Heterogeneous histologic and clinical evolution in 3 cases of dense deposit disease with long-term follow-up

Human Pathology

Volumn 45, Issue 11, 2014, Pages 2326-2333

  Figuères, Marie Lucile ^a   Frémeaux Bacchi, Véronique ^b,c   Rabant, Marion ^a,d   Galmiche, Louise ^a,d   Marinozzi, Maria Chiara ^c   Grünfeld, Jean Pierre ^a,d   Noël, Laure Hélène ^a   Servais, Aude ^a,d  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b HÔPITAL EUROPÉEN GEORGES POMPIDOU   (France)

^c CENTRE DE RECHERCHE DES CORDELIERS   (France)

^d UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

C3 deposits; C3 glomerulopathy; CFHR5; Complement; Dense deposit disease; Factor I

Indexed keywords

COMPLEMENT COMPONENT C1Q; COMPLEMENT MEMBRANE ATTACK COMPLEX; CORTICOSTEROID; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; NEPHRITIC FACTOR;

ADULT; ARTHRALGIA; ARTICLE; BOWMAN CAPSULE; CASE REPORT; CELL PROLIFERATION; CHILD; CORTICOSTEROID THERAPY; DENSE DEPOSIT DISEASE; ELECTRON MICROSCOPY; END STAGE RENAL DISEASE; ERYTHEMA INFECTIOSUM; FAMILY HISTORY; FEMALE; FEVER; FIBROSING ALVEOLITIS; FOLLOW UP; GENERALIZED EDEMA; GENETIC ANALYSIS; GENETIC VARIABILITY; GLOMERULUS BASEMENT MEMBRANE; HEMATURIA; HUMAN; INFLAMMATORY CELL; KIDNEY BIOPSY; KIDNEY FUNCTION; KIDNEY TUBULE BASEMENT MEMBRANE; LIPODYSTROPHY; MALE; MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS; MESANGIUM CELL; MILD RENAL IMPAIRMENT; NEPHROTIC SYNDROME; PRESCHOOL CHILD; PROTEINURIA; SCHOOL CHILD; VIRUS INFECTION; YOUNG ADULT; ADOLESCENT; DISEASE COURSE; GLOMERULONEPHRITIS; GLOMERULUS; KIDNEY FAILURE; PATHOLOGY;

ADOLESCENT; ADULT; CHILD; DISEASE PROGRESSION; FEMALE; FOLLOW-UP STUDIES; GLOMERULONEPHRITIS; GLOMERULONEPHRITIS, MEMBRANOPROLIFERATIVE; HUMANS; KIDNEY GLOMERULUS; MALE; NEPHROTIC SYNDROME; RENAL INSUFFICIENCY; YOUNG ADULT;

EID: 84908338323     PISSN: 00468177     EISSN: 15328392     Source Type: Journal    
DOI: 10.1016/j.humpath.2014.07.021     Document Type: Article

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