Roles of the nucleolus in the CAG RNA-mediated toxicity

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1842, Issue 6, 2014, Pages 779-784

  Tsoi, Ho ^a   Chan, Ho Yin Edwin ^a  

^a CHINESE UNIVERSITY OF HONG KONG   (Hong Kong)

Author keywords

Nucleolar stress; Nucleolin; P53; Patient fibroblast; Polyglutamine disease; UCE methylation

Indexed keywords

POLYGLUTAMINE; RIBOSOME RNA; RNA; PROTEIN P53; TP53 PROTEIN, HUMAN;

ARTICLE; CAG REPEAT; CELL FUNCTION; GENETIC REGULATION; GENETIC TRANSCRIPTION; HUMAN; HUNTINGTON CHOREA; NERVE CELL DEGENERATION; NERVE CELL NECROSIS; NEUROLOGIC DISEASE; NONHUMAN; NUCLEOLUS; PRIORITY JOURNAL; PROTEIN STRUCTURE; RNA RECOGNITION MOTIF; SPINOCEREBELLAR DEGENERATION; STRESS; TOXICITY; TRANSCRIPTION INITIATION; TRINUCLEOTIDE REPEAT; FIBROBLAST; GENETICS; METABOLISM; PATHOLOGY; PROTEIN SYNTHESIS;

CELL NUCLEOLUS; FIBROBLASTS; HUMANS; HUNTINGTON DISEASE; PROTEIN BIOSYNTHESIS; RNA, RIBOSOMAL; SPINOCEREBELLAR ATAXIAS; TRANSCRIPTION, GENETIC; TRINUCLEOTIDE REPEAT EXPANSION; TUMOR SUPPRESSOR PROTEIN P53;

EID: 84897043536     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2013.11.015     Document Type: Article

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