Long-term Outcomes of Patients With Wilson Disease in a Large Austrian Cohort

Clinical Gastroenterology and Hepatology

Volumn 12, Issue 4, 2014, Pages 683-689

  Beinhardt, Sandra ^a   Leiss, Waltraud ^b   Stättermayer, Albert Friedrich ^a   Graziadei, Ivo ^c   Zoller, Heinz ^c   Stauber, Rudolf ^d   Maieron, Andreas ^e   Datz, Christian ^f   Steindl Munda, Petra ^a   Hofer, Harald ^a   Vogel, Wolfgang ^c   Trauner, Michael ^a   Ferenci, Peter ^a  

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b UNIVERSITY OF BERN   (Switzerland)

^c INNSBRUCK MEDICAL UNIVERSITY   (Austria)

^d MEDICAL UNIVERSITY OF GRAZ   (Austria)

^e Hospital of Elisabethinen   (Austria)

^f Oberndorf Hospital   (Austria)

Author keywords

Genetic liver disease; Inherited liver disease; Mortality; Population

Indexed keywords

CERULOPLASMIN; COPPER; WILSON DISEASE PROTEIN;

ADULT; AGE DISTRIBUTION; ARTICLE; AUSTRIA; CHELATION THERAPY; CHOLESTASIS; COHORT ANALYSIS; DECOMPENSATED LIVER CIRRHOSIS; DYSARTHRIA; FEMALE; FOLLOW UP; FULMINANT HEPATIC FAILURE; GENE FREQUENCY; GENE MUTATION; HETEROZYGOSITY; HUMAN; LIVER DISEASE; LIVER TRANSPLANTATION; LONG TERM CARE; MAJOR CLINICAL STUDY; MALE; MENTAL DISEASE; NEUROLOGIC DISEASE; OUTCOME ASSESSMENT; OUTPATIENT DEPARTMENT; RETROSPECTIVE STUDY; SURVIVAL RATE; SURVIVAL TIME; TREMOR; WILSON DISEASE; YOUNG ADULT;

GENETIC LIVER DISEASE; INHERITED LIVER DISEASE; MORTALITY; POPULATION;

ADOLESCENT; ADULT; AUSTRIA; CHILD; CHILD, PRESCHOOL; FEMALE; HEPATOLENTICULAR DEGENERATION; HUMANS; MALE; MIDDLE AGED; PROGNOSIS; RETROSPECTIVE STUDIES; SURVIVAL ANALYSIS; TREATMENT OUTCOME; YOUNG ADULT;

EID: 84896064958     PISSN: 15423565     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cgh.2013.09.025     Document Type: Article

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