Culture of primary ciliary dyskinesia epithelial cells at air-liquid interface can alter ciliary phenotype but remains a robust and informative diagnostic aid

PLoS ONE

Volumn 9, Issue 2, 2014, Pages

  Hirst, Robert A ^a   Jackson, Claire L ^b,c   Coles, Janice L ^b,c   Williams, Gwyneth ^a   Rutman, Andrew ^a   Goggin, Patricia M ^b,c   Adam, Elizabeth C ^b,c   Page, Anthony ^b,c   Evans, Hazel J ^b   Lackie, Peter M ^c   O'Callaghan, Christopher ^a,d   Lucas, Jane S ^b,c  

^a UNIVERSITY OF LEICESTER   (United Kingdom)

^b UNIVERSITY HOSPITAL SOUTHAMPTON NHS FOUNDATION TRUST   (United Kingdom)

^c Queen Mary University of London and Barts NIHR BRC NHS Trust National Institute for Health and Care Research   (United Kingdom)

^d UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

AIR LIQUID INTERFACE; ARTICLE; CELL CULTURE; CELLULAR PARAMETERS; CILIARY BEAT FREQUENCY; CILIARY DYSKINESIA; CILIATED EPITHELIUM; CULTURE TECHNIQUE; EPITHELIUM CELL; HUMAN; HUMAN CELL; MAJOR CLINICAL STUDY; RETROSPECTIVE STUDY; TRANSMISSION ELECTRON MICROSCOPY; VIDEO MICROSCOPY; AIR; CILIARY MOTILITY DISORDERS; CYTOLOGY; EUKARYOTIC FLAGELLUM; GENETICS; KARTAGENER SYNDROME; NOSE MUCOSA; PHENOTYPE; PHYSIOLOGY;

AIR; CELL CULTURE TECHNIQUES; CELLS, CULTURED; CILIA; CILIARY MOTILITY DISORDERS; EPITHELIAL CELLS; HUMANS; KARTAGENER SYNDROME; MICROSCOPY, ELECTRON, TRANSMISSION; MICROSCOPY, VIDEO; NASAL MUCOSA; PHENOTYPE; RETROSPECTIVE STUDIES;

EID: 84896123256     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0089675     Document Type: Article

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