Phosphorylase re-expression, increase in the force of contraction and decreased fatigue following notexin-induced muscle damage and regeneration in the ovine model of McArdle disease

Neuromuscular Disorders

Volumn 24, Issue 2, 2014, Pages 167-177

  Howell, J McC ^a,b   Walker, K R ^b   Creed, K E ^a   Dunton, E ^a   Davies, L ^a   Quinlivan, R ^d   Karpati, G ^c  

^a MURDOCH UNIVERSITY   (Australia)

^b UNIVERSITY OF WESTERN AUSTRALIA   (Australia)

^c MCGILL UNIVERSITY   (Canada)

^d NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

Author keywords

Glycogen phosphorylase; McArdle disease; Myophosphorylase; Notexin; Ovine model of McArdle disease; Phosphorylase isoforms

Indexed keywords

GLYCOGEN PHOSPHORYLASE; MCARDLE DISEASE; MYOPHOSPHORYLASE; NOTEXIN; OVINE MODEL OF MCARDLE DISEASE; PHOSPHORYLASE ISOFORMS.;

ANIMALS; BLOTTING, WESTERN; ELAPID VENOMS; GLYCOGEN; GLYCOGEN PHOSPHORYLASE; GLYCOGEN STORAGE DISEASE TYPE V; ISOENZYMES; MALE; MUSCLE FATIGUE; MUSCLE STRENGTH; MUSCLE, SKELETAL; NECROSIS; NEUROTOXINS; PHOSPHORYLASES; REGENERATION; SHEEP; TIME FACTORS;

EID: 84893723317     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2013.10.003     Document Type: Article

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