An induced pluripotent stem cell model of hypoplastic left heart syndrome (HLHS) reveals multiple expression and functional differences in HLHS-derived cardiac myocytes

Stem Cells Translational Medicine

Volumn 3, Issue 4, 2014, Pages 416-423

  Jiang, Yan ^a,b   Habibollah, Saba ^a   Tilgner, Katarzyna ^a   Collin, Joseph ^a   Barta, Tomas ^a   Al Aama, Jumana Yousuf ^b   Tesarov, Lenka ^a,c   Hussain, Rafiqul ^a   Trafford, Andrew W ^d   Kirkwood, Graham ^d   Sernagor, Evelyne ^e   Eleftheriou, Cyril G ^e   Przyborski, Stefan ^f   Stojkovi, Miodrag ^g   Lako, Majlinda ^a   Keavney, Bernard ^a,d   Armstrong, Lyle ^a  

^a NEWCASTLE UNIVERSITY   (United Kingdom)

^b SOOCHOW UNIVERSITY   (China)

^c KING ABDULAZIZ UNIVERSITY   (Saudi Arabia)

^d MASARYK UNIVERSITY   (Czech Republic)

^e UNIVERSITY OF MANCHESTER   (United Kingdom)

^f DURHAM UNIVERSITY   (United Kingdom)

^g UNIVERSITY OF KRAGUJEVAC   (Serbia)

Author keywords

Cardiac development; Cardiac myocytes; Hypoplastic left heart syndrome; Induced pluripotent stem cells; Pluripotent stem cell differentiation

Indexed keywords

BETA ADRENERGIC RECEPTOR BLOCKING AGENT; CAFFEINE; INOSITOL 1, 4, 5 TRISPHOSPHATE RECEPTOR; RYANODINE RECEPTOR; UNCLASSIFIED DRUG;

ARTICLE; CALCIUM CELL LEVEL; CONTROLLED STUDY; DNA SEQUENCE; ELECTROPHYSIOLOGY; EXPERIMENTAL STUDY; FIBROBLAST CULTURE; FLOW CYTOMETRY; GENE EXPRESSION; HEART FUNCTION; HEART MUSCLE CELL; HUMAN; HUMAN CELL; HYPOPLASTIC LEFT HEART SYNDROME; NORMAL HUMAN DERMAL FIBROBLAST; PLURIPOTENT STEM CELL; RISK FACTOR; STEM CELL TRANSPLANTATION;

CARDIAC DEVELOPMENT; CARDIAC MYOCYTES; HYPOPLASTIC LEFT HEART SYNDROME; INDUCED PLURIPOTENT STEM CELLS; PLURIPOTENT STEM CELL DIFFERENTIATION;

CELLS, CULTURED; GENE EXPRESSION REGULATION; HUMANS; HYPOPLASTIC LEFT HEART SYNDROME; INDUCED PLURIPOTENT STEM CELLS; INFANT, NEWBORN; MALE; MODELS, BIOLOGICAL; MUSCLE PROTEINS; MYOCYTES, CARDIAC;

EID: 84897546322     PISSN: 21576564     EISSN: 21576580     Source Type: Journal    
DOI: 10.5966/sctm.2013-0105     Document Type: Article

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