Liver transplantation for children with Wilson disease: Comparison of outcomes between children and adults

Clinical Transplantation

Volumn 25, Issue 1, 2011, Pages

  Arnon, Ronen ^a,b   Annunziato, Rachel ^a,c   Schilsky, Michael ^d   Miloh, Tamir ^a,b   Willis, Asha ^a   Sturdevant, Mark ^a,b   Sakworawich, Arnond ^c   Suchy, Frederick ^a   Kerkar, Nanda ^a,b  

^a MOUNT SINAI SCHOOL OF MEDICINE   (United States)

^b MOUNT SINAI MEDICAL CENTER   (United States)

^c FORDHAM UNIVERSITY   (United States)

^d YALE UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Adult; Chronic liver failure; Fulminant liver failure; Liver transplantation; Outcome; Pediatric; Wilson disease

Indexed keywords

ALKALINE PHOSPHATASE; BILIRUBIN; CREATININE;

ADOLESCENT; ADULT; ADULT DISEASE; AGED; ALKALINE PHOSPHATASE BLOOD LEVEL; ARTICLE; BACTERIAL PERITONITIS; BILIRUBIN BLOOD LEVEL; CHILD; CHILDHOOD DISEASE; CHRONIC LIVER DISEASE; COMPARATIVE STUDY; CONTROLLED STUDY; CREATININE BLOOD LEVEL; DIALYSIS; FEMALE; FULMINANT HEPATIC FAILURE; GRAFT FAILURE; HUMAN; LIVER TRANSPLANTATION; MAJOR CLINICAL STUDY; MALE; PRESCHOOL CHILD; PRIORITY JOURNAL; RISK FACTOR; SCHOOL CHILD; VENTILATOR; WILSON DISEASE;

ADOLESCENT; ADULT; AGED; CHILD; CHILD, PRESCHOOL; END STAGE LIVER DISEASE; FEMALE; FOLLOW-UP STUDIES; HEPATOLENTICULAR DEGENERATION; HUMANS; LIVER FAILURE, ACUTE; LIVER TRANSPLANTATION; MALE; MIDDLE AGED; RISK FACTORS; SURVIVAL RATE; TREATMENT OUTCOME; YOUNG ADULT;

EID: 79551718663     PISSN: 09020063     EISSN: 13990012     Source Type: Journal    
DOI: 10.1111/j.1399-0012.2010.01327.x     Document Type: Article

References (28)

1. Ala A, Schilsky ML. Wilson disease: pathophysiology, diagnosis, treatment and screening. Clin Liver Dis 2004: 8: 787.
2. Roberts EA, Schilsky ML. Diagnosis and treatment of Wilson disease: an update. Hepatology 2008: 6: 2089.
3. Emre S, Atillasoy EO, Ozdemir S et al. Orthotopic liver transplantation for Wilson's disease: a single-center experience. Transplantation 2001: 72: 1232.
4. DuBois RS, Rodgerson DO, Martineau G et al. Orthotopic liver transplantation for Wilson's disease. Lancet 1971: 1: 505.
5. Sternlieb I. Wilson's disease: indications for liver transplants. Hepatology 1984: 4: 15S.
6. Gitlin JD. Wilson disease. Gastroenterology 2003: 125: 1868.
7. Sutcliffe RP, Maguire DD, Muiesan P et al. Liver transplantation for Wilson's disease: long-term results and quality-of-life assessment. Transplantation 2003: 75: 1003.
8. Schilsky ML. Diagnosis and treatment of Wilson's disease. Pediatr Transplant 2002: 6: 15.
9. Ping CC, Hassan Y, Aziz NA, Ghazali R, Awaisu A. Discontinuation of penicillamine in the absence of alternative orphan drugs (trientine-zinc): a case of decompensated liver cirrhosis in Wilson's disease. J Clin Pharm Ther 2007: 32: 101.
10. El-Youssef M. Wilson disease. Mayo Clin Proc 2003: 78: 1126.
11. Walshe JM, Dixon AK. Dangers of non-compliance in Wilson's disease. Lancet 1986: 1: 845.
12. Roberts EA, Schilsky ML. A practice guideline on Wilson disease. Hepatology 2003: 37: 1475.
13. Ala A, Walker AP, Ashkan K, Dooley JS, Schilsky ML. Wilson's disease. Lancet 2007: 3: 397.
14. Kasai N, Miyoshi I, Osanai T, Yamashita T, Kamimura E, Yoshida MC. Effects of sex hormones on fulminant hepatitis in LEC rats: a model of Wilson's disease. Lab Anim Sci 1992: 42: 363.
15. Asfaha S, Almansori M, Qarni U, Gutfreund KS. Plasmapheresis for hemolytic crisis and impending acute liver failure in Wilson disease. J Clin Apher 2007: 22: 295.
16. Jhang JS, Schilsky ML, Lefkowitch JH, Schwartz J. Therapeutic plasmapheresis as a bridge to liver transplantation in fulminant Wilson disease. J Clin Apher 2007: 22: 10.
17. Aagaard NK, Thomsen KL, Holland-Fischer P, Jørgensen SP, Ott P. A 15-year-old girl with severe hemolytic Wilson's crisis recovered without transplantation after extracorporeal circulation with the Prometheus system. Blood Purif 2009: 28: 102.
18. Chiu A, Tsoi NS, Fan ST. Use of the molecular adsorbents recirculating system as a treatment for acute decompensated Wilson disease. Liver Transpl 2008: 14: 1512.
19. Ozcay F, Bayrakci US, Baskin E et al. Long term follow-up of glomerular and tubular functions in liver transplanted patients with Wilson's disease. Pediatr Transplant 2008: 12: 785.
20. Asonuma K, Inomata Y, Kasahara M et al. Living related liver transplantation from heterozygote genetic carriers to children with Wilson's disease. Pediatr Transplant 1999: 3: 201.
21. Yoshitoshi EY, Takada Y, Oike F et al. Long-term outcomes for 32 cases of Wilson's disease after living-donor liver transplantation. Transplantation 2009: 87: 261.
22. Cheng F, Li GQ, Zhang F et al. Outcomes of living-related liver transplantation for Wilson's disease: a single-center experience in China. Transplantation 2009: 87: 751.
23. Pabón V, Dumortier J, Gincul R et al. Long-term results of liver transplantation for Wilson's disease. Gastroenterol Clin Biol 2008: 32: 378.
24. Eghtesad B, Nezakatgoo N, Geraci LC et al. Liver transplantation for Wilson's disease: a single-center experience. Liver Transpl Surg 1999: 5: 467.
25. Sevmis S, Karakayali H, Aliosmanoglu I et al. Liver transplantation for Wilson's disease. Transplant Proc 2008: 40: 228.
26. Sze YK, Dhawan A, Taylor RM et al. Pediatric liver transplantation for metabolic liver disease: experience at King's College Hospital. Transplantation 2009: 87: 87.
27. Dhawan A, Taylor RM, Cheeseman P, De Silva P, Katsiyiannakis L, Mieli-Vergani G. Wilson's disease in children: 37-year experience and revised King's score for liver transplantation. Liver Transpl 2005: 11: 441.
28. Ferenci P, Członkowska A, Merle U et al. Late-onset Wilson's disease. Gastroenterology 2007: 132: 1294.