Plasmacytoid dendritic cell depletion in DOCK8 deficiency: Rescue of severe herpetic infections with IFN-α 2b therapy

Journal of Allergy and Clinical Immunology

Volumn 133, Issue 6, 2014, Pages

  Keles, Sevgi ^a,b   Jabara, Haifa H ^b   Reisli, Ismail ^a   McDonald, Douglas R ^b   Barlan, Isil ^c   Hanna Wakim, Rima ^d   Dbaibo, Ghassan ^d   Lefranc, Gerard ^e   Al Herz, Waleed ^f   Geha, Raif S ^b   Chatila, Talal A ^b  

^a NECMETTIN ERBAKAN UNIVERSITY   (Turkey)

^b BOSTON CHILDREN S HOSPITAL   (United States)

^c MARMARA UNIVERSITY SCHOOL OF MEDICINE   (Turkey)

^d AMERICAN UNIVERSITY OF BEIRUT   (Lebanon)

^e UNIV MONTPELLIER   (France)

^f KUWAIT UNIVERSITY   (Kuwait)

Author keywords

[No Author keywords available]

Indexed keywords

ACICLOVIR; DEDICATOR OF CYTOKINESIS 8; IMMUNOGLOBULIN; PEGINTERFERON ALPHA2B; PROTEIN DERIVATIVE; UNCLASSIFIED DRUG; VALACICLOVIR; ANTIBIOTIC AGENT;

CASE REPORT; CHILD; DISEASE SEVERITY; FEMALE; HERPES SIMPLEX; HUMAN; IMMUNE DEFICIENCY; LETTER; OUTCOME ASSESSMENT; PLASMACYTOID DENDRITIC CELL; PRESCHOOL CHILD; PRIORITY JOURNAL; TREATMENT RESPONSE; ABSENCE OF SIDE EFFECTS; ANTIBIOTIC THERAPY; ANTIVIRAL THERAPY; CELLULAR IMMUNODEFICIENCY; COMBINED IMMUNODEFICIENCY; DEDICATOR OF CYTOKINESIS 8 DEFICIENCY; DOSE RESPONSE; DRUG DOSE INCREASE; DRUG MEGADOSE; EAR DISEASE; EAR ULCERATION; EXON; GENE DELETION; HERPES LABIALIS; IMMUNOPROPHYLAXIS; INFECTION PREVENTION; INTRON; MAINTENANCE THERAPY; PLASMACYTOID DENDRITIC CELL DEPLETION; REMISSION; SUBCUTANEOUS IMMUNOTHERAPY; SUPPURATIVE OTITIS MEDIA; TOPICAL TREATMENT; TURK (PEOPLE); ULCER; VESICULAR RASH;

ANTIVIRAL AGENTS; CHILD; CHILD, PRESCHOOL; DENDRITIC CELLS; FEMALE; GUANINE NUCLEOTIDE EXCHANGE FACTORS; HERPESVIRIDAE INFECTIONS; HOMOZYGOTE; HUMANS; IMMUNOPHENOTYPING; INTERFERON-ALPHA; MUTATION; RECOMBINANT PROTEINS; SEVERE COMBINED IMMUNODEFICIENCY; TREATMENT OUTCOME;

EID: 84901807538     PISSN: 00916749     EISSN: 10976825     Source Type: Journal    
DOI: 10.1016/j.jaci.2014.03.032     Document Type: Article

References (11)

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