Rapid iron loading in heart and liver in a patient with transfusion dependent thalassaemia after brief poor compliance with iron chelation therapy

Sultan Qaboos University Medical Journal

Volumn 10, Issue 3, 2010, Pages 401-404

  Daar, Shahina ^a   Ahmed, Saeed ^b   Berdoukas, Vasili ^c  

^a SULTAN QABOOS UNIVERSITY   (Oman)

^b SULTAN QABOOS UNIVERSITY HOSPITAL   (Oman)

^c CHILDREN S HOSPITAL LOS ANGELES   (United States)

Author keywords

Case report; Chelation therapy; Deferiprone; Deferoxamine; Iron overload; Magnetic resonance imaging; Oman; Thalassaemia major

Indexed keywords

EID: 84898317538     PISSN: 2075051X     EISSN: 20750528     Source Type: Journal    
DOI: None     Document Type: Article

References (9)

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2. Tanner MA, Galanello R, Dessi C, Westwood MA, Smith GC, Nair SV, et al. Myocardial iron loading in patients with thalassemia major on deferoxamine chelation. J Cardiovasc Magn Reson 2006; 8:543-7.
3. Anderson LJ, Holden S, Davis B, Prescott E, Charrier CC, Bunce NH, et al. Cardiovascular T2-star (T2*) magnetic resonance for the early diagnosis of myocardial iron overload. Eur Heart J 2001; 22:2171-9.
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7. Farmaki K, Gotsis E, Tzoumari I, Berdoukas V. Rapid iron loading in a pregnant woman with transfusion-dependent thalassemia after brief cessation of iron chelation therapy. Eur J Haematol 2008; 81:157-9.
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9. Farmaki K, Tzoumari I, Pappa C, Chouliaras G, Berdoukas V. Normalisation of total body iron load with very intensive combined chelation reverses cardiac and endocrine complications of thalassaemia major. Br J Haematol 2010; 148:466-75.