Blood-brain barrier impairment in MPS III patients

BMC Neurology

Volumn 13, Issue , 2013, Pages

  Garbuzova Davis, Svitlana ^a   Mirtyl, Santhia ^a   Sallot, Sebastian A ^a   Hernandez Ontiveros, Diana G ^a   Haller, Edward ^b   Sanberg, Paul R ^a  

^a UNIVERSITY OF SOUTH FLORIDA   (United States)

^b UNIVERSITY OF SOUTH FLORIDA   (United States)

Author keywords

Blood brain barrier; Endothelial cells; Lysosomal accumulation; Mucopolysaccharidosis type III; Patients; Pericytes

Indexed keywords

CLAUDIN 5; IMMUNOGLOBULIN G; OCCLUDIN; TIGHT JUNCTION PROTEIN;

ADULT; ARTICLE; AUTOPHAGOSOME; AUTOPSY; BASEMENT MEMBRANE; BLOOD BRAIN BARRIER; BRAIN ATROPHY; BRAIN CAPILLARY ENDOTHELIAL CELL; CAPILLARY LEAK SYNDROME; CELL DAMAGE; CEREBELLUM; CHILD; CONTROLLED STUDY; EDEMA; EXTRACELLULAR SPACE; FEMALE; FUNCTIONAL DISEASE; HIPPOCAMPUS; HUMAN; HUMAN TISSUE; LYSOSOME; MALE; PERICYTE; PRIMARY MOTOR CORTEX; PROTEIN EXPRESSION; PUTAMEN; SANFILIPPO SYNDROME; SCHOOL CHILD;

ADULT; BLOOD-BRAIN BARRIER; BRAIN; CHILD; FEMALE; HUMANS; MALE; MUCOPOLYSACCHARIDOSIS III; YOUNG ADULT;

EID: 84887361050     PISSN: None     EISSN: 14712377     Source Type: Journal    
DOI: 10.1186/1471-2377-13-174     Document Type: Article

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