IgG4- related disease: An orphan disease with many faces

Orphanet Journal of Rare Diseases

Volumn 9, Issue 1, 2014, Pages

  Pieringer, Herwig ^a,b   Parzer, Ilse ^c   Wöhrer, Adelheid ^d   Reis, Petra ^e   Oppl, Bastian ^c   Zwerina, Jochen ^c  

^a KEPLER UNIVERSITY HOSPITAL   (Austria)

^b PARACELSUS MEDICAL UNIVERSITY   (Austria)

^c HANUSCH HOSPITAL   (Austria)

^d MEDICAL UNIVERSITY OF VIENNA   (Austria)

^e UNIVERSITY OF ERLANGEN NUREMBERG   (Germany)

Author keywords

IgG4 RD; Immunoglobulin 4; Lymphoplasmacytic inflammation; Storiform fibrosis

Indexed keywords

BORTEZOMIB; CYCLOPHOSPHAMIDE; FLUDARABINE; GLUCOCORTICOID; PREDNISOLONE; RITUXIMAB; AZATHIOPRINE; CHLORAMBUCIL; IMMUNOGLOBULIN G; IMMUNOGLOBULIN G4; PREDNISONE;

ANGIOFOLLICULAR LYMPH NODE HYPERPLASIA; AUTOIMMUNE HEPATITIS; CHOLANGITIS; CHRONIC PANCREATITIS; CORTICOSTEROID THERAPY; DACRYOCYSTITIS; HEMATOLOGIC DISEASE; HUMAN; IMMUNOGLOBULIN G4 RELATED DISEASE; INTENSIVE CARE; INTERSTITIAL NEPHRITIS; LYMPHOMA; METASTASIS; OBSTRUCTIVE JAUNDICE; ORBIT TUMOR; PATHOPHYSIOLOGY; RETROPERITONEAL FIBROSIS; REVIEW; SIALOADENITIS; SIALOLITHIASIS; THYROIDITIS; ADULT; CASE REPORT; CHEMORADIOTHERAPY; DRY EYE; ENUCLEATION; EOSINOPHILIA; EXTRAOCULAR MUSCLE; FEMALE; HUMAN TISSUE; LYMPHADENOPATHY; LYMPHOCYTIC INFILTRATION; MIDDLE AGED; ORBIT PSEUDOTUMOR; PAROTID GLAND; PHLEBITIS; PHYSICAL EXAMINATION; PLASMA CELL; PSEUDOLYMPHOMA; SJOEGREN SYNDROME; SUBMANDIBULAR GLAND; XEROSTOMIA; IMMUNOLOGY; RARE DISEASES;

HUMANS; IMMUNOGLOBULIN G; RARE DISEASES;

EID: 84906537154     PISSN: None     EISSN: 17501172     Source Type: Journal    
DOI: 10.1186/s13023-014-0110-z     Document Type: Review

References (129)

1. Mikulicz J: Über eine eigenartige symmetrische Erkrankung der Tränen und Mundspeicheldrüsen. In Beitr Chir Fortsch Gewidmet Theodor Billroth. Stuttgart: ; 1892:610-630.
2. Über entzündliche Tumoren der submaxillär- speicheldrüse. H Küttner, Beitr Klin Chir 1896 15 815 834
3. Die chronische zur Bildung eisenharter Tumoren fuehrende Entzuendung der Schilddruese. BM Riedel, Verh Ges Chir 1896 25 101 105
4. Sclerosing cholangitis: its possible association with Riedel's struma and fibrous retroperitonitis: report of two cases. LG Bartholomew, JC Cain, LB Woolner, DC Utz, DO Ferris, N Engl J Med 1963 269 8 12 13969693
5. Chronic pancreatitis caused by an autoimmune abnormality. Proposal of the concept of autoimmune pancreatitis. K Yoshida, F Toki, T Takeuchi, S Watanabe, K Shiratori, N Hayashi, Dig Dis Sci 1995 40 1561 1568 7628283
6. High serum IgG4 concentrations in patients with sclerosing pancreatitis. H Hamano, S Kawa, A Horiuchi, H Unno, N Furuya, T Akamatsu, M Fukushima, T Nikaido, K Nakayama, N Usuda, K Kiyosawa, N Engl J Med 2001 344 732 738 11236777 (Pubitemid 32204991)
7. Hydronephrosis associated with retroperitoneal fibrosis and sclerosing pancreatitis. H Hamano, S Kawa, Y Ochi, H Unno, N Shiba, M Wajiki, K Nakazawa, H Shimojo, K Kiyosawa, Lancet 2002 359 1403 1404 11978339 (Pubitemid 34442382)
8. Diagnosis of autoimmune pancreatitis: the Mayo Clinic experience. ST Chari, TC Smyrk, MJ Levy, MD Topazian, N Takahashi, L Zhang, JE Clain, RK Pearson, BT Petersen, SS Vege, MB Farnell, Clin Gastroenterol Hepatol 2006 4 1010 1016 16843735 (Pubitemid 44118845)
9. Review of 67 patients with autoimmune pancreatitis in Korea: a multicenter nationwide study. JK Ryu, JB Chung, SW Park, JK Lee, KT Lee, WJ Lee, JH Moon, KB Cho, DW Kang, JH Hwang, KS Yoo, BM Yoo, DH Lee, HK Kim, YS Moon, J Lee, HS Lee, HS Choi, SK Lee, YT Kim, CD Kim, SJ Kim, JS Hahm, YB Yoon, Pancreas 2008 37 377 385 18953249
10. Recommendations for the nomenclature of IgG4-related disease and its individual organ system manifestations. JH Stone, A Khosroshahi, V Deshpande, JK Chan, JG Heathcote, R Aalberse, A Azumi, DB Bloch, WR Brugge, MN Carruthers, W Cheuk, L Cornell, CF Castillo, JA Ferry, D Forcione, G Klöppel, DL Hamilos, T Kamisawa, S Kasashima, S Kawa, M Kawano, Y Masaki, K Notohara, K Okazaki, JK Ryu, T Saeki, D Sahani, Y Sato, T Smyrk, JR Stone, et al. Arthritis Rheum 2012 64 3061 3067 22736240
11. Histopathological findings in 29 lymph node biopsies with increased IgG4 plasma cells. KE Grimm, TS Barry, V Chizhevsky, A Hii, LM Weiss, IN Siddiqi, RK Brynes, DP O'Malley, Mod Pathol 2012 25 480 489 22080064
12. Retroperitoneal and aortic manifestations of immunoglobulin G4-related disease. Y Zen, S Kasashima, D Inoue, Semin Diagn Pathol 2012 29 212 218 23068300
13. Membranous glomerulonephritis is a manifestation of IgG4-related disease. MP Alexander, CP Larsen, IW Gibson, SH Nasr, S Sethi, ME Fidler, Y Raissian, N Takahashi, S Chari, TC Smyrk, LD Cornell, Kidney Int 2013 83 455 462 23254897
14. The immunobiology and clinical characteristics of IgG4 related diseases. H Takahashi, M Yamamoto, T Tabeya, C Suzuki, Y Naishiro, Y Shinomura, K Imai, J Autoimmun 2012 39 93 96 22341851
15. Immunohistochemical Characteristics of IgG4-Related Tubulointerstitial Nephritis: Detailed Analysis of 20 Japanese Cases. M Kawano, I Mizushima, Y Yamaguchi, N Imai, H Nakashima, S Nishi, S Hisano, N Yamanaka, M Yamamoto, H Takahashi, H Umehara, T Saito, T Saeki, Int J Rheumatol 2012 2012 609795 22899937
16. Prevalence of atopy, eosinophilia, and IgE elevation in IgG4-related disease. E Della Torre, H Mattoo, VS Mahajan, M Carruthers, S Pillai, JH Stone, Allergy 2013 [Epub ahead of print]
17. Pathologies Associated with Serum IgG4 Elevation. M Ebbo, A Grados, E Bernit, F Vély, J Boucraut, JR Harlé L Daniel, N Schleinitz, Int J Rheumatol 2012 2012 602809 22966232
18. The diagnostic utility of serum IgG4 concentrations in IgG4-related disease. MN Carruthers, A Khosroshahi, T Augustin, V Deshpande, JH Stone, Ann Rheum Dis 2014 [Epub ahead of print]
19. Serum Immunoglobulin G4 Level Is a Poor Predictor of Immunoglobulin G4-Related Disease. TN Ngwa, R Law, D Murray, ST Chari, Pancreas 2014 43 704 707 24632552
20. Brief Report: spuriously low serum IgG4 concentrations caused by the prozone phenomenon in patients with IgG4-related disease. A Khosroshahi, LA Cheryk, MN Carruthers, JA Edwards, DB Bloch, JH Stone, Arthritis Rheumatol 2014 66 213 217 24431286
21. The pathology of IgG4-related disease: critical issues and challenges. V Deshpande, Semin Diagn Pathol 2012 29 191 196 23068297
22. Comprehensive diagnostic criteria for IgG4-related disease (IgG4-RD), 2011. H Umehara, K Okazaki, Y Masaki, M Kawano, M Yamamoto, T Saeki, S Matsui, T Yoshino, S Nakamura, S Kawa, H Hamano, T Kamisawa, T Shimosegawa, A Shimatsu, S Nakamura, T Ito, K Notohara, T Sumida, Y Tanaka, T Mimori, T Chiba, M Mishima, T Hibi, H Tsubouchi, K Inui, H Ohara, Mod Rheumatol 2012 22 21 30 22218969
23. Proposal for diagnostic criteria for IgG4-related kidney disease. M Kawano, T Saeki, H Nakashima, S Nishi, Y Yamaguchi, S Hisano, N Yamanaka, D Inoue, M Yamamoto, H Takahashi, H Nomura, T Taguchi, H Umehara, H Makino, T Saito, Clin Exp Nephrol 2011 15 615 626 21898030
24. International consensus diagnostic criteria for autoimmune pancreatitis: guidelines of the International Association of Pancreatology. T Shimosegawa, ST Chari, L Frulloni, T Kamisawa, S Kawa, M Mino-Kenudson, MH Kim, G Klöppel, MM Lerch, M Löhr, K Notohara, K Okazaki, A Schneider, L Zhang, Pancreas 2011 40 352 358 21412117
25. Prevalence of IgG4-Related Disease in Japan Based on Nationwide Survey in 2009. K Uchida, A Masamune, T Shimosegawa, K Okazaki, Int J Rheumatol 2012 2012 358371 22899936
26. HLA DRB10405-DQB10401 haplotype is associated with autoimmune pancreatitis in the Japanese population. S Kawa, M Ota, K Yoshizawa, A Horiuchi, H Hamano, Y Ochi, K Nakayama, Y Tokutake, Y Katsuyama, S Saito, O Hasebe, K Kiyosawa, Gastroenterology 2002 122 1264 1269 11984513 (Pubitemid 34465169)
27. Genetic association of Fc receptor-like 3 polymorphisms with autoimmune pancreatitis in Japanese patients. T Umemura, M Ota, H Hamano, Y Katsuyama, K Kiyosawa, S Kawa, Gut 2006 55 1367 1368 16905709 (Pubitemid 44277378)
28. T-cell regulatory gene CTLA-4 polymorphism/haplotype association with autoimmune pancreatitis. MC Chang, YT Chang, YW Tien, PC Liang, IS Jan, SC Wei, JM Wong, Clin Chem 2007 53 1700 1705 17712006
29. Identification of a novel antibody associated with autoimmune pancreatitis. L Frulloni, C Lunardi, R Simone, M Dolcino, C Scattolini, M Falconi, L Benini, I Vantini, R Corrocher, A Puccetti, N Engl J Med 2009 361 2135 2142 19940298
30. Autoantibodies in autoimmune pancreatitis. DS Smyk, EI Rigopoulou, AL Koutsoumpas, S Kriese, AK Burroughs, DP Bogdanos, Int J Rheumatol 2012 2012 940831 22844291
31. Serum antibodies to carbonic anhydrase IV in patients with autoimmune pancreatitis. I Nishimori, E Miyaji, K Morimoto, K Nagao, M Kamada, S Onishi, Gut 2005 54 274 281 15647194 (Pubitemid 40139246)
32. Increased T-helper 2 cytokines in bile from patients with IgG4-related cholangitis disrupt the tight junction-associated biliary epithelial cell barrier. T Müller, C Beutler, AH Picó M Otten, A Dürr, H Al-Abadi, O Guckelberger, D Meyer Zum Büschenfelde, K Jöhrens, M Volkmann, T Lankisch, T Voigtländer, M Anders, O Shibolet, DM Jefferson, DK Podolsky, A Fischer, W Veltzke-Schlieker, A Adler, DC Baumgart, A Sturm, B Wiedenmann, E Schott, T Berg, Gastroenterology 2013 144 1116 28 23391819
33. The Clinical and Pathological Features of IgG(4)-Related Disease. A Khosroshahi, V Deshpande, JH Stone, Curr Rheumatol Rep 2011 13 473 481 21964954
34. Th2 and regulatory immune reactions contribute to IgG4 production and the initiation of Mikulicz disease. A Tanaka, M Moriyama, H Nakashima, K Miyake, JN Hayashida, T Maehara, S Shinozaki, Y Kubo, S Nakamura, Arthritis Rheum 2012 64 254 263 21898360
35. An amplification of IL-10 and TGF-beta in patients with IgG4-related tubulointerstitial nephritis. H Nakashima, K Miyake, M Moriyama, A Tanaka, M Watanabe, Y Abe, H Sato, S Nakamura, T Saito, Clin Nephrol 2010 73 385 391 20420800
36. Analysis of IgG4 class switch-related molecules in IgG4-related disease. H Tsuboi, N Matsuo, M Iizuka, S Tsuzuki, Y Kondo, A Tanaka, M Moriyama, I Matsumoto, S Nakamura, T Sumida, Arthritis Res Ther 2012 14 171 22824292
37. Studies on human antibodies. VI. Selective variations in subgroup composition and genetic markers. WJ Yount, MM Dorner, HG Kunkel, EA Kabat, J Exp Med 1968 127 633 646 4169968
38. Anti-inflammatory activity of human IgG4 antibodies by dynamic Fab arm exchange. KM van der Neut, J Schuurman, M Losen, WK Bleeker, P Martínez-Martínez, E Vermeulen, TH den Bleker, L Wiegman, T Vink, LA Aarden, MH De Baets, JG van de Winkel, RC Aalberse, PW Parren, Science 2007 317 1554 1557 (Pubitemid 47417435)
39. M-type phospholipase A2 receptor as target antigen in idiopathic membranous nephropathy. LH Beck Jr, RG Bonegio, G Lambeau, DM Beck, DW Powell, TD Cummins, JB Klein, DJ Salant, N Engl J Med 2009 361 11 21 19571279
40. IgG subclass distribution of anti-ADAMTS13 antibodies in patients with acquired thrombotic thrombocytopenic purpura. S Ferrari, GC Mudde, M Rieger, A Veyradier, JA Kremer Hovinga, F Scheiflinger, J Thromb Haemost 2009 7 1703 1710 19682238
41. Deposition of complement C3c, immunoglobulin (Ig)G4 and IgG at the basement membrane of pancreatic ducts and acini in autoimmune pancreatitis. S Detlefsen, JH Bräsen, G Zamboni, P Capelli, G Klöppel, Histopathology 2010 57 825 835 21166697
42. De novo oligoclonal expansions of circulating plasmablasts in active and relapsing IgG4-related disease. H Mattoo, VS Mahajan, E Della-Torre, Y Sekigami, M Carruthers, ZS Wallace, V Deshpande, JH Stone, S Pillai, J Allergy Clin Immunol. 2014 [Epub ahead of print] 24815737
43. Plasmablasts as a biomarker for IgG4-related disease, independent of serum IgG4 concentrations. ZS Wallace, H Mattoo, M Carruthers, VS Mahajan, E Della Torre, H Lee, M Kulikova, V Deshpande, S Pillai, JH Stone, Ann Rheum Dis. 2014 [Epub ahead of print]
44. Subclassification of autoimmune pancreatitis: a histologic classification with clinical significance. V Deshpande, R Gupta, N Sainani, DV Sahani, R Virk, C Ferrone, A Khosroshahi, JH Stone, GY Lauwers, Am J Surg Pathol 2011 35 26 35 21164284
45. Type 1 autoimmune pancreatitis. Y Zen, DP Bogdanos, S Kawa, Orphanet J Rare Dis 2011 6 82 22151922
46. Differences in clinical profile and relapse rate of type 1 versus type 2 autoimmune pancreatitis. RP Sah, ST Chari, R Pannala, A Sugumar, JE Clain, MJ Levy, RK Pearson, TC Smyrk, BT Petersen, MD Topazian, N Takahashi, MB Farnell, SS Vege, Gastroenterology 2010 139 140 148 20353791
47. Autoimmune pancreatitis: imaging features. DV Sahani, SP Kalva, J Farrell, MM Maher, S Saini, PR Mueller, GY Lauwers, CD Fernandez, AL Warshaw, JF Simeone, Radiology 2004 233 345 352 15459324 (Pubitemid 39423790)
48. Autoimmune pancreatitis: a guide for the histopathologist. S Shinagare, AB Shinagare, V Deshpande, Semin Diagn Pathol 2012 29 197 204 23068298
49. Strategy to differentiate autoimmune pancreatitis from pancreas cancer. K Takuma, T Kamisawa, R Gopalakrishna, S Hara, T Tabata, Y Inaba, N Egawa, Y Igarashi, World J Gastroenterol 2012 18 1015 1020 22416175
50. Results of pancreaticoduodenectomy for lymphoplasmacytic sclerosing pancreatitis. JM Hardacre, CA Iacobuzio-Donahue, TA Sohn, SC Abraham, CJ Yeo, KD Lillemoe, MA Choti, KA Campbell, RD Schulick, RH Hruban, JL Cameron, SD Leach, Ann Surg 2003 237 853 858 12796582
51. Does autoimmune pancreatitis increase the risk of pancreatic carcinoma?: a retrospective analysis of pancreatic resections. R Gupta, A Khosroshahi, S Shinagare, C Fernandez, C Ferrone, GY Lauwers, JH Stone, V Deshpande, Pancreas 2013 42 506 510 23271394
52. Immunoglobulin G4-associated cholangitis: clinical profile and response to therapy. A Ghazale, ST Chari, L Zhang, TC Smyrk, N Takahashi, MJ Levy, MD Topazian, JE Clain, RK Pearson, BT Petersen, SS Vege, K Lindor, MB Farnell, Gastroenterology 2008 134 706 715 18222442 (Pubitemid 351312724)
53. Immunoglobulin G4-related sclerosing cholangitis: pathologic features and histologic mimics. Y Zen, Y Nakanuma, B Portmann, Semin Diagn Pathol 2012 29 205 211 23068299
54. Autoimmune pancreatitis-related cholecystitis: a morphologically and immunologically distinctive form of lymphoplasmacytic sclerosing cholecystitis. WL Wang, AB Farris, GY Lauwers, V Deshpande, Histopathology 2009 54 829 836 19635102
55. Immunoglobin G4-hepatopathy: association of immunoglobin G4-bearing plasma cells in liver with autoimmune pancreatitis. T Umemura, Y Zen, H Hamano, S Kawa, Y Nakanuma, K Kiyosawa, Hepatology 2007 46 463 471 17634963 (Pubitemid 47344782)
56. Clinical significance of immunoglobulin G4-associated autoimmune hepatitis. T Umemura, Y Zen, H Hamano, S Joshita, T Ichijo, K Yoshizawa, K Kiyosawa, M Ota, S Kawa, Y Nakanuma, E Tanaka, J Gastroenterol 2011 46 Suppl 1 48 55 20862498
57. Differentiating immunoglobulin g4-related sclerosing cholangitis from hilar cholangiocarcinoma. T Tabata, T Kamisawa, S Hara, S Kuruma, K Chiba, G Kuwata, T Fujiwara, H Egashira, K Koizumi, J Fujiwara, T Arakawa, K Momma, M Kurata, G Honda, K Tsuruta, T Itoi, Gut Liver 2013 7 234 238 23560161
58. Clinical and histopathological study of follicular cholangitis: Sclerosing cholangitis with prominent lymphocytic infiltration masquerading as hilar cholangiocarcinoma. T Fujita, M Kojima, Y Kato, N Gotohda, S Takahashi, M Konishi, T Kinoshita, Hepatol Res 2010 40 1239 1247 20880060
59. IgG4+ plasma cell infiltrates in liver explants with primary sclerosing cholangitis. L Zhang, JT Lewis, SC Abraham, TC Smyrk, S Leung, ST Chari, JJ Poterucha, CB Rosen, CM Lohse, JA Katzmann, TT Wu, Am J Surg Pathol 2010 34 88 94 20035148
60. Sclerosing cholangitis with granulocytic epithelial lesion: a benign form of sclerosing cholangiopathy. Y Zen, T Grammatikopoulos, MA Heneghan, D Vergani, G Mieli-Vergani, BC Portmann, Am J Surg Pathol 2012 36 1555 1561 22982898
61. Riedel's thyroiditis and multifocal fibrosclerosis are part of the IgG4-related systemic disease spectrum. M Dahlgren, A Khosroshahi, GP Nielsen, V Deshpande, JH Stone, Arthritis Care Res (Hoboken) 2010 62 1312 1318
62. Riedel's thyroiditis: a clinical review. JV Hennessey, J Clin Endocrinol Metab 2011 96 3031 3041 21832114
63. Invasive fibrous thyroiditis (Riedel thyroiditis): the Mayo Clinic experience, 1976-2008. MM Fatourechi, ID Hay, B McIver, TJ Sebo, V Fatourechi, Thyroid 2011 21 765 772 21568724
64. Radiology quiz case 1. Riedel thyroiditis. S Gaddikeri, PR Chapman, Arch Otolaryngol Head Neck Surg 2012 138 867 868 22986723
65. Fibrosing variant of Hashimoto thyroiditis is an IgG4 related disease. V Deshpande, A Huck, E Ooi, JH Stone, WC Faquin, GP Nielsen, J Clin Pathol 2012 65 725 728 22659333
66. Evaluation and Clinical Validity of a New Questionnaire for Mikulicz's Disease. M Yamamoto, H Takahashi, K Ishigami, H Yajima, Y Shimizu, T Tabeya, M Matsui, C Suzuki, Y Naishiro, H Yamamoto, K Imai, Y Shinomura, Int J Rheumatol 2012 2012 283459 22649453
67. A new conceptualization for Mikulicz's disease as an IgG4-related plasmacytic disease. M Yamamoto, H Takahashi, M Ohara, C Suzuki, Y Naishiro, H Yamamoto, Y Shinomura, K Imai, Mod Rheumatol 2006 16 335 340 17164992 (Pubitemid 44921578)
68. Clinical and pathological characteristics of IgG4-related sclerosing sialadenitis. N Ohta, K Kurakami, A Ishida, T Furukawa, F Saito, S Kakehata, K Izuhara, Laryngoscope 2012 122 572 577 22241660
69. IgG4-related disease in the head and neck. JA Ferry, V Deshpande, Semin Diagn Pathol 2012 29 235 244 23068303
70. Abundant IgG4-positive plasma cell infiltration characterizes chronic sclerosing sialadenitis (Küttner's tumor). S Kitagawa, Y Zen, K Harada, M Sasaki, Y Sato, H Minato, K Watanabe, H Kurumaya, K Katayanagi, S Masuda, H Niwa, K Tsuneyama, K Saito, J Haratake, K Takagawa, Y Nakanuma, Am J Surg Pathol 2005 29 783 791 15897744 (Pubitemid 40734427)
71. Chronic sclerosing sialadenitis (Küttner tumor) is an IgG4-associated disease. JT Geyer, JA Ferry, NL Harris, JH Stone, LR Zukerberg, GY Lauwers, BZ Pilch, V Deshpande, Am J Surg Pathol 2010 34 202 210 20061932
72. A clinicopathologic study of Mikulicz's disease. WS Morgan, B Castelman, Am J Pathol 1953 29 471 503 13040489
73. Proposal for a new clinical entity, IgG4-positive multiorgan lymphoproliferative syndrome: analysis of 64 cases of IgG4-related disorders. Y Masaki, L Dong, N Kurose, K Kitagawa, Y Morikawa, M Yamamoto, H Takahashi, Y Shinomura, K Imai, T Saeki, A Azumi, S Nakada, E Sugiyama, S Matsui, T Origuchi, S Nishiyama, I Nishimori, T Nojima, K Yamada, M Kawano, Y Zen, M Kaneko, K Miyazaki, K Tsubota, K Eguchi, K Tomoda, T Sawaki, T Kawanami, M Tanaka, T Fukushima, et al. Ann Rheum Dis 2009 68 1310 1315 18701557
74. Clinical Aspects of IgG4-Related Orbital Inflammation in a Case Series of Ocular Adnexal Lymphoproliferative Disorders. M Takahira, Y Ozawa, M Kawano, Y Zen, S Hamaoka, K Yamada, K Sugiyama, Int J Rheumatol 2012 2012 635473 22548072
75. Orbital IgG4-Related Disease: clinical features and diagnosis. T Kubota, S Moritani, ISRN Rheumatol 2012 2012 412896 22778989
76. Idiopathic fibroinflammatory disease of the face, eyelids, and periorbital membrane with immunoglobulin G4-positive plasma cells. M Mehta, F Jakobiec, A Fay, Arch Pathol Lab Med 2009 133 1251 1255 19653720
77. A unique case of IgG4 sclerosing dacryocystitis. R Batra, HS Mudhar, S Sandramouli, Ophthal Plast Reconstr Surg 2012 28 70 e72 21946772
78. Locally destructive skull base lesion: IgG4-related sclerosing disease. JA Alt, GT Whitaker, RW Allan, M Vaysberg, Allergy Rhinol (Providence) 2012 3 41 e45
79. Ocular adnexal IgG4-related disease: CT and MRI findings. YS Song, HK Choung, SW Park, JH Kim, SI Khwarg, YK Jeon, Br J Ophthalmol 2013 97 412 418 23385629
80. Retroperitoneal fibrosis. N Pipitone, A Vaglio, C Salvarani, Best Pract Res Clin Rheumatol 2012 26 439 448 23040359
81. Immunoglobulin G4-related periaortitis and periarteritis: CT findings in 17 patients. D Inoue, Y Zen, H Abo, T Gabata, H Demachi, J Yoshikawa, S Miyayama, Y Nakanuma, O Matsui, Radiology 2011 261 625 633 21803920
82. Ruptured abdominal aortic aneurysm related to IgG4 periaortitis. Q Qian, KB Kashani, DV Miller, N Engl J Med 2009 361 1121 1123 19741239
83. Positron emission tomography (PET): evaluation of chronic periaortitis. C Salvarani, N Pipitone, A Versari, A Vaglio, D Serafini, G Bajocchi, D Salvo, C Buzio, P Greco, L Boiardi, Arthritis Rheum 2005 53 298 303 15818649 (Pubitemid 40530173)
84. Rethinking Ormond's disease: idiopathic retroperitoneal fibrosis in the era of IgG4-related disease. A Khosroshahi, MN Carruthers, JH Stone, S Shinagare, N Sainani, RP Hasserjian, V Deshpande, Medicine (Baltimore) 2013 92 82 91
85. A new clinicopathological entity of IgG4-related inflammatory abdominal aortic aneurysm. S Kasashima, Y Zen, A Kawashima, M Endo, Y Matsumoto, F Kasashima, J Vasc Surg 2009 49 1264 1271 19217746
86. IgG4-related systemic disease accounts for a significant proportion of thoracic lymphoplasmacytic aortitis cases. JH Stone, A Khosroshahi, V Deshpande, JR Stone, Arthritis Care Res (Hoboken) 2010 62 316 322
87. A clinicopathologic study of immunoglobulin G4-related disease of the femoral and popliteal arteries in the spectrum of immunoglobulin G4-related periarteritis. S Kasashima, A Kawashima, M Endo, Y Matsumoto, F Kasashima, Y Zen, Y Nakanuma, J Vasc Surg 2013 57 816 822 23159475
88. Pathologic manifestations of Immunoglobulin(Ig)G4-related lung disease. ES Yi, H Sekiguchi, T Peikert, JH Ryu, TV Colby, Semin Diagn Pathol 2012 29 219 225 23068301
89. Immunoglobulin G4-related lung disease: CT findings with pathologic correlations. D Inoue, Y Zen, H Abo, T Gabata, H Demachi, T Kobayashi, J Yoshikawa, S Miyayama, M Yasui, Y Nakanuma, O Matsui, Radiology 2009 251 260 270 19221056
90. Pulmonary manifestations of immunoglobulin G4-related sclerosing disease. JH Ryu, H Sekiguchi, ES Yi, Eur Respir J 2012 39 180 186 21719489
91. Clinical features of central airway involvement in autoimmune pancreatitis. H Yamamoto, M Yasuo, M Ito, T Yokoyama, H Hamano, T Uehara, S Kawakami, K Kubo, Eur Respir J 2011 38 1233 1236 22045794
92. IgG4-related lung and pleural disease: a clinicopathologic study of 21 cases. Y Zen, D Inoue, A Kitao, M Onodera, H Abo, S Miyayama, T Gabata, O Matsui, Y Nakanuma, Am J Surg Pathol 2009 33 1886 1893 19898222
93. Lymphadenopathy of IgG4-related sclerosing disease. W Cheuk, HK Yuen, SY Chu, EK Chiu, LK Lam, JK Chan, Am J Surg Pathol 2008 32 671 681 18344866 (Pubitemid 351600815)
94. IgG4-Related Lymphadenopathy. Y Sato, T Yoshino, Int J Rheumatol 2012 2012 572539 22719769
95. Clinicopathological characteristics of patients with IgG4-related tubulointerstitial nephritis. T Saeki, S Nishi, N Imai, T Ito, H Yamazaki, M Kawano, M Yamamoto, H Takahashi, S Matsui, S Nakada, T Origuchi, A Hirabayashi, N Homma, Y Tsubata, T Takata, Y Wada, A Saito, S Fukase, K Ishioka, K Miyazaki, Y Masaki, H Umehara, S Sugai, I Narita, Kidney Int 2010 78 1016 1023 20720530
96. IgG4-related kidney disease. LD Cornell, Semin Diagn Pathol 2012 29 245 250 23068304
97. Renal involvement in patients with autoimmune pancreatitis: CT and MR imaging findings. N Takahashi, A Kawashima, JG Fletcher, ST Chari, Radiology 2007 242 791 801 17229877
98. IgG4-related kidney disease. LD Cornell, Curr Opin Nephrol Hypertens 2012 21 279 288 22487688
99. IgG4-Related Disease Is Not Associated with Antibody to the Phospholipase A2 Receptor. A Khosroshahi, R Ayalon, LH Beck Jr, DJ Salant, DB Bloch, JH Stone, Int J Rheumatol 2012 2012 139409 22654915
100. IgG4-Related Perineural Disease. D Inoue, Y Zen, Y Sato, H Abo, H Demachi, A Uchiyama, T Gabata, O Matsui, Int J Rheumatol 2012 2012 401890 22523496
101. IgG4-related hypophysitis: a new addition to the hypophysitis spectrum. P Leporati, MA Landek-Salgado, I Lupi, L Chiovato, P Caturegli, J Clin Endocrinol Metab 2011 96 1971 1980 21593109
102. IgG4-associated multifocal systemic fibrosis complicating sclerosing sialadenitis, hypophysitis, and retroperitoneal fibrosis, but lacking pancreatic involvement. T Tanabe, K Tsushima, M Yasuo, K Urushihata, M Hanaoka, T Koizumi, K Fujimoto, K Kubo, T Uehara, S Shigematsu, H Hamano, S Kawa, Intern Med 2006 45 1243 1247 17139126 (Pubitemid 44848861)
103. Inflammatory pseudotumors of the central nervous system. PC Lui, YS Fan, SS Wong, AN Chan, G Wong, TK Chau, GM Tse, Y Cheng, WS Poon, HK Ng, Hum Pathol 2009 40 1611 1617 19656549
104. Wallace ZS, Carruthers MN, Khosroshahi A, Carruthers R, Shinagare S, Stemmer-Rachamimov A, Deshpande V, Stone JH: IgG4-Related Disease and Hypertrophic Pachymeningitis. Medicine (Baltimore)2013,: [Epub ahead of print].
105. Idiopathic cervical fibrosis-a new member of IgG4-related sclerosing diseases: report of 4 cases, 1 complicated by composite lymphoma. W Cheuk, FK Tam, AN Chan, IS Luk, AP Yuen, WK Chan, TC Hung, JK Chan, Am J Surg Pathol 2010 34 1678 1685 20871392
106. IgG4-related sclerosing mastitis: description of a new member of the IgG4-related sclerosing diseases. W Cheuk, AC Chan, WL Lam, SM Chow, P Crowley, R Lloydd, I Campbell, M Thorburn, JK Chan, Am J Surg Pathol 2009 3 1058 1064
107. IgG4-related autoimmune prostatitis: two cases with or without autoimmune pancreatitis. I Nishimori, T Kohsaki, S Onishi, T Shuin, S Kohsaki, Y Ogawa, M Matsumoto, M Hiroi, H Hamano, S Kawa, Intern Med 2007 46 1983 1989 18084121
108. Migita K, Miyashita T, Mizuno A, Jiuchi Y, Ito M, Matsuo M, Izumi Y, Takeoka A, Nishino A, Hayashi M: IgG4-related epididymo-orchitis associated with bladder cancer: possible involvement of BAFF/BAFF-R interaction in IgG4-related urogenital disease. Mod Rheumatol 2012,: [Epub ahead of print].
109. IgG4-related paratesticular pseudotumor in a patient with autoimmune pancreatitis and retroperitoneal fibrosis: an extrapancreatic manifestation of IgG4-related disease. PA Hart, AM Moyer, ES Yi, MC Hogan, RK Pearson, ST Chari, Hum Pathol 2012 43 2084 2087 22974477
110. Clinicopathologic analysis of IgG4-related skin disease. Y Sato, M Takeuchi, K Takata, K Ohno, N Iwaki, Y Orita, N Goto, AI Hida, T Iwamoto, N Asano, T Ito, H Hanakawa, H Yanai, T Yoshino, Mod Pathol 2013 26 523 532 23174935
111. Constrictive pericarditis as an emerging manifestation of hyper-IgG4 disease. T Sugimoto, Y Morita, K Isshiki, T Yamamoto, T Uzu, A Kashiwagi, M Horie, T Asai, Int J Cardiol 2008 130 100 e101 17727980
112. IgG4-related systemic disease presenting with lung entrapment and constrictive pericarditis. H Sekiguchi, R Horie, JP Utz, JH Ryu, Chest 2012 142 781 783 22948582
113. Eosinophilic angiocentric fibrosis is a form of IgG4-related systemic disease. V Deshpande, A Khosroshahi, GP Nielsen, DL Hamilos, JH Stone, Am J Surg Pathol 2011 35 701 706 21502911
114. A case of IgG4-related dacryoadenitis that regressed without systemic steroid administration. K Ohshima, Y Sato, T Yoshino, J Clin Exp Hematop 2013 53 53 56 23801134
115. Relapse patterns in IgG4-related disease. M Yamamoto, H Takahashi, K Ishigami, H Yajima, Y Shimizu, T Tabeya, M Matsui, C Suzuki, Y Naishiro, K Imai, Y Shinomura, Ann Rheum Dis 2012 71 1755 22589378
116. The Utility of Serum IgG4 Concentrations as a Biomarker. S Kawa, T Ito, T Watanabe, M Maruyama, H Hamano, M Maruyama, T Muraki, N Arakura, Int J Rheumatol 2012 2012 198314 22536256
117. IgG4-related disease: nomenclature, clinical features, and treatment. JH Stone, Semin Diagn Pathol 2012 29 177 190 23068296
118. Treatment of autoimmune pancreatitis with the anecdotes of the first report. T Kamisawa, T Takeuchi, Int J Rheumatol 2012 2012 597643 22548071
119. Optimising corticosteroid treatment for autoimmune pancreatitis. A Ghazale, ST Chari, Gut 2007 56 1650 1652 17998320 (Pubitemid 350206287)
120. Rituximab therapy leads to rapid decline of serum IgG4 levels and prompt clinical improvement in IgG4-related systemic disease. A Khosroshahi, DB Bloch, V Deshpande, JH Stone, Arthritis Rheum 2010 62 1755 1762 20191576
121. IgG4-related systemic disease: features and treatment response in a French cohort: results of a multicenter registry. M Ebbo, L Daniel, M Pavic, P Sève, M Hamidou, E Andres, S Burtey, L Chiche, J Serratrice, M Longy-Boursier, M Ruivard, J Haroche, B Godeau, AB Beucher, JM Berthelot, T Papo, JL Pennaforte, A Benyamine, N Jourde, C Landron, P Roblot, O Moranne, C Silvain, B Granel, F Bernard, V Veit, K Mazodier, E Bernit, H Rousset, J Boucraut, et al. Medicine (Baltimore) 2012 91 49 56
122. Caputo C, Bazargan A, McKelvie PA, Sutherland T, Su CS, Inder WJ: Hypophysitis due to IgG4-related disease responding to treatment with azathioprine: an alternative to corticosteroid therapy. Pituitary 2013,: [Epub ahead of print].
123. Extra-pancreatic manifestations of IgG4-related systemic disease: a single-centre experience of treatment with combined immunosuppression. JJ Bosco, D Suan, W Varikatt, MW Lin, Intern Med J 2013 43 417 423 23013529
124. IgG4-related disease with hypergammaglobulinemic hyperviscosity and retinopathy. PC Wong, AT Fung, AS Gerrie, G Moloney, D Maberley, D Rossman, V White, D Collins, R Coupland, LY Chen, Eur J Haematol 2013 90 250 256 23278107
125. Treatment with bortezomib of a patient having hyper IgG4 disease. ML Khan, TV Colby, RW Viggiano, R Fonseca, Clin Lymphoma Myeloma Leuk 2010 10 217 219 20511168
126. Rituximab therapy for refractory biliary strictures in immunoglobulin G4-associated cholangitis. M Topazian, TE Witzig, TC Smyrk, JS Pulido, MJ Levy, PS Kamath, ST Chari, Clin Gastroenterol Hepatol 2008 6 364 366 18328441 (Pubitemid 351318380)
127. Recurrence of IgG4-related disease following treatment with rituximab. J Murakami, S Matsui, S Ishizawa, K Arita, A Wada, T Miyazono, H Hounoki, K Shinoda, H Taki, T Sugiyama, Mod Rheumatol 2013 23 1226 1230 22956241
128. Serial changes of elevated serum IgG4 levels in IgG4-related systemic disease. T Tabata, T Kamisawa, K Takuma, N Egawa, K Setoguchi, K Tsuruta, T Obayashi, T Sasaki, Intern Med 2011 50 69 75 21245628
129. 18F-FDG PET/CT for staging and evaluation of treatment response in IgG4-related disease: a retrospective multicenter study. M Ebbo, A Grados, E Guedj, D Gobert, C Colavolpe, M Zaidan, A Masseau, F Bernard, JM Berthelot, N Morel, F Lifermann, S Palat, J Haroche, X Mariette, B Godeau, E Bernit, N Costedoat-Chalumeau, T Papo, M Hamidou, JR Harlé N Schleinitz, Arthritis Care Res (Hoboken) 2013 [Epub ahead of print]