Characterization of a canine model of glycogen storage disease type IIIa

DMM Disease Models and Mechanisms

Volumn 5, Issue 6, 2012, Pages 804-811

  Yi, Haiqing ^a   Thurberg, Beth L ^b   Curtis, Sarah ^a   Austin, Stephanie ^a   Fyfe, John ^c   Koeberl, Dwight D ^a   Kishnani, Priya S ^a   Sun, Baodong ^a  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b GENZYME CORPORATION   (United States)

^c MICHIGAN STATE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE AMINOTRANSFERASE; ALKALINE PHOSPHATASE; AMINOTRANSFERASE; ASPARTATE AMINOTRANSFERASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL MEMBRANE; CONTROLLED STUDY; CREATINE KINASE BLOOD LEVEL; DISEASE COURSE; DOG; FRAMESHIFT MUTATION; GLYCOGEN ANALYSIS; GLYCOGEN METABOLISM; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 3A; LIVER; LIVER CELL; LIVER FIBROSIS; LIVER HISTOLOGY; MUSCLE; MUSCLE FIBRIL; MUSCLE INJURY; NONHUMAN; PRIORITY JOURNAL; SARCOPLASM; TURNOVER TIME;

ADIPOCYTES; ANIMALS; DISEASE MODELS, ANIMAL; DOG DISEASES; DOGS; FASTING; GLYCOGEN; GLYCOGEN STORAGE DISEASE TYPE III; HEPATOCYTES; LIPIDS; LIVER; LIVER CIRRHOSIS; MUSCLES;

CANIS FAMILIARIS;

EID: 84870017723     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.009712     Document Type: Article

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