Fatal human herpesvirus 6-associated encephalitis in two boys with underlying POLG mitochondrial disorders

Pediatric Neurology

Volumn 51, Issue 3, 2014, Pages 448-452

  Al Zubeidi, Duha ^a   Thangarajh, Mathula ^b   Pathak, Sheel ^c   Cai, Chunyu ^c   Schlaggar, Bradley L ^c   Storch, Gregory A ^d   Grange, Dorothy K ^d   Watson Jr , Michael E ^e  

^a CHILDREN S MERCY HOSPITAL   (United States)

^b CHILDREN'S NATIONAL MEDICAL CENTER   (United States)

^c WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d WASHINGTON UNIVERSITY   (United States)

^e UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

Author keywords

child; encephalitis; human herpesvirus 6 (HHV 6); POLG

Indexed keywords

ANTICONVULSIVE AGENT; GANCICLOVIR; DNA DIRECTED DNA POLYMERASE; POLG PROTEIN, HUMAN;

ALPERS DISEASE; ARTICLE; AUTOPSY; BLOOD ANALYSIS; BRAIN DISEASE; CASE REPORT; CEREBROSPINAL FLUID ANALYSIS; CHILD; DISEASE COURSE; DISEASE EXACERBATION; DISEASE SEVERITY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FATALITY; GENE; GENE MUTATION; HERPES VIRUS; HUMAN; HUMAN HERPESVIRUS 6; HUMAN TISSUE; INFANT; INTRACTABLE EPILEPSY; KIDNEY FAILURE; LIVER FAILURE; MALE; MOTOR DYSFUNCTION; MYOCLONUS SEIZURE; PHENOTYPE; POLG GENE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; VIRUS ENCEPHALITIS; VIRUS LOAD; BRAIN; COMPLICATION; ENCEPHALITIS, VIRAL; GENETICS; PATHOLOGY; PATHOPHYSIOLOGY; ROSEOLOVIRUS INFECTIONS;

BRAIN; DNA-DIRECTED DNA POLYMERASE; ENCEPHALITIS, VIRAL; FATAL OUTCOME; HERPESVIRUS 6, HUMAN; HUMANS; INFANT; MALE; MITOCHONDRIAL DISEASES; MOVEMENT DISORDERS; ROSEOLOVIRUS INFECTIONS;

EID: 84907347252     PISSN: 08878994     EISSN: 18735150     Source Type: Journal    
DOI: 10.1016/j.pediatrneurol.2014.04.006     Document Type: Article

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