Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties

Emerging Infectious Diseases

Volumn 20, Issue 12, 2014, Pages 1969-1979

  Diack, Abigail B ^a   Ritchie, Diane L ^b   Peden, Alexander H ^b   Brown, Deborah ^a   Boyle, Aileen ^a   Morabito, Laura ^a   Maclennan, David ^a   Burgoyne, Paul ^a   Jansen, Casper ^d   Knight, Richard S ^b   Piccardo, Pedro ^c   Ironside, James W ^b   Manson, Jean C ^a  

^a UNIVERSITY OF EDINBURGH   (United Kingdom)

^b UNIVERSITY OF EDINBURGH   (United Kingdom)

^c CENTER FOR DRUG EVALUATION AND RESEARCH   (United States)

^d UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

METHIONINE; PRION PROTEIN; THIOFLAVINE; VALINE; PRION;

ADULT; AGED; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CASE REPORT; CELL VACUOLE; CONTROLLED STUDY; DISEASE TRANSMISSION; FEMALE; GEL ELECTROPHORESIS; GENE EXPRESSION; GENETIC SIMILARITY; GLIOSIS; HUMAN; IMMUNOHISTOCHEMISTRY; MALE; MIDDLE AGED; MOUSE; NONHUMAN; PRION DISEASE; PROTEASE SENSITIVE PRIONOPATHY; SCORING SYSTEM; WESTERN BLOTTING; ANIMAL; ASTROCYTE; BRAIN; DISEASE MODEL; GENETIC VARIATION; GENETICS; GENOTYPE; METABOLISM; PATHOLOGY; PRION; TRANSGENIC MOUSE; TRANSMISSION;

ANIMALS; ASTROCYTES; BRAIN; DISEASE MODELS, ANIMAL; GENETIC VARIATION; GENOTYPE; GLIOSIS; HUMANS; MICE; MICE, TRANSGENIC; PRION DISEASES; PRIONS;

EID: 84922931281     PISSN: 10806040     EISSN: 10806059     Source Type: Journal    
DOI: 10.3201/eid2012.140214     Document Type: Article

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