Deficiency of interleukin-1 receptor-associated kinase 4 presenting as fatal Pseudomonas aeruginosa bacteremia in two siblings

Pediatric Infectious Disease Journal

Volumn 34, Issue 3, 2015, Pages 299-300

  Stergiopoulou, Theodouli ^a,b   Walsh, Thomas J ^b   Seghaye, Marie Christine ^a   Netea, Mihai G ^c   Casanova, Jean Laurent ^d,e,f   Moutschen, Michel ^g   Picard, Capucine ^e,h  

^a UNIVERSITY OF LIÈGE   (Belgium)

^b UNIVERSITY OF LIÈGE   (Belgium)

^c WEILL CORNELL MEDICAL CENTER   (United States)

^d RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^e ROCKEFELLER UNIVERSITY   (United States)

^f IMAGINE INSTITUTE   (France)

^g HOWARD HUGHES MEDICAL INSTITUTE   (United States)

^h HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

delayed umbilical cord separation; ecthyma gangrenosum; interleukin 1 receptor associated kinase 4; primary immunodeficiency; Pseudomonas sepsis

Indexed keywords

CEFOTAXIME; INOTROPIC AGENT; INTERLEUKIN 1 RECEPTOR ASSOCIATED KINASE 4; INTERLEUKIN 1 RECEPTOR ASSOCIATED KINASE;

ANTIBIOTIC THERAPY; ARTICLE; AUTOPSY; CASE REPORT; CHILD; GENETIC ANALYSIS; GRAM NEGATIVE SEPSIS; HUMAN; IMMUNE DEFICIENCY; MALE; PRIORITY JOURNAL; PSEUDOMONAS AERUGINOSA; PSEUDOMONAS AERUGINOSA BACTEREMIA; PSEUDOMONAS INFECTION; RESUSCITATION; SEPTIC SHOCK; SIBLING; THORAX RADIOGRAPHY; BACTEREMIA; FATALITY; GENETICS; INFANT; METABOLISM; MICROBIOLOGY; PSEUDOMONAS INFECTIONS;

BACTEREMIA; FATAL OUTCOME; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT; INTERLEUKIN-1 RECEPTOR-ASSOCIATED KINASES; MALE; PSEUDOMONAS AERUGINOSA; PSEUDOMONAS INFECTIONS; SIBLINGS;

EID: 84924270268     PISSN: 08913668     EISSN: 15320987     Source Type: Journal    
DOI: 10.1097/INF.0000000000000550     Document Type: Article

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