Ablation of Cypher, a PDZ-LIM domain Z-line protein, causes a severe form of congenital myopathy

Journal of Cell Biology

Volumn 155, Issue 3, 2001, Pages 605-612

  Zhou, Qiang ^a   Chu, Po Hsien ^a   Huang, Chenqun ^a   Cheng, Ching Feng ^a   Martone, Maryann E ^b   Knoll, Gudrun ^a   Diane Shelton, G ^c   Evans, Sylvia ^a   Chen, Ju ^a  

^a UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Congenital myopathy; Cypher; LIM; PDZ; Z line

Indexed keywords

ALPHA ACTININ; CYTOSKELETON PROTEIN; LIM PROTEIN; PROTEIN CYPHER; UNCLASSIFIED DRUG; ACTININ; ACTN2 PROTEIN, MOUSE; ACTN2 PROTEIN, RAT; AMINO ACID; CARRIER PROTEIN; HOMEODOMAIN PROTEIN; LDB3 PROTEIN, MOUSE; MUSCLE PROTEIN; SIGNAL TRANSDUCING ADAPTOR PROTEIN;

ANIMAL CELL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CONGENITAL DISORDER; CYTOSKELETON; MUSCLE CONTRACTION; MUSCLE FUNCTION; MYOPATHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN LOCALIZATION; RAT; SARCOMERE; ANIMAL; BINDING SITE; CELL CULTURE; CYTOLOGY; GENETICS; HEART MUSCLE; KNOCKOUT MOUSE; METABOLISM; MOUSE; MUTANT MOUSE STRAIN; PATHOLOGY; PHYSIOLOGY; SKELETAL MUSCLE;

ANIMALIA;

ACTININ; ADAPTOR PROTEINS, SIGNAL TRANSDUCING; AMINO ACIDS; ANIMALS; BINDING SITES; CARRIER PROTEINS; CELLS, CULTURED; HOMEODOMAIN PROTEINS; LIM DOMAIN PROTEINS; MICE; MICE, KNOCKOUT; MICE, MUTANT STRAINS; MUSCLE PROTEINS; MUSCLE, SKELETAL; MYOCARDIUM; MYOPATHIES, STRUCTURAL, CONGENITAL; RATS;

EID: 84924110084     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.200107092     Document Type: Article

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