Early onset of ataxia in moonwalker mice is accompanied by complete ablation of type II unipolar brush cells and purkinje cell dysfunction

Journal of Neuroscience

Volumn 33, Issue 50, 2013, Pages 19689-19694

  Sekerková, Gabriella ^a   Kim, Jin Ah ^a   Nigro, Maximiliano J ^a   Becker, Esther B E ^b   Hartmann, Jana ^c   Birnbaumer, Lutz ^d   Mugnaini, Enrico ^a   Martina, Marco ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

^b MRC Functional Genetics Unit   (United Kingdom)

^c TECHNICAL UNIVERSITY OF MUNICH   (Germany)

^d NATIONAL INSTITUTE OF ENVIRONMENTAL HEALTH SCIENCES   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CALRETININ; METABOTROPIC RECEPTOR; TRANSIENT RECEPTOR POTENTIAL CHANNEL 3;

ANIMAL TISSUE; ARTICLE; BRAIN DYSFUNCTION; BRAIN ELECTROPHYSIOLOGY; BRIGHT FIELD MICROSCOPY; BRUSH BORDER; CALCIUM HOMEOSTASIS; CELL LOSS; CELL STRUCTURE; CEREBELLAR ATAXIA; CONTROLLED STUDY; GAIN OF FUNCTION MUTATION; IMMUNOFLUORESCENCE MICROSCOPY; IMMUNOHISTOCHEMISTRY; IMMUNOLOCALIZATION; IMMUNOREACTIVITY; MALE; MOUSE; NERVE EXCITABILITY; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PURKINJE CELL; SYNAPTIC TRANSMISSION;

ACTION POTENTIALS; ANIMALS; CEREBELLAR ATAXIA; CEREBELLUM; MICE; NEURONS; PATCH-CLAMP TECHNIQUES; PURKINJE CELLS; TRPC CATION CHANNELS;

EID: 84889788069     PISSN: 02706474     EISSN: 15292401     Source Type: Journal    
DOI: 10.1523/JNEUROSCI.2294-13.2013     Document Type: Article

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