Neurophysiological studies and non-motor symptoms prior to ataxia in a patient with Machado-Joseph disease: Trying to understand the natural history of brain degeneration

Cerebellum

Volumn 13, Issue 4, 2014, Pages 447-451

  Pedroso, José Luiz ^a,b   Bor Seng Shu, Edson ^c   Braga Neto, Pedro ^a,d   Ribeiro, Rodrigo Souza ^a   Bezerra, Márcio Luiz Escorcio ^a   Do Prado, Lucila B F ^a   Batista, Ilza Rosa ^a,b   Alessi, Helena ^a   Teixeira, Manoel Jacobsen ^c   Manzano, Gilberto Mastrocola ^a   Do Prado, Gilmar Fernandes ^a   Barsottini, Orlando Graziani Povoas ^a,b  

^a FEDERAL UNIVERSITY OF SÃO PAULO   (Brazil)

^b HOSPITAL ISRAELITA ALBERT EINSTEIN   (Brazil)

^c UNIVERSITY OF SÃO PAULO   (Brazil)

^d STATE UNIVERSITY OF CEARÁ   (Brazil)

Author keywords

Machado Joseph disease; Pathophysiology; Polysomnography; Transcranial sonography; Vestibular evoked myogenic potential

Indexed keywords

[2 [[2 [[[3 (4 CHLOROPHENYL) 8 METHYL 8 AZABICYCLO[3.2.1]OCT 2 YL]METHYL](2 MERCAPTOETHYL)AMINO]ETHYL]AMINO]ETHANETHIOLATO]OXOTECHNETIUM TC 99M; TECHNETIUM COMPLEX; TECHNETIUM TC 99M TRODAT-1; TROPANE DERIVATIVE;

ADULT; AMNESIA; ARTICLE; ATAXIA; BRAIN DEGENERATION; CAG REPEAT; CASE REPORT; CHOLINERGIC SYSTEM; CLINICAL EVALUATION; CONTROLLED STUDY; DISEASE ASSOCIATION; DOPPLER ECHOGRAPHY; FAMILY HISTORY; FUNCTIONAL NEUROIMAGING; GENETIC SCREENING; HUMAN; IMAGE ANALYSIS; MACHADO JOSEPH DISEASE; MALE; NEUROANATOMY; NEUROPHYSIOLOGY; NORADRENERGIC SYSTEM; POLYSOMNOGRAPHY; PRIORITY JOURNAL; REM SLEEP; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY; SLEEP DISORDER; SUBSTANTIA NIGRA; VESTIBULAR EVOKED MYOGENIC POTENTIAL; VIVID DREAM; BRAIN; COMPLICATION; DIAGNOSTIC USE; ELECTROENCEPHALOGRAPHY; PATHOLOGY; PATHOPHYSIOLOGY; SCINTISCANNING; SLEEP DISORDERS;

ADULT; BRAIN; ELECTROENCEPHALOGRAPHY; HUMANS; MACHADO-JOSEPH DISEASE; MALE; NEUROPHYSIOLOGY; ORGANOTECHNETIUM COMPOUNDS; POLYSOMNOGRAPHY; SLEEP DISORDERS; TOMOGRAPHY, EMISSION-COMPUTED, SINGLE-PHOTON; TROPANES; ULTRASONOGRAPHY, DOPPLER, TRANSCRANIAL; VESTIBULAR EVOKED MYOGENIC POTENTIALS;

EID: 84904615064     PISSN: 14734222     EISSN: 14734230     Source Type: Journal    
DOI: 10.1007/s12311-014-0553-8     Document Type: Article

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