of elastin degradation
-
Ma S., Lin Y.Y., He J., Rouhani F.N., Brantly M., Turino G.M. Alpha-1 antitrypsin augmentation therapy and biomarkers of elastin degradation. COPD 2013, 10:473-481.
-
(2013)
COPD
, vol.10
, pp. 473-481
-
-
Ma, S.1
Lin, Y.Y.2
He, J.3
Rouhani, F.N.4
Brantly, M.5
Turino, G.M.6
-
43
-
-
0038166283
-
Alpha 1-protease inhibitor deficiency. Diagnosis, follow-up and therapy options
-
Köhnlein T., Klein H., Welte T. Alpha 1-protease inhibitor deficiency. Diagnosis, follow-up and therapy options. Med Klin (Munich) 1999, 94:371-376.
-
(1999)
Med Klin (Munich)
, vol.94
, pp. 371-376
-
-
Köhnlein, T.1
Klein, H.2
Welte, T.3
-
44
-
-
0033796561
-
Formation and current results of a patient-organized registry for alpha(1)-antitrypsin deficiency
-
Stoller J.K., Brantly M., Fleming L.E., Bean J.A., Walsh J. Formation and current results of a patient-organized registry for alpha(1)-antitrypsin deficiency. Chest 2000, 118:843-848.
-
(2000)
Chest
, vol.118
, pp. 843-848
-
-
Stoller, J.K.1
Brantly, M.2
Fleming, L.E.3
Bean, J.A.4
Walsh, J.5
-
45
-
-
0034066328
-
Feasibility of a clinical trial of augmentation therapy for alpha(1)-antitrypsin deficiency. The Alpha 1-Antitrypsin Deficiency Registry Study Group
-
Schluchter M.D., Stoller J.K., Barker A.F., Buist A.S., Crystal R.G., Donohue J.F., et al. Feasibility of a clinical trial of augmentation therapy for alpha(1)-antitrypsin deficiency. The Alpha 1-Antitrypsin Deficiency Registry Study Group. Am J Respir Crit Care Med 2000, 161:796-801.
-
(2000)
Am J Respir Crit Care Med
, vol.161
, pp. 796-801
-
-
Schluchter, M.D.1
Stoller, J.K.2
Barker, A.F.3
Buist, A.S.4
Crystal, R.G.5
Donohue, J.F.6
-
46
-
-
0033739182
-
Augmentation therapy reduces frequency of lung infections in antitrypsin deficiency: A new hypothesis with supporting data
-
Lieberman J. Augmentation therapy reduces frequency of lung infections in antitrypsin deficiency: A new hypothesis with supporting data. Chest 2000, 118:1480-1485.
-
(2000)
Chest
, vol.118
, pp. 1480-1485
-
-
Lieberman, J.1
-
47
-
-
0034017941
-
Should health-care systems pay for replacement therapy in patients with alpha(1)-antitrypsin deficiency? A critical review and cost-effectiveness analysis
-
Alkins S.A., O'Malley P. Should health-care systems pay for replacement therapy in patients with alpha(1)-antitrypsin deficiency? A critical review and cost-effectiveness analysis. Chest 2000, 117:875-880.
-
(2000)
Chest
, vol.117
, pp. 875-880
-
-
Alkins, S.A.1
O'Malley, P.2
-
48
-
-
0033995116
-
Distribution of alpha(1)-antitrypsin alleles in patients with bronchiectasis
-
Cuvelier A., Muir J.F., Hellot M.F., Benhamou D., Martin J.P., Bénichou J., et al. Distribution of alpha(1)-antitrypsin alleles in patients with bronchiectasis. Chest 2000, 117:415-419.
-
(2000)
Chest
, vol.117
, pp. 415-419
-
-
Cuvelier, A.1
Muir, J.F.2
Hellot, M.F.3
Benhamou, D.4
Martin, J.P.5
Bénichou, J.6
-
49
-
-
0033979879
-
Risk of hospital admission for obstructive pulmonary disease in alpha(1)-antitrypsin heterozygotes of phenotype PiMZ
-
Seersholm N., Wilcke J.T., Kok-Jensen A., Dirksen A. Risk of hospital admission for obstructive pulmonary disease in alpha(1)-antitrypsin heterozygotes of phenotype PiMZ. Am J Respir Crit Care Med 2000, 161:81-84.
-
(2000)
Am J Respir Crit Care Med
, vol.161
, pp. 81-84
-
-
Seersholm, N.1
Wilcke, J.T.2
Kok-Jensen, A.3
Dirksen, A.4
-
50
-
-
0034743745
-
Alpha1-antitrypsin deficiency: A position statement of the Canadian Thoracic Society
-
Standards Committee of the Canadian Thoracic Society
-
Abboud R.T., Ford G.T., Chapman K.R. Alpha1-antitrypsin deficiency: A position statement of the Canadian Thoracic Society. Can Respir J 2001, 8:81-88. Standards Committee of the Canadian Thoracic Society.
-
(2001)
Can Respir J
, vol.8
, pp. 81-88
-
-
Abboud, R.T.1
Ford, G.T.2
Chapman, K.R.3
-
51
-
-
0034889702
-
High-resolution computed tomography scanning in alpha1-antitrypsin deficiency: Relationship to lung function and health status
-
Dowson L.J., Guest P.J., Hill S.L., Holder R.L., Stockley R.A. High-resolution computed tomography scanning in alpha1-antitrypsin deficiency: Relationship to lung function and health status. Eur Respir J 2001, 17:1097-1104.
-
(2001)
Eur Respir J
, vol.17
, pp. 1097-1104
-
-
Dowson, L.J.1
Guest, P.J.2
Hill, S.L.3
Holder, R.L.4
Stockley, R.A.5
-
52
-
-
0036447470
-
A preliminary assessment of alpha-1 antitrypsin S and Z deficiency allele frequencies in common variable immunodeficiency patients with and without bronchiectasis
-
Sansom M.E., Ferry B.L., Sherrell Z.P., Chapel H.M. A preliminary assessment of alpha-1 antitrypsin S and Z deficiency allele frequencies in common variable immunodeficiency patients with and without bronchiectasis. Clin Exp Immunol 2002, 130:489-494.
-
(2002)
Clin Exp Immunol
, vol.130
, pp. 489-494
-
-
Sansom, M.E.1
Ferry, B.L.2
Sherrell, Z.P.3
Chapel, H.M.4
-
53
-
-
0035095548
-
Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen. Longitudinal follow-up of patients with alpha (1)-protease inhibitor deficiency before and during therapy with IV alpha(1)-protease inhibitor
-
Wencker M., Fuhrmann B., Banik N., Konietzko N. Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen. Longitudinal follow-up of patients with alpha (1)-protease inhibitor deficiency before and during therapy with IV alpha(1)-protease inhibitor. Chest 2001, 119:737-744.
-
(2001)
Chest
, vol.119
, pp. 737-744
-
-
Wencker, M.1
Fuhrmann, B.2
Banik, N.3
Konietzko, N.4
-
54
-
-
0035990476
-
Screening for alpha1-Pi deficiency in patients with lung diseases
-
Wencker M., Marx A., Konietzko N., Schaefer B., Campbell E.J. Screening for alpha1-Pi deficiency in patients with lung diseases. Eur Respir J 2002, 20:319-324.
-
(2002)
Eur Respir J
, vol.20
, pp. 319-324
-
-
Wencker, M.1
Marx, A.2
Konietzko, N.3
Schaefer, B.4
Campbell, E.J.5
-
55
-
-
0036606880
-
The effect of augmentation therapy on bronchial inflammation in alpha1-antitrypsin deficiency
-
Stockley R.A., Bayley D.L., Unsal I., Dowson L.J. The effect of augmentation therapy on bronchial inflammation in alpha1-antitrypsin deficiency. Am J Respir Crit Care Med 2002, 165:1494-1498.
-
(2002)
Am J Respir Crit Care Med
, vol.165
, pp. 1494-1498
-
-
Stockley, R.A.1
Bayley, D.L.2
Unsal, I.3
Dowson, L.J.4
-
56
-
-
0036488898
-
Influence of deficient alpha1-anti-trypsin phenotypes on clinical characteristics and severity of asthma in adults
-
Miravitlles M., Vilà S., Torrella M., Balcells E., Rodríguez-Frías F., de la Roza C., et al. Influence of deficient alpha1-anti-trypsin phenotypes on clinical characteristics and severity of asthma in adults. Respir Med 2002, 96:186-192.
-
(2002)
Respir Med
, vol.96
, pp. 186-192
-
-
Miravitlles, M.1
Vilà, S.2
Torrella, M.3
Balcells, E.4
Rodríguez-Frías, F.5
de la Roza, C.6
-
57
-
-
0038216603
-
Augmentation therapy with alpha1-antitrypsin: Patterns of use and adverse events
-
Stoller J.K., Fallat R., Schluchter M.D., O'Brien R.G., Connor J.T., Gross N., et al. Augmentation therapy with alpha1-antitrypsin: Patterns of use and adverse events. Chest 2003, 123:1425-1434.
-
(2003)
Chest
, vol.123
, pp. 1425-1434
-
-
Stoller, J.K.1
Fallat, R.2
Schluchter, M.D.3
O'Brien, R.G.4
Connor, J.T.5
Gross, N.6
-
58
-
-
0347291902
-
Predictors of mortality in alpha1-antitrypsin deficiency
-
Dawkins P.A., Dowson L.J., Guest P.J., Stockley R.A. Predictors of mortality in alpha1-antitrypsin deficiency. Thorax 2003, 58:1020-1026.
-
(2003)
Thorax
, vol.58
, pp. 1020-1026
-
-
Dawkins, P.A.1
Dowson, L.J.2
Guest, P.J.3
Stockley, R.A.4
-
59
-
-
0141558799
-
Major components of the direct medical costs of alpha1-antitrypsin deficiency
-
Mullins C.D., Wang J., Stoller J.K. Major components of the direct medical costs of alpha1-antitrypsin deficiency. Chest 2003, 124:826-831.
-
(2003)
Chest
, vol.124
, pp. 826-831
-
-
Mullins, C.D.1
Wang, J.2
Stoller, J.K.3
-
60
-
-
0037952677
-
Cost-effectiveness analysis of augmentation therapy for severe alpha1-antitrypsin deficiency
-
Gildea T.R., Shermock K.M., Singer M.E., Stoller J.K. Cost-effectiveness analysis of augmentation therapy for severe alpha1-antitrypsin deficiency. Am J Respir Crit Care Med 2003, 167:1387-1392.
-
(2003)
Am J Respir Crit Care Med
, vol.167
, pp. 1387-1392
-
-
Gildea, T.R.1
Shermock, K.M.2
Singer, M.E.3
Stoller, J.K.4
-
61
-
-
6344238675
-
Chronic obstructive pulmonary disease in a1-antitrypsin PI MZ heterozygotes: A meta-analysis
-
Hersh C.P., Dahl M., Ly N.P., Berkey C.S., Nordestgaard B.G., Silverman E.K. Chronic obstructive pulmonary disease in a1-antitrypsin PI MZ heterozygotes: A meta-analysis. Thorax 2004, 59:843-849.
-
(2004)
Thorax
, vol.59
, pp. 843-849
-
-
Hersh, C.P.1
Dahl, M.2
Ly, N.P.3
Berkey, C.S.4
Nordestgaard, B.G.5
Silverman, E.K.6
-
63
-
-
14944385198
-
Emphysema in alpha1-antitrypsin deficiency: Does replacement therapy affect outcome?
-
Abboud R.T., Ford G.T., Chapman K.R. Emphysema in alpha1-antitrypsin deficiency: Does replacement therapy affect outcome?. Treat Respir Med 2005, 4:1-8.
-
(2005)
Treat Respir Med
, vol.4
, pp. 1-8
-
-
Abboud, R.T.1
Ford, G.T.2
Chapman, K.R.3
-
64
-
-
33745076743
-
Cost-effectiveness of population screening for alpha-1 antitrypsin deficiency: A decision analysis
-
Shermock K.M., Gildea T.R., Singer M., Stoller J.K. Cost-effectiveness of population screening for alpha-1 antitrypsin deficiency: A decision analysis. COPD 2005, 2:411-418.
-
(2005)
COPD
, vol.2
, pp. 411-418
-
-
Shermock, K.M.1
Gildea, T.R.2
Singer, M.3
Stoller, J.K.4
-
65
-
-
33745032125
-
Multi-center study: The biochemical efficacy, safety and tolerability of a new alpha1-proteinase inhibitor, Zemaira
-
Stocks J.M., Brantly M., Pollock D., Barker A., Kueppers F., Strange C., et al. Multi-center study: The biochemical efficacy, safety and tolerability of a new alpha1-proteinase inhibitor, Zemaira. COPD 2006, 3:17-23.
-
(2006)
COPD
, vol.3
, pp. 17-23
-
-
Stocks, J.M.1
Brantly, M.2
Pollock, D.3
Barker, A.4
Kueppers, F.5
Strange, C.6
-
66
-
-
33845227581
-
Alpha-1-antitrypsin deficiency: Optimal therapeutic regimen based on population pharmacokinetics
-
Soy D., de la Roza C., Lara B., Esquinas C., Torres A., Miravitlles M. Alpha-1-antitrypsin deficiency: Optimal therapeutic regimen based on population pharmacokinetics. Thorax 2006, 61:1059-1064.
-
(2006)
Thorax
, vol.61
, pp. 1059-1064
-
-
Soy, D.1
de la Roza, C.2
Lara, B.3
Esquinas, C.4
Torres, A.5
Miravitlles, M.6
-
67
-
-
33751067225
-
Pharmacokinetics of alpha1-antitrypsin replacement therapy in severe congenital emphysema
-
Vidal R., Padullés N., Sala F., Jardí R., Rodríguez F., Montoro J.B. Pharmacokinetics of alpha1-antitrypsin replacement therapy in severe congenital emphysema. Arch Bronconeumol 2006, 42:553-556.
-
(2006)
Arch Bronconeumol
, vol.42
, pp. 553-556
-
-
Vidal, R.1
Padullés, N.2
Sala, F.3
Jardí, R.4
Rodríguez, F.5
Montoro, J.B.6
-
68
-
-
33645223500
-
Results of a survey of patients with alpha-1 antitrypsin deficiency
-
Strange C., Stoller J.K., Sandhaus R.A., Dickson R., Turino G. Results of a survey of patients with alpha-1 antitrypsin deficiency. Respiration 2006, 73:185-190.
-
(2006)
Respiration
, vol.73
, pp. 185-190
-
-
Strange, C.1
Stoller, J.K.2
Sandhaus, R.A.3
Dickson, R.4
Turino, G.5
-
69
-
-
33748653991
-
Alpha-1-antitrypsin replacement therapy: Current status
-
Abusriwil H., Stockley R.A. Alpha-1-antitrypsin replacement therapy: Current status. Curr Opin Pulm Med 2006, 12:125-131.
-
(2006)
Curr Opin Pulm Med
, vol.12
, pp. 125-131
-
-
Abusriwil, H.1
Stockley, R.A.2
-
70
-
-
33746192129
-
Deficient alpha-1-antitrypsin phenotypes and persistent airflow limitation in severe asthma
-
Van Veen I.H., ten Brinke A., van der Linden A.C., Rabe K.F., Bel E.H. Deficient alpha-1-antitrypsin phenotypes and persistent airflow limitation in severe asthma. Respir Med 2006, 100:1534-1539.
-
(2006)
Respir Med
, vol.100
, pp. 1534-1539
-
-
Van Veen, I.H.1
ten Brinke, A.2
van der Linden, A.C.3
Rabe, K.F.4
Bel, E.H.5
-
71
-
-
33746881048
-
Estimating the risk for alpha-1 antitrypsin deficiency among COPD patients: Evidence supporting targeted screening
-
De Serres F.J., Blanco I., Fernández-Bustillo E. Estimating the risk for alpha-1 antitrypsin deficiency among COPD patients: Evidence supporting targeted screening. COPD 2006, 3:133-139.
-
(2006)
COPD
, vol.3
, pp. 133-139
-
-
De Serres, F.J.1
Blanco, I.2
Fernández-Bustillo, E.3
-
72
-
-
34548071486
-
An overview of alpha-1 antitrypsin deficiency
-
Hericks A.J., Bhat A. An overview of alpha-1 antitrypsin deficiency. Mo Med 2007, 104:255-259.
-
(2007)
Mo Med
, vol.104
, pp. 255-259
-
-
Hericks, A.J.1
Bhat, A.2
-
73
-
-
35648984600
-
Aralast: An alpha 1-protease inhibitor for the treatment of alpha-antitrypsin deficiency
-
Mordwinkin N.M., Louie S.G. Aralast: An alpha 1-protease inhibitor for the treatment of alpha-antitrypsin deficiency. Expert Opin Pharmacother 2007, 8:2609-2614.
-
(2007)
Expert Opin Pharmacother
, vol.8
, pp. 2609-2614
-
-
Mordwinkin, N.M.1
Louie, S.G.2
-
74
-
-
36148968064
-
Development and results of the Spanish registry of patients with alpha-1-antitrypsin deficiency
-
Lara B., de la Roza C., Vilà S., Vidal R., Miravitlles M. Development and results of the Spanish registry of patients with alpha-1-antitrypsin deficiency. Int J Chron Obstruct Pulmon Dis 2007, 2:393-398.
-
(2007)
Int J Chron Obstruct Pulmon Dis
, vol.2
, pp. 393-398
-
-
Lara, B.1
de la Roza, C.2
Vilà, S.3
Vidal, R.4
Miravitlles, M.5
-
75
-
-
34547647784
-
Alpha one antitrypsin deficiency: From gene to treatment
-
Wood A.M., Stockley R.A. Alpha one antitrypsin deficiency: From gene to treatment. Respiration 2007, 74:481-492.
-
(2007)
Respiration
, vol.74
, pp. 481-492
-
-
Wood, A.M.1
Stockley, R.A.2
-
76
-
-
42149182337
-
Alpha-1 antitrypsin: Now available, but do we need it
-
Russi E.W. Alpha-1 antitrypsin: Now available, but do we need it. Swiss Med Wkly 2008, 138:191-196.
-
(2008)
Swiss Med Wkly
, vol.138
, pp. 191-196
-
-
Russi, E.W.1
-
77
-
-
59549098869
-
Detection of alpha-1 antitrypsin deficiency: A review
-
Aboussouan L.S., Stoller J.K. Detection of alpha-1 antitrypsin deficiency: A review. Respir Med 2009, 103:335-341.
-
(2009)
Respir Med
, vol.103
, pp. 335-341
-
-
Aboussouan, L.S.1
Stoller, J.K.2
-
78
-
-
74449091958
-
Safety and efficacy of alpha-1-antitrypsin augmentation therapy in the treatment of patients with alpha-1-antitrypsin deficiency
-
Petrache I., Hajjar J., Campos M. Safety and efficacy of alpha-1-antitrypsin augmentation therapy in the treatment of patients with alpha-1-antitrypsin deficiency. Biologics 2009, 3:193-204.
-
(2009)
Biologics
, vol.3
, pp. 193-204
-
-
Petrache, I.1
Hajjar, J.2
Campos, M.3
-
79
-
-
70350455493
-
Augmentation therapy in alpha-1 antitrypsin deficiency
-
Sandhaus R.A. Augmentation therapy in alpha-1 antitrypsin deficiency. COPD 2009, 6:147-148.
-
(2009)
COPD
, vol.6
, pp. 147-148
-
-
Sandhaus, R.A.1
-
80
-
-
67649390890
-
Alpha1-antitrypsin deficiency
-
Silverman E.K., Sandhaus R.A. Alpha1-antitrypsin deficiency. N Engl J Med 2009, 360:2749-2757.
-
(2009)
N Engl J Med
, vol.360
, pp. 2749-2757
-
-
Silverman, E.K.1
Sandhaus, R.A.2
-
81
-
-
85104566196
-
Augmentation therapy with alpha1-antitrypsin: Patterns of use and adverse events
-
Stoller J.K., Fallat R., Schluchter M.D., O'Brien R.G., Connor J.T., Gross N., et al. Augmentation therapy with alpha1-antitrypsin: Patterns of use and adverse events. Chest 2009, 136(5 Suppl):e30.
-
(2009)
Chest
, vol.136
, Issue.5
-
-
Stoller, J.K.1
Fallat, R.2
Schluchter, M.D.3
O'Brien, R.G.4
Connor, J.T.5
Gross, N.6
-
82
-
-
70349694399
-
Alpha1-antitrypsin deficiency: Best clinical practice
-
Kalsheker N.A. Alpha1-antitrypsin deficiency: Best clinical practice. J Clin Pathol 2009, 62:865-869.
-
(2009)
J Clin Pathol
, vol.62
, pp. 865-869
-
-
Kalsheker, N.A.1
-
83
-
-
77949329900
-
Alpha-1-antitrypsin augmentation therapy in deficient individuals enrolled in the Alpha-1 Foundation DNA and Tissue Bank
-
Tonelli A.R., Rouhani F., Li N., Schreck P., Brantly M.L. Alpha-1-antitrypsin augmentation therapy in deficient individuals enrolled in the Alpha-1 Foundation DNA and Tissue Bank. Int J Chron Obstruct Pulmon Dis 2009, 4:443-452.
-
(2009)
Int J Chron Obstruct Pulmon Dis
, vol.4
, pp. 443-452
-
-
Tonelli, A.R.1
Rouhani, F.2
Li, N.3
Schreck, P.4
Brantly, M.L.5
-
84
-
-
69249101657
-
Rate of progression of lung function impairment in alpha1-antitrypsin deficiency
-
Dawkins P.A., Dawkins C.L., Wood A.M., Nightingale P.G., Stockley J.A., Stockley R.A. Rate of progression of lung function impairment in alpha1-antitrypsin deficiency. Eur Respir J 2009, 33:1338-1344.
-
(2009)
Eur Respir J
, vol.33
, pp. 1338-1344
-
-
Dawkins, P.A.1
Dawkins, C.L.2
Wood, A.M.3
Nightingale, P.G.4
Stockley, J.A.5
Stockley, R.A.6
-
85
-
-
77952806527
-
Augmentation therapy for alpha-1 antitrypsin deficiency -not enough evidence to support its use yet!
-
McCarthy C., Dimitrov B.D. Augmentation therapy for alpha-1 antitrypsin deficiency -not enough evidence to support its use yet!. COPD 2010, 7:234.
-
(2010)
COPD
, vol.7
, pp. 234
-
-
McCarthy, C.1
Dimitrov, B.D.2
-
86
-
-
75849124048
-
Alpha1-antitrypsin deficiency: Forgotten etiology
-
Kaplan A., Cosentino L. Alpha1-antitrypsin deficiency: Forgotten etiology. Can Fam Physician 2010, 56:19-24.
-
(2010)
Can Fam Physician
, vol.56
, pp. 19-24
-
-
Kaplan, A.1
Cosentino, L.2
-
87
-
-
78349253871
-
Accelerated spirometric decline in New York City firefighters with a1-antitrypsin deficiency
-
Banauch G.I., Brantly M., Izbicki G., Hall C., Shanske A., Chavko R., et al. Accelerated spirometric decline in New York City firefighters with a1-antitrypsin deficiency. Chest 2010, 138:1116-1124.
-
(2010)
Chest
, vol.138
, pp. 1116-1124
-
-
Banauch, G.I.1
Brantly, M.2
Izbicki, G.3
Hall, C.4
Shanske, A.5
Chavko, R.6
-
88
-
-
78649460678
-
Emerging drugs for alpha-1-antitrypsin deficiency
-
Stockley R.A. Emerging drugs for alpha-1-antitrypsin deficiency. Expert Opin Emerg Drugs 2010, 15:685-694.
-
(2010)
Expert Opin Emerg Drugs
, vol.15
, pp. 685-694
-
-
Stockley, R.A.1
-
89
-
-
77957935340
-
Augmentation therapy in alpha-1 antitrypsin deficiency: Advances and controversies
-
Tonelli A.R., Brantly M.L. Augmentation therapy in alpha-1 antitrypsin deficiency: Advances and controversies. Ther Adv Respir Dis 2010, 4:289-312.
-
(2010)
Ther Adv Respir Dis
, vol.4
, pp. 289-312
-
-
Tonelli, A.R.1
Brantly, M.L.2
-
90
-
-
77957000718
-
COPD and alpha-1-antitrypsin deficiency
-
Lara B. COPD and alpha-1-antitrypsin deficiency. Arch Bronconeumol 2010, 46:2-8.
-
(2010)
Arch Bronconeumol
, vol.46
, pp. 2-8
-
-
Lara, B.1
-
91
-
-
77953319553
-
Alpha-1 antitrypsin deficiency: Whom to test, whom to treat
-
Sandhaus R.A. Alpha-1 antitrypsin deficiency: Whom to test, whom to treat. Semin Respir Crit Care Med 2010, 31:343-347.
-
(2010)
Semin Respir Crit Care Med
, vol.31
, pp. 343-347
-
-
Sandhaus, R.A.1
-
92
-
-
78349265383
-
α1-Antitrypsin protease inhibitor MZ heterozygosity is associated with airflow obstruction in two large cohorts
-
Sørheim I.C., Bakke P., Gulsvik A., Pillai S.G., Johannessen A., Gaarder P.I., et al. α1-Antitrypsin protease inhibitor MZ heterozygosity is associated with airflow obstruction in two large cohorts. Chest 2010, 138:1125-1132.
-
(2010)
Chest
, vol.138
, pp. 1125-1132
-
-
Sørheim, I.C.1
Bakke, P.2
Gulsvik, A.3
Pillai, S.G.4
Johannessen, A.5
Gaarder, P.I.6
-
93
-
-
79951631719
-
The role of augmentation therapy in alpha-1 antitrypsin deficiency
-
Kueppers F. The role of augmentation therapy in alpha-1 antitrypsin deficiency. Curr Med Res Opin 2011, 27:579-588.
-
(2011)
Curr Med Res Opin
, vol.27
, pp. 579-588
-
-
Kueppers, F.1
-
94
-
-
84856144387
-
Why has it been so difficult to prove the efficacy of alpha-1-antitrypsin replacement therapy Insights from the study of disease pathogenesis
-
Dickens J.A., Lomas D.A. Why has it been so difficult to prove the efficacy of alpha-1-antitrypsin replacement therapy Insights from the study of disease pathogenesis. Drug Des Devel Ther 2011, 5:391-405.
-
(2011)
Drug Des Devel Ther
, vol.5
, pp. 391-405
-
-
Dickens, J.A.1
Lomas, D.A.2
-
95
-
-
84859345065
-
Rare alpha-1-antitrypsin variants: Are they really so rare
-
Rodriguez-Frías F., Miravitlles M., Vidal R., Camos S., Jardí R. Rare alpha-1-antitrypsin variants: Are they really so rare. Ther Adv Respir Dis 2012, 6:79-85.
-
(2012)
Ther Adv Respir Dis
, vol.6
, pp. 79-85
-
-
Rodriguez-Frías, F.1
Miravitlles, M.2
Vidal, R.3
Camos, S.4
Jardí, R.5
-
96
-
-
84859354170
-
Reduction of severe exacerbations and hospitalization-derived costs in alpha-1-antitrypsin-deficient patients treated with alpha-1-antitrypsin augmentation therapy
-
Investigators of the rEXA study group
-
Barros-Tizón J.C., Torres M.L., Blanco I., Martínez M.T. Reduction of severe exacerbations and hospitalization-derived costs in alpha-1-antitrypsin-deficient patients treated with alpha-1-antitrypsin augmentation therapy. Ther Adv Respir Dis 2012, 6:67-78. Investigators of the rEXA study group.
-
(2012)
Ther Adv Respir Dis
, vol.6
, pp. 67-78
-
-
Barros-Tizón, J.C.1
Torres, M.L.2
Blanco, I.3
Martínez, M.T.4
-
97
-
-
84862298546
-
Alpha-1-antitrypsin and other proteinase inhibitors
-
Miravitlles M. Alpha-1-antitrypsin and other proteinase inhibitors. Curr Opin Pharmacol 2012, 12:309-314.
-
(2012)
Curr Opin Pharmacol
, vol.12
, pp. 309-314
-
-
Miravitlles, M.1
-
98
-
-
84872257169
-
The effects of weekly augmentation therapy in patients with PiZZ α1-antitrypsin deficiency
-
Schmid S.T., Koepke J., Dresel M., Hattesohl A., Frenzel E., Perez J., et al. The effects of weekly augmentation therapy in patients with PiZZ α1-antitrypsin deficiency. Int J Chron Obstruct Pulmon Dis 2012, 7:687-696.
-
(2012)
Int J Chron Obstruct Pulmon Dis
, vol.7
, pp. 687-696
-
-
Schmid, S.T.1
Koepke, J.2
Dresel, M.3
Hattesohl, A.4
Frenzel, E.5
Perez, J.6
-
99
-
-
84861319134
-
A review of augmentation therapy for alpha-1 antitrypsin deficiency
-
Mohanka M., Khemasuwan D., Stoller J.K. A review of augmentation therapy for alpha-1 antitrypsin deficiency. Expert Opin Biol Ther 2012, 12:685-700.
-
(2012)
Expert Opin Biol Ther
, vol.12
, pp. 685-700
-
-
Mohanka, M.1
Khemasuwan, D.2
Stoller, J.K.3
-
100
-
-
84859787234
-
α1-Proteinase inhibitor (human) in the treatment of hereditary emphysema secondary to α1-antitrypsin deficiency: Number and costs of years of life gained
-
Sclar D.A., Evans M.A., Robison L.M., Skaer T.L. α1-Proteinase inhibitor (human) in the treatment of hereditary emphysema secondary to α1-antitrypsin deficiency: Number and costs of years of life gained. Clin Drug Investig 2012, 32:353-360.
-
(2012)
Clin Drug Investig
, vol.32
, pp. 353-360
-
-
Sclar, D.A.1
Evans, M.A.2
Robison, L.M.3
Skaer, T.L.4
-
101
-
-
84875675170
-
The challenge of detecting alpha-1 antitrypsin deficiency
-
Stoller J.K., Brantly M. The challenge of detecting alpha-1 antitrypsin deficiency. COPD 2013, 10:26-34.
-
(2013)
COPD
, vol.10
, pp. 26-34
-
-
Stoller, J.K.1
Brantly, M.2
-
102
-
-
84875670108
-
Alpha-1 antitrypsin deficiency: The European experience
-
Stockley R.A., Dirksen A., Stolk J. Alpha-1 antitrypsin deficiency: The European experience. COPD 2013, 10:50-53.
-
(2013)
COPD
, vol.10
, pp. 50-53
-
-
Stockley, R.A.1
Dirksen, A.2
Stolk, J.3
-
103
-
-
84875668547
-
Alpha-1 antitrypsin augmentation therapy
-
Wewers M.D., Crystal R.G. Alpha-1 antitrypsin augmentation therapy. COPD 2013, 10:64-67.
-
(2013)
COPD
, vol.10
, pp. 64-67
-
-
Wewers, M.D.1
Crystal, R.G.2
-
104
-
-
84875646576
-
Airway disease in alpha-1 antitrypsin deficiency
-
Strange C. Airway disease in alpha-1 antitrypsin deficiency. COPD 2013, 10:68-73.
-
(2013)
COPD
, vol.10
, pp. 68-73
-
-
Strange, C.1
-
105
-
-
84887955432
-
Safety and pharmacokinetics of 120mg/kg versus 60mg/kg weekly intravenous infusions of alpha-1 proteinase inhibitor in alpha-1 antitrypsin deficiency: A multicenter, randomized, double-blind, crossover Study (SPARK)
-
Campos M.A., Kueppers F., Stocks J.M., Strange C., Chen J., Griffin R., et al. Safety and pharmacokinetics of 120mg/kg versus 60mg/kg weekly intravenous infusions of alpha-1 proteinase inhibitor in alpha-1 antitrypsin deficiency: A multicenter, randomized, double-blind, crossover Study (SPARK). COPD 2013, 10:687-695.
-
(2013)
COPD
, vol.10
, pp. 687-695
-
-
Campos, M.A.1
Kueppers, F.2
Stocks, J.M.3
Strange, C.4
Chen, J.5
Griffin, R.6
-
106
-
-
84880752065
-
Inhaled alpha 1-antitrypsin: Gauging patient interest in a new treatment
-
Monk R., Graves M., Williams P., Strange C. Inhaled alpha 1-antitrypsin: Gauging patient interest in a new treatment. COPD 2013, 10:411-415.
-
(2013)
COPD
, vol.10
, pp. 411-415
-
-
Monk, R.1
Graves, M.2
Williams, P.3
Strange, C.4
-
107
-
-
84885015158
-
Augmentation therapy for alpha-1 antitrypsin deficiency: Towards a personalised approach
-
Stockley R.A., Miravitlles M., Vogelmeier C. Augmentation therapy for alpha-1 antitrypsin deficiency: Towards a personalised approach. Orphanet J Rare Dis 2013, 8:149.
-
(2013)
Orphanet J Rare Dis
, vol.8
, pp. 149
-
-
Stockley, R.A.1
Miravitlles, M.2
Vogelmeier, C.3
-
108
-
-
33748305617
-
An official ATS statement: Grading the quality of evidence and strength of recommendations in ATS guidelines and recommendations
-
ATS Documents Development and Implementation Committee
-
Schünemann H.J., Jaeschke R., Cook D.J., Bria W.F., El-Solh A.A., Ernst A., et al. An official ATS statement: Grading the quality of evidence and strength of recommendations in ATS guidelines and recommendations. Am J Respir Crit Care Med 2006, 174:605-614. ATS Documents Development and Implementation Committee.
-
(2006)
Am J Respir Crit Care Med
, vol.174
, pp. 605-614
-
-
Schünemann, H.J.1
Jaeschke, R.2
Cook, D.J.3
Bria, W.F.4
El-Solh, A.A.5
Ernst, A.6
-
109
-
-
84878014819
-
Calidad y fuerza: el sistema GRADE para la formulación de recomendaciones en las guías de práctica clínica
-
Alonso-Coello P., Rigau D., Juliana Sanabria A., Plaza V., Miravitlles M., Martínez L. Calidad y fuerza: el sistema GRADE para la formulación de recomendaciones en las guías de práctica clínica. Arch Bronconeumol 2013, 49:261-267.
-
(2013)
Arch Bronconeumol
, vol.49
, pp. 261-267
-
-
Alonso-Coello, P.1
Rigau, D.2
Juliana Sanabria, A.3
Plaza, V.4
Miravitlles, M.5
Martínez, L.6
-
110
-
-
33144490691
-
Grading strength of recommendations and quality of evidence in clinical guidelines: Report from an American Colleg Chest Physicians Task Force
-
Guyatt G., Gutterman D., Baumann M.H., Adrizzo-Harris D., Hylek E.M., Phillips B., et al. Grading strength of recommendations and quality of evidence in clinical guidelines: Report from an American Colleg Chest Physicians Task Force. Chest 2006, 129:178-181.
-
(2006)
Chest
, vol.129
, pp. 178-181
-
-
Guyatt, G.1
Gutterman, D.2
Baumann, M.H.3
Adrizzo-Harris, D.4
Hylek, E.M.5
Phillips, B.6
-
111
-
-
85047695769
-
Guía Española de la EPOC (GesEPOC). Tratamiento farmacológico de la EPOC estable
-
Miravitlles M., Soler-Cataluña J.J., Calle M., Molina J., Almagro P., Quintano J.A., et al. Guía Española de la EPOC (GesEPOC). Tratamiento farmacológico de la EPOC estable. Arch Bronconeumol 2012, 48:247-257.
-
(2012)
Arch Bronconeumol
, vol.48
, pp. 247-257
-
-
Miravitlles, M.1
Soler-Cataluña, J.J.2
Calle, M.3
Molina, J.4
Almagro, P.5
Quintano, J.A.6
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