Mouse model of glycogen storage disease type III

Molecular Genetics and Metabolism

Volumn 111, Issue 4, 2014, Pages 467-476

  Liu, Kai Ming ^a,b   Wu, Jer Yuarn ^a   Chen, Yuan Tsong ^a,c  

^a INSTITUTE OF BIOMEDICAL SCIENCES   (Taiwan)

^b NATIONAL YANG MING UNIVERSITY   (Taiwan)

^c DUKE UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

GDE; Glycogen debranching enzyme; Glycogen storage disease type III; GSD III; Mouse model

Indexed keywords

ALANINE AMINOTRANSFERASE; ALKALINE PHOSPHATASE; ASPARTATE AMINOTRANSFERASE; CREATINE KINASE; GLYCOGEN; GLYCOGEN DEBRANCHING ENZYME;

ALANINE AMINOTRANSFERASE BLOOD LEVEL; ALKALINE PHOSPHATASE BLOOD LEVEL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; BLOOD CHEMISTRY; CONTROLLED STUDY; CREATINE KINASE BLOOD LEVEL; DIET RESTRICTION; ENZYMATIC ASSAY; ENZYME ACTIVITY; ENZYME DEFICIENCY; EXON; FEEDING; FEMALE; FORELIMB; GLYCOGEN STORAGE DISEASE TYPE 3; GRIP STRENGTH; HEART; HEPATOMEGALY; HETEROZYGOTE; HINDLIMB; HISTOPATHOLOGY; HOMOZYGOTE; HYPERLIPIDEMIA; HYPOGLYCEMIA; LIFESPAN; LIVER FIBROSIS; MALE; MOTOR ACTIVITY; MOUSE; MUSCLE WEAKNESS; NONHUMAN; PRIORITY JOURNAL; WESTERN BLOTTING; WILD TYPE; ANIMAL; ANTIBODY SPECIFICITY; BLOOD; DEFICIENCY; DISEASE MODEL; ENZYMOLOGY; GENETICS; HUMAN; IMMUNOBLOTTING; KNOCKOUT MOUSE; LIVER; METABOLISM; MUSCLE STRENGTH; PATHOLOGY; PATHOPHYSIOLOGY;

MUS;

ANIMALS; DISEASE MODELS, ANIMAL; FASTING; FEMALE; GLYCOGEN; GLYCOGEN DEBRANCHING ENZYME SYSTEM; GLYCOGEN STORAGE DISEASE TYPE III; HUMANS; IMMUNOBLOTTING; LIVER; MALE; MICE; MICE, KNOCKOUT; MUSCLE STRENGTH; ORGAN SPECIFICITY;

EID: 84897576233     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2014.02.005     Document Type: Article

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