Treatment of bile acid amidation defects with glycocholic acid

Hepatology

Volumn 61, Issue 1, 2015, Pages 268-274

  Heubi, James E ^a   Setchell, Kenneth D R ^a   Jha, Pinky ^a   Buckley, Donna ^a   Zhang, Wujuan ^a   Rosenthal, Philip ^b   Potter, Carol ^c   Horslen, Simon ^d   Suskind, David ^d  

^a UNIVERSITY OF CINCINNATI   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c OHIO STATE UNIVERSITY   (United States)

^d UNIVERSITY OF WASHINGTON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BILE ACID; ERGOCALCIFEROL; GLYCINE; GLYCOCHOLIC ACID; TAURINE; TOCOPHEROL; VITAMIN; ACYLTRANSFERASE; BILE ACID-COA AMINO ACID N-ACYLTRANSFERASE; CHOLAGOGUE;

ABSORPTION; AMIDATION; ARTICLE; BILE ACID METABOLISM; BILE SECRETION; CHILD; CLINICAL ARTICLE; CONCENTRATION (PARAMETERS); CONJUGATION; DRUG EFFICACY; DRUG SAFETY; DUODENUM; FAMILY; FAST ATOM BOMBARDMENT MASS SPECTROMETRY; FEMALE; GROWTH RETARDATION; HUMAN; INBORN ERROR OF METABOLISM; INTESTINE ABSORPTION; MALE; PREPUBERTY; PRIORITY JOURNAL; SCHOOL CHILD; SERUM; URINE; ADOLESCENT; BLOOD; CHILD DEVELOPMENT; DEFICIENCY; GENETICS; INFANT; METABOLISM; METABOLISM, INBORN ERRORS; PRESCHOOL CHILD;

ACYLTRANSFERASES; ADOLESCENT; BILE ACIDS AND SALTS; CHILD; CHILD DEVELOPMENT; CHILD, PRESCHOOL; CHOLAGOGUES AND CHOLERETICS; ERGOCALCIFEROLS; FEMALE; GLYCOCHOLIC ACID; HUMANS; INFANT; MALE; METABOLISM, INBORN ERRORS; TOCOPHEROLS;

EID: 84920970025     PISSN: 02709139     EISSN: 15273350     Source Type: Journal    
DOI: 10.1002/hep.27401     Document Type: Article

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