CAG expansion induces nucleolar stress in polyglutamine diseases

Proceedings of the National Academy of Sciences of the United States of America

Volumn 109, Issue 33, 2012, Pages 13428-13433

  Tsoi, Ho ^a   Lau, Terrence Chi Kong ^b   Tsang, Suk Ying ^a   Lau, Kwok Fai ^a   Chan, Ho Yin Edwin ^a  

^a CHINESE UNIVERSITY OF HONG KONG   (Hong Kong)

^b CITY UNIVERSITY OF HONG KONG   (Hong Kong)

Author keywords

Drosophila; Machado Joseph disease; Rna toxicity; Spinocerebellar ataxia

Indexed keywords

CAG PROTEIN; CYTOCHROME C; NUCLEOLIN; POLYGLUTAMINE; PROTEIN; PROTEIN BAK; PROTEIN BCL XL; PROTEIN MDM2; PROTEIN P53; RIBOSOME PROTEIN; RIBOSOME RNA; UNCLASSIFIED DRUG; UPSTREAM CONTROL ELEMENT;

ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; ARTICLE; CONTROLLED STUDY; DNA METHYLATION; DOWN REGULATION; MITOCHONDRION; MOUSE; NONHUMAN; NUCLEOLAR STRESS; PRIORITY JOURNAL; PROTEIN RNA BINDING; PROTEIN STRUCTURE; RNA TRANSCRIPTION;

EID: 84865191445     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1204089109     Document Type: Article

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