메뉴 건너뛰기




Volumn 10, Issue 1, 2014, Pages 105-116

Failure of the fontan circulation

Author keywords

Chronic low output; Circulatory failure; Fontan circulation; Pulmonary vascular resistance

Indexed keywords

BRONCHITIS; CAVOPULMONARY CONNECTION; DIASTOLIC BLOOD PRESSURE; FENESTRATION; FONTAN CIRCULATION FAILURE; FONTAN PROCEDURE; FUNCTIONAL DISEASE; HEART OUTPUT; HEART PRELOAD; HEART VENTRICLE ENDDIASTOLIC PRESSURE; HEART VENTRICLE FUNCTION; HUMAN; ISCHEMIA; LIVER CIRRHOSIS; LIVER FIBROSIS; LUNG BLOOD VESSEL; LUNG VASCULAR RESISTANCE; PRESSURE GRADIENT; PRESSURE VOLUME CURVE; PROTEIN LOSING GASTROENTEROPATHY; REVIEW; VENOUS CONGESTION; VENOUS PRESSURE;

EID: 84888041740     PISSN: 15517136     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.hfc.2013.09.010     Document Type: Review
Times cited : (173)

References (46)
  • 1
    • 0015060609 scopus 로고
    • Surgical repair of tricuspid atresia
    • Fontan F., Baudet E. Surgical repair of tricuspid atresia. Thorax 1971, 26:240-248.
    • (1971) Thorax , vol.26 , pp. 240-248
    • Fontan, F.1    Baudet, E.2
  • 2
    • 20044378182 scopus 로고    scopus 로고
    • The Fontan circulation
    • Gewillig M. The Fontan circulation. Heart 2005, 91:839-846.
    • (2005) Heart , vol.91 , pp. 839-846
    • Gewillig, M.1
  • 4
    • 0034532499 scopus 로고    scopus 로고
    • Pathophysiological aspects after cavopulmonary anastomosis
    • Gewillig M., Kalis N. Pathophysiological aspects after cavopulmonary anastomosis. Thorac Cardiovasc Surg 2000, 48:336-341.
    • (2000) Thorac Cardiovasc Surg , vol.48 , pp. 336-341
    • Gewillig, M.1    Kalis, N.2
  • 5
    • 84055182266 scopus 로고    scopus 로고
    • What limits cardiac performance during exercise in normal subjects and in healthy Fontan patients?
    • pii:791291
    • La Gerche A., Gewillig M. What limits cardiac performance during exercise in normal subjects and in healthy Fontan patients?. Int J Pediatr 2010, 2010. pii:791291.
    • (2010) Int J Pediatr , vol.2010
    • La Gerche, A.1    Gewillig, M.2
  • 6
    • 84888051214 scopus 로고    scopus 로고
    • Sildanafil improves exercise hemodynamics in Fontan patients
    • [abstract]
    • Van de Bruaene A., La Gerche A., Claessen G., et al. Sildanafil improves exercise hemodynamics in Fontan patients. Cardiol Young 2013, 23:S54. [abstract].
    • (2013) Cardiol Young , vol.23
    • Van de Bruaene, A.1    La Gerche, A.2    Claessen, G.3
  • 7
    • 45849129460 scopus 로고    scopus 로고
    • Across-sectional study of exercise performance during the first 2 decades of life after the Fontan operation
    • Paridon S.M., Mitchell P.D., Colan S.D., et al. Across-sectional study of exercise performance during the first 2 decades of life after the Fontan operation. JAm Coll Cardiol 2008, 52:99-107.
    • (2008) JAm Coll Cardiol , vol.52 , pp. 99-107
    • Paridon, S.M.1    Mitchell, P.D.2    Colan, S.D.3
  • 8
    • 39149131708 scopus 로고    scopus 로고
    • Natural history of exercise capacity after the Fontan operation: a longitudinal study
    • Giardini A., Hager A., Pace Napoleone C., et al. Natural history of exercise capacity after the Fontan operation: a longitudinal study. Ann Thorac Surg 2008, 85:818-821.
    • (2008) Ann Thorac Surg , vol.85 , pp. 818-821
    • Giardini, A.1    Hager, A.2    Pace Napoleone, C.3
  • 9
    • 23844535863 scopus 로고    scopus 로고
    • Exercise intolerance in adult congenital heart disease: comparative severity, correlates, and prognostic implication
    • Diller G.P., Dimopoulos K., Okonko D., et al. Exercise intolerance in adult congenital heart disease: comparative severity, correlates, and prognostic implication. Circulation 2005, 112:828-835.
    • (2005) Circulation , vol.112 , pp. 828-835
    • Diller, G.P.1    Dimopoulos, K.2    Okonko, D.3
  • 10
    • 78650389666 scopus 로고    scopus 로고
    • Predictors of morbidity and mortality in contemporary Fontan patients: results from a multicenter study including cardiopulmonary exercise testing in 321 patients
    • Diller G.P., Giardini A., Dimopoulos K., et al. Predictors of morbidity and mortality in contemporary Fontan patients: results from a multicenter study including cardiopulmonary exercise testing in 321 patients. Eur Heart J 2010, 31:3073-3083.
    • (2010) Eur Heart J , vol.31 , pp. 3073-3083
    • Diller, G.P.1    Giardini, A.2    Dimopoulos, K.3
  • 11
    • 0025022573 scopus 로고
    • Impact of Fontan operation on left ventricular size and contractility in tricuspid atresia
    • Gewillig M.H., Lundstrom U.R., Deanfield J.E., et al. Impact of Fontan operation on left ventricular size and contractility in tricuspid atresia. Circulation 1990, 81:118-127.
    • (1990) Circulation , vol.81 , pp. 118-127
    • Gewillig, M.H.1    Lundstrom, U.R.2    Deanfield, J.E.3
  • 12
    • 0026454830 scopus 로고
    • Abolishment of chronic volume overload. Implications for diastolic function of the systemic ventricle immediately after Fontan repair
    • Gewillig M., Daenen W., Aubert A., et al. Abolishment of chronic volume overload. Implications for diastolic function of the systemic ventricle immediately after Fontan repair. Circulation 1992, 86:II93-II99.
    • (1992) Circulation , vol.86
    • Gewillig, M.1    Daenen, W.2    Aubert, A.3
  • 13
    • 0019022571 scopus 로고
    • Left ventricular function in severe pure mitral stenosis as seen at the Kenyatta National Hospital
    • Silverstein D.M., Hansen D.P., Ojiambo H.P., et al. Left ventricular function in severe pure mitral stenosis as seen at the Kenyatta National Hospital. Am Heart J 1980, 99:727-733.
    • (1980) Am Heart J , vol.99 , pp. 727-733
    • Silverstein, D.M.1    Hansen, D.P.2    Ojiambo, H.P.3
  • 14
    • 79958100222 scopus 로고    scopus 로고
    • Renin-angiotensin-aldosterone genotype influences ventricular remodeling in infants with single ventricle
    • Mital S., Chung W.K., Colan S.D., et al. Renin-angiotensin-aldosterone genotype influences ventricular remodeling in infants with single ventricle. Circulation 2011, 123:2353-2362.
    • (2011) Circulation , vol.123 , pp. 2353-2362
    • Mital, S.1    Chung, W.K.2    Colan, S.D.3
  • 15
    • 6344239028 scopus 로고    scopus 로고
    • Evidence of pulmonary vascular disease after heart transplantation for Fontan circulation failure
    • Mitchell M.B., Campbell D.N., Ivy D., et al. Evidence of pulmonary vascular disease after heart transplantation for Fontan circulation failure. JThorac Cardiovasc Surg 2004, 128:693-702.
    • (2004) JThorac Cardiovasc Surg , vol.128 , pp. 693-702
    • Mitchell, M.B.1    Campbell, D.N.2    Ivy, D.3
  • 16
    • 84867872955 scopus 로고    scopus 로고
    • The precarious state of the liver after a Fontan operation: summary of a multidisciplinary symposium
    • Rychik J., Veldtman G., Rand E., et al. The precarious state of the liver after a Fontan operation: summary of a multidisciplinary symposium. Pediatr Cardiol 2012, 33:1001-1012.
    • (2012) Pediatr Cardiol , vol.33 , pp. 1001-1012
    • Rychik, J.1    Veldtman, G.2    Rand, E.3
  • 17
    • 84879410187 scopus 로고    scopus 로고
    • Magnetic resonance imaging identifies unsuspected liver abnormalities in patients after the Fontan procedure
    • Bulut O.P., Romero R., Mahle W.T., et al. Magnetic resonance imaging identifies unsuspected liver abnormalities in patients after the Fontan procedure. JPediatr 2013, 163:201-206.
    • (2013) JPediatr , vol.163 , pp. 201-206
    • Bulut, O.P.1    Romero, R.2    Mahle, W.T.3
  • 18
    • 79956263980 scopus 로고    scopus 로고
    • Liver disease in the patient with Fontan circulation
    • Wu F.M., Ukomadu C., Odze R.D., et al. Liver disease in the patient with Fontan circulation. Congenit Heart Dis 2011, 6:190-201.
    • (2011) Congenit Heart Dis , vol.6 , pp. 190-201
    • Wu, F.M.1    Ukomadu, C.2    Odze, R.D.3
  • 19
    • 84877275159 scopus 로고    scopus 로고
    • Hepatocellular carcinoma after the Fontan procedure
    • Asrani S., Warnes C., Kamath P. Hepatocellular carcinoma after the Fontan procedure. NEngl J Med 2013, 368:1756-1757.
    • (2013) NEngl J Med , vol.368 , pp. 1756-1757
    • Asrani, S.1    Warnes, C.2    Kamath, P.3
  • 20
    • 84872596879 scopus 로고    scopus 로고
    • Portal and sinusoidal fibrosis are common on liver biopsy after Fontan surgery
    • Schwartz M.C., Sullivan L.M., Glatz A.C., et al. Portal and sinusoidal fibrosis are common on liver biopsy after Fontan surgery. Pediatr Cardiol 2013, 34:135-142.
    • (2013) Pediatr Cardiol , vol.34 , pp. 135-142
    • Schwartz, M.C.1    Sullivan, L.M.2    Glatz, A.C.3
  • 21
    • 40149090642 scopus 로고    scopus 로고
    • Noninvasive assessment of liver fibrosis in patients with Fontan circulation using transient elastography and biochemical fibrosis markers
    • Friedrich-Rust M., Koch C., Rentzsch A., et al. Noninvasive assessment of liver fibrosis in patients with Fontan circulation using transient elastography and biochemical fibrosis markers. JThorac Cardiovasc Surg 2008, 135:560-567.
    • (2008) JThorac Cardiovasc Surg , vol.135 , pp. 560-567
    • Friedrich-Rust, M.1    Koch, C.2    Rentzsch, A.3
  • 22
    • 34548778629 scopus 로고    scopus 로고
    • Protein-losing enteropathy after Fontan operation
    • Rychik J. Protein-losing enteropathy after Fontan operation. Congenit Heart Dis 2007, 2:288-300.
    • (2007) Congenit Heart Dis , vol.2 , pp. 288-300
    • Rychik, J.1
  • 23
    • 76749146029 scopus 로고    scopus 로고
    • Use of oral budesonide in the management of protein-losing enteropathy after the Fontan operation
    • Thacker D., Patel A., Dodds K., et al. Use of oral budesonide in the management of protein-losing enteropathy after the Fontan operation. Ann Thorac Surg 2010, 89:837-842.
    • (2010) Ann Thorac Surg , vol.89 , pp. 837-842
    • Thacker, D.1    Patel, A.2    Dodds, K.3
  • 24
    • 80053329051 scopus 로고    scopus 로고
    • The use of oral budesonide in adolescents and adults with protein-losing enteropathy after the Fontan operation
    • John A.S., Driscoll D.J., Warnes C.A., et al. The use of oral budesonide in adolescents and adults with protein-losing enteropathy after the Fontan operation. Ann Thorac Surg 2011, 92:1451-1456.
    • (2011) Ann Thorac Surg , vol.92 , pp. 1451-1456
    • John, A.S.1    Driscoll, D.J.2    Warnes, C.A.3
  • 25
    • 67650725410 scopus 로고    scopus 로고
    • Evaluating failing Fontans for heart transplantation: predictors of death
    • [discussion: 563-4]
    • Griffiths E.R., Kaza A.K., Wyler von Ballmoos M.C., et al. Evaluating failing Fontans for heart transplantation: predictors of death. Ann Thorac Surg 2009, 88:558-563. [discussion: 563-4].
    • (2009) Ann Thorac Surg , vol.88 , pp. 558-563
    • Griffiths, E.R.1    Kaza, A.K.2    Wyler von Ballmoos, M.C.3
  • 26
    • 83555174316 scopus 로고    scopus 로고
    • Prospective, longitudinal study of plastic bronchitis cast pathology and responsiveness to tissue plasminogen activator
    • Heath L., Ling S., Racz J., et al. Prospective, longitudinal study of plastic bronchitis cast pathology and responsiveness to tissue plasminogen activator. Pediatr Cardiol 2011, 32:1182-1189.
    • (2011) Pediatr Cardiol , vol.32 , pp. 1182-1189
    • Heath, L.1    Ling, S.2    Racz, J.3
  • 27
    • 33646832365 scopus 로고    scopus 로고
    • Plastic bronchitis: is thoracic duct ligation a real surgical option?
    • Shah S.S., Drinkwater D.C., Christian K.G. Plastic bronchitis: is thoracic duct ligation a real surgical option?. Ann Thorac Surg 2006, 81:2281-2283.
    • (2006) Ann Thorac Surg , vol.81 , pp. 2281-2283
    • Shah, S.S.1    Drinkwater, D.C.2    Christian, K.G.3
  • 28
    • 3042592353 scopus 로고    scopus 로고
    • Plastic bronchitis after Fontan operation: treatment with stent fenestration of the Fontan circuit
    • Chaudhari M., Stumper O. Plastic bronchitis after Fontan operation: treatment with stent fenestration of the Fontan circuit. Heart 2004, 90:801.
    • (2004) Heart , vol.90 , pp. 801
    • Chaudhari, M.1    Stumper, O.2
  • 29
    • 79960373077 scopus 로고    scopus 로고
    • Plastic bronchitis: resolution after heart transplantation
    • ElMallah M.K., Prabhakaran S., Chesrown S.E. Plastic bronchitis: resolution after heart transplantation. Pediatr Pulmonol 2011, 46:824-825.
    • (2011) Pediatr Pulmonol , vol.46 , pp. 824-825
    • ElMallah, M.K.1    Prabhakaran, S.2    Chesrown, S.E.3
  • 30
    • 29544445614 scopus 로고    scopus 로고
    • Fenestration of the Fontan circuit as treatment for plastic bronchitis
    • Wilson J., Russell J., Williams W., et al. Fenestration of the Fontan circuit as treatment for plastic bronchitis. Pediatr Cardiol 2005, 26:717-719.
    • (2005) Pediatr Cardiol , vol.26 , pp. 717-719
    • Wilson, J.1    Russell, J.2    Williams, W.3
  • 31
    • 0020053276 scopus 로고
    • Rest and exercise hemodynamics after the Fontan procedure
    • Shachar G.B., Fuhrman B.P., Wang Y., et al. Rest and exercise hemodynamics after the Fontan procedure. Circulation 1982, 65:1043-1048.
    • (1982) Circulation , vol.65 , pp. 1043-1048
    • Shachar, G.B.1    Fuhrman, B.P.2    Wang, Y.3
  • 32
    • 0023709443 scopus 로고
    • Total cavopulmonary connection: a logical alternative to atriopulmonary connection for complex Fontan operations. Experimental studies and early clinical experience
    • de Leval M.R., Kilner P., Gewillig M., et al. Total cavopulmonary connection: a logical alternative to atriopulmonary connection for complex Fontan operations. Experimental studies and early clinical experience. JThorac Cardiovasc Surg 1988, 96:682-695.
    • (1988) JThorac Cardiovasc Surg , vol.96 , pp. 682-695
    • de Leval, M.R.1    Kilner, P.2    Gewillig, M.3
  • 33
    • 0028849270 scopus 로고
    • Comparison by computerized numeric modeling of energy losses in different Fontan connections
    • Van Haesdonck J.M., Mertens L., Sizaire R., et al. Comparison by computerized numeric modeling of energy losses in different Fontan connections. Circulation 1995, 92:II322-II326.
    • (1995) Circulation , vol.92
    • Van Haesdonck, J.M.1    Mertens, L.2    Sizaire, R.3
  • 34
    • 0032868778 scopus 로고    scopus 로고
    • Management of late complications after classic Fontan procedure by conversion to total cavopulmonary connection
    • Conte S., Gewillig M., Eyskens B., et al. Management of late complications after classic Fontan procedure by conversion to total cavopulmonary connection. Cardiovasc Surg 1999, 7:651-655.
    • (1999) Cardiovasc Surg , vol.7 , pp. 651-655
    • Conte, S.1    Gewillig, M.2    Eyskens, B.3
  • 35
    • 0000236848 scopus 로고    scopus 로고
    • The favorable impact of arrhythmia surgery on total cavopulmonary artery Fontan conversion. Seminars in thoracic and cardiovascular surgery
    • Mavroudis C., Deal B.J., Backer C.L., et al. The favorable impact of arrhythmia surgery on total cavopulmonary artery Fontan conversion. Seminars in thoracic and cardiovascular surgery. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 1999, 2:143-156.
    • (1999) Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu , vol.2 , pp. 143-156
    • Mavroudis, C.1    Deal, B.J.2    Backer, C.L.3
  • 36
    • 78649961606 scopus 로고    scopus 로고
    • Living at an altitude adversely affects exercise capacity in Fontan patients
    • Darst J.R., Vezmar M., McCrindle B.W., et al. Living at an altitude adversely affects exercise capacity in Fontan patients. Cardiol Young 2010, 20:593-601.
    • (2010) Cardiol Young , vol.20 , pp. 593-601
    • Darst, J.R.1    Vezmar, M.2    McCrindle, B.W.3
  • 37
    • 79953055063 scopus 로고    scopus 로고
    • Impact of oral sildenafil on exercise performance in children and young adults after the Fontan operation: a randomized, double-blind, placebo-controlled, crossover trial
    • Goldberg D.J., French B., McBride M.G., et al. Impact of oral sildenafil on exercise performance in children and young adults after the Fontan operation: a randomized, double-blind, placebo-controlled, crossover trial. Circulation 2011, 123:1185-1193.
    • (2011) Circulation , vol.123 , pp. 1185-1193
    • Goldberg, D.J.1    French, B.2    McBride, M.G.3
  • 38
    • 70349221143 scopus 로고    scopus 로고
    • The effect of bosentan in patients with a failing Fontan circulation
    • Ovaert C., Thijs D., Dewolf D., et al. The effect of bosentan in patients with a failing Fontan circulation. Cardiol Young 2009, 19:331-339.
    • (2009) Cardiol Young , vol.19 , pp. 331-339
    • Ovaert, C.1    Thijs, D.2    Dewolf, D.3
  • 39
    • 84885640563 scopus 로고    scopus 로고
    • Effect of inhaled iloprost on the exercise function of Fontan patients: a demonstration of concept
    • Rhodes J., Ubeda-Tikkanen A., Clair M., et al. Effect of inhaled iloprost on the exercise function of Fontan patients: a demonstration of concept. Int J Cardiol 2013, 168(3):2435-2440.
    • (2013) Int J Cardiol , vol.168 , Issue.3 , pp. 2435-2440
    • Rhodes, J.1    Ubeda-Tikkanen, A.2    Clair, M.3
  • 40
    • 0025037294 scopus 로고
    • Baffle fenestration with subsequent transcatheter closure. Modification of the Fontan operation for patients at increased risk
    • Bridges N.D., Lock J.E., Castaneda A.R. Baffle fenestration with subsequent transcatheter closure. Modification of the Fontan operation for patients at increased risk. Circulation 1990, 82:1681-1689.
    • (1990) Circulation , vol.82 , pp. 1681-1689
    • Bridges, N.D.1    Lock, J.E.2    Castaneda, A.R.3
  • 41
    • 0023883384 scopus 로고
    • Hemodynamic responses to isolated increments in heart rate by atrial pacing after a Fontan procedure
    • Barber G., Di Sessa T., Child J.S., et al. Hemodynamic responses to isolated increments in heart rate by atrial pacing after a Fontan procedure. Am Heart J 1988, 115:837-841.
    • (1988) Am Heart J , vol.115 , pp. 837-841
    • Barber, G.1    Di Sessa, T.2    Child, J.S.3
  • 42
    • 0035075525 scopus 로고    scopus 로고
    • Atrial pacing: an alternative treatment for protein-losing enteropathy after the Fontan operation
    • Cohen M.I., Rhodes L.A., Wernovsky G., et al. Atrial pacing: an alternative treatment for protein-losing enteropathy after the Fontan operation. JThorac Cardiovasc Surg 2001, 121:582-583.
    • (2001) JThorac Cardiovasc Surg , vol.121 , pp. 582-583
    • Cohen, M.I.1    Rhodes, L.A.2    Wernovsky, G.3
  • 43
    • 0030805363 scopus 로고    scopus 로고
    • Enalapril does not enhance exercise capacity in patients after Fontan procedure
    • Kouatli A.A., Garcia J.A., Zellers T.M., et al. Enalapril does not enhance exercise capacity in patients after Fontan procedure. Circulation 1997, 96:1507-1512.
    • (1997) Circulation , vol.96 , pp. 1507-1512
    • Kouatli, A.A.1    Garcia, J.A.2    Zellers, T.M.3
  • 44
    • 49549092535 scopus 로고    scopus 로고
    • Right-sided univentricular cardiac assistance in a failing Fontan circulation
    • Pretre R., Haussler A., Bettex D., et al. Right-sided univentricular cardiac assistance in a failing Fontan circulation. Ann Thorac Surg 2008, 86:1018-1020.
    • (2008) Ann Thorac Surg , vol.86 , pp. 1018-1020
    • Pretre, R.1    Haussler, A.2    Bettex, D.3
  • 45
    • 84888047639 scopus 로고    scopus 로고
    • Successful use of the total artificial heart in the failing Fontan circulation
    • in press.
    • Rossano J, Goldberg D, Fuller S, etal. Successful use of the total artificial heart in the failing Fontan circulation. Ann Thorac Surg, in press.
    • Ann Thorac Surg
    • Rossano, J.1    Goldberg, D.2    Fuller, S.3
  • 46
    • 84873648681 scopus 로고    scopus 로고
    • Is heart transplantation for complex congenital heart disease a good option? A 25-year single centre experience
    • [discussion: 611]
    • Seddio F., Gorislavets N., Iacovoni A., et al. Is heart transplantation for complex congenital heart disease a good option? A 25-year single centre experience. Eur J Cardiothorac Surg 2013, 43:605-611. [discussion: 611].
    • (2013) Eur J Cardiothorac Surg , vol.43 , pp. 605-611
    • Seddio, F.1    Gorislavets, N.2    Iacovoni, A.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.