Complexes of Usher proteins preassemble at the endoplasmic reticulum and are required for trafficking and ER homeostasis

DMM Disease Models and Mechanisms

Volumn 7, Issue 5, 2014, Pages 547-559

  Blanco Sánchez, Bernardo ^a   Clément, Aurélie ^a   Fierro Jr , Javier ^a   Washbourne, Philip ^a   Westerfield, Monte ^a  

^a UNIVERSITY OF OREGON   (United States)

Author keywords

Cadherin23; ER stress; Hair cell; Harmonin; Ift88; Myo7aa; Trafficking; Usher syndrome; Zebrafish

Indexed keywords

CADHERIN 23; MEMBRANE PROTEIN; PROTEIN HARMONIN; PROTEIN IFT88; PROTEIN MYO7AA; UNCLASSIFIED DRUG; MULTIPROTEIN COMPLEX; PROTEIN BINDING; SIGNAL TRANSDUCING ADAPTOR PROTEIN; ZEBRAFISH PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CELL MIGRATION; COMPLEX FORMATION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; GENE MUTATION; HAIR CELL; INNER EAR; MECHANORECEPTOR; NONHUMAN; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; PROTEIN SECRETION; ZEBRA FISH; ANIMAL; CELL FRACTIONATION; ENDOPLASMIC RETICULUM STRESS; GENETICS; HOMEOSTASIS; METABOLISM; MUTATION; PROTEIN TRANSPORT; TRANSPORT VESICLE;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ANIMALS; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; HAIR CELLS, AUDITORY, INNER; HOMEOSTASIS; MECHANORECEPTORS; MULTIPROTEIN COMPLEXES; MUTATION; PROTEIN BINDING; PROTEIN TRANSPORT; SUBCELLULAR FRACTIONS; TRANSPORT VESICLES; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 84900444834     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.014068     Document Type: Article

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