-
1
-
-
0033779795
-
Deflazacort increases laminin expression and myogenic repair, and induces early persistent functional gain in mdx mouse muscular dystrophy
-
Anderson, J. E., Weber, M. and Vargas, C. (2000). Deflazacort increases laminin expression and myogenic repair, and induces early persistent functional gain in mdx mouse muscular dystrophy. Cell Transplant. 9, 551-564.
-
(2000)
Cell Transplant.
, vol.9
, pp. 551-564
-
-
Anderson, J.E.1
Weber, M.2
Vargas, C.3
-
2
-
-
0028280495
-
Deflazacort in Duchenne dystrophy: Study of long-term effect
-
Angelini, C., Pegoraro, E., Turella, E., Intino, M. T., Pini, A. and Costa, C. (1994). Deflazacort in Duchenne dystrophy: study of long-term effect. Muscle Nerve 17, 386-391.
-
(1994)
Muscle Nerve
, vol.17
, pp. 386-391
-
-
Angelini, C.1
Pegoraro, E.2
Turella, E.3
Intino, M.T.4
Pini, A.5
Costa, C.6
-
3
-
-
12144263634
-
Intermittent prednisone therapy in Duchenne muscular dystrophy: A randomized controlled trial
-
Beenakker, E. A., Fock, J. M., Van Tol, M. J., Maurits, N. M., Koopman, H. M., Brouwer, O. F. and Van der Hoeven, J. H. (2005). Intermittent prednisone therapy in Duchenne muscular dystrophy: a randomized controlled trial. Arch. Neurol. 62, 128-132.
-
(2005)
Arch. Neurol.
, vol.62
, pp. 128-132
-
-
Beenakker, E.A.1
Fock, J.M.2
Van Tol, M.J.3
Maurits, N.M.4
Koopman, H.M.5
Brouwer, O.F.6
Van Der Hoeven, J.H.7
-
4
-
-
33744784550
-
α7β1-Integrin regulates mechanotransduction and prevents skeletal muscle injury
-
Boppart, M. D., Burkin, D. J. and Kaufman, S. J. (2006). α7β1-Integrin regulates mechanotransduction and prevents skeletal muscle injury. Am. J. Physiol. 290, C1660-C1665.
-
(2006)
Am. J. Physiol.
, vol.290
-
-
Boppart, M.D.1
Burkin, D.J.2
Kaufman, S.J.3
-
5
-
-
0345731966
-
X chromosome-linked muscular dystrophy (mdx) in the mouse
-
Bulfield, G., Siller, W. G., Wight, P. A. and Moore, K. J. (1984). X chromosome-linked muscular dystrophy (mdx) in the mouse. Proc. Natl. Acad. Sci. USA 81, 1189-1192.
-
(1984)
Proc. Natl. Acad. Sci. USA
, vol.81
, pp. 1189-1192
-
-
Bulfield, G.1
Siller, W.G.2
Wight, P.A.3
Moore, K.J.4
-
6
-
-
0032588041
-
The alpha7beta1 integrin in muscle development and disease
-
Burkin, D. J. and Kaufman, S. J. (1999). The alpha7beta1 integrin in muscle development and disease. Cell Tissue Res. 296, 183-190.
-
(1999)
Cell Tissue Res.
, vol.296
, pp. 183-190
-
-
Burkin, D.J.1
Kaufman, S.J.2
-
7
-
-
0035911960
-
Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice
-
Burkin, D. J., Wallace, G. Q., Nicol, K. J., Kaufman, D. J. and Kaufman, S. J. (2001). Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice. J. Cell Biol. 152, 1207-1218.
-
(2001)
J. Cell Biol.
, vol.152
, pp. 1207-1218
-
-
Burkin, D.J.1
Wallace, G.Q.2
Nicol, K.J.3
Kaufman, D.J.4
Kaufman, S.J.5
-
8
-
-
11144231268
-
Transgenic expression of alpha7beta1 integrin maintains muscle integrity, increases regenerative capacity, promotes hypertrophy, and reduces cardiomyopathy in dystrophic mice
-
Burkin, D. J., Wallace, G. Q., Milner, D. J., Chaney, E. J., Mulligan, J. A. and Kaufman, S. J. (2005). Transgenic expression of alpha7beta1 integrin maintains muscle integrity, increases regenerative capacity, promotes hypertrophy, and reduces cardiomyopathy in dystrophic mice. Am. J. Pathol. 166, 253-263.
-
(2005)
Am. J. Pathol.
, vol.166
, pp. 253-263
-
-
Burkin, D.J.1
Wallace, G.Q.2
Milner, D.J.3
Chaney, E.J.4
Mulligan, J.A.5
Kaufman, S.J.6
-
9
-
-
0023883621
-
The homologue of the Duchenne locus is defective in X-linked muscular dystrophy of dogs
-
Cooper, B. J., Winand, N. J., Stedman, H., Valentine, B. A., Hoffman, E. P., Kunkel, L. M., Scott, M. O., Fischbeck, K. H., Kornegay, J. N., Avery, R. J. et al. (1988). The homologue of the Duchenne locus is defective in X-linked muscular dystrophy of dogs. Nature 334, 154-156.
-
(1988)
Nature
, vol.334
, pp. 154-156
-
-
Cooper, B.J.1
Winand, N.J.2
Stedman, H.3
Valentine, B.A.4
Hoffman, E.P.5
Kunkel, L.M.6
Scott, M.O.7
Fischbeck, K.H.8
Kornegay, J.N.9
Avery, R.J.10
-
10
-
-
79960289893
-
Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dy(W) mouse model of merosin-deficient congenital muscular dystrophy type 1A
-
Doe, J. A., Wuebbles, R. D., Allred, E. T., Rooney, J. E., Elorza, M. and Burkin, D. J. (2011). Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dy(W) mouse model of merosin-deficient congenital muscular dystrophy type 1A. J. Cell Sci. 124, 2287-2297.
-
(2011)
J. Cell Sci.
, vol.124
, pp. 2287-2297
-
-
Doe, J.A.1
Wuebbles, R.D.2
Allred, E.T.3
Rooney, J.E.4
Elorza, M.5
Burkin, D.J.6
-
11
-
-
0026344234
-
Longterm benefit from prednisone therapy in Duchenne muscular dystrophy
-
Fenichel, G. M., Florence, J. M., Pestronk, A., Mendell, J. R., Moxley, R. T., 3rd, Griggs, R. C., Brooke, M. H., Miller, J. P., Robison, J., King, W. et al. (1991). Longterm benefit from prednisone therapy in Duchenne muscular dystrophy. Neurology 41, 1874-1877.
-
(1991)
Neurology
, vol.41
, pp. 1874-1877
-
-
Fenichel, G.M.1
Florence, J.M.2
Pestronk, A.3
Mendell, J.R.4
Moxley III, R.T.5
Griggs, R.C.6
Brooke, M.H.7
Miller, J.P.8
Robison, J.9
King, W.10
-
12
-
-
23944462348
-
Role for the alpha7beta1 integrin in vascular development and integrity
-
Flintoff-Dye, N. L., Welser, J., Rooney, J., Scowen, P., Tamowski, S., Hatton, W. and Burkin, D. J. (2005). Role for the alpha7beta1 integrin in vascular development and integrity. Dev. Dyn. 234, 11-21.
-
(2005)
Dev. Dyn.
, vol.234
, pp. 11-21
-
-
Flintoff-Dye, N.L.1
Welser, J.2
Rooney, J.3
Scowen, P.4
Tamowski, S.5
Hatton, W.6
Burkin, D.J.7
-
13
-
-
33644778843
-
Absence of alpha 7 integrin in dystrophin-deficient mice causes a myopathy similar to Duchenne muscular dystrophy
-
Guo, C., Willem, M., Werner, A., Raivich, G., Emerson, M., Neyses, L. and Mayer, U. (2006). Absence of alpha 7 integrin in dystrophin-deficient mice causes a myopathy similar to Duchenne muscular dystrophy. Hum. Mol. Genet. 15, 989-998.
-
(2006)
Hum. Mol. Genet.
, vol.15
, pp. 989-998
-
-
Guo, C.1
Willem, M.2
Werner, A.3
Raivich, G.4
Emerson, M.5
Neyses, L.6
Mayer, U.7
-
14
-
-
62549105268
-
Valproic acid activates the PI3K/Akt/mTOR pathway in muscle and ameliorates pathology in a mouse model of Duchenne muscular dystrophy
-
Gurpur, P. B., Liu, J., Burkin, D. J. and Kaufman, S. J. (2009). Valproic acid activates the PI3K/Akt/mTOR pathway in muscle and ameliorates pathology in a mouse model of Duchenne muscular dystrophy. Am. J. Pathol. 174, 999-1008.
-
(2009)
Am. J. Pathol.
, vol.174
, pp. 999-1008
-
-
Gurpur, P.B.1
Liu, J.2
Burkin, D.J.3
Kaufman, S.J.4
-
15
-
-
17344372250
-
Mutations in the integrin alpha7 gene cause congenital myopathy
-
Hayashi, Y. K., Chou, F. L., Engvall, E., Ogawa, M., Matsuda, C., Hirabayashi, S., Yokochi, K., Ziober, B. L., Kramer, R. H., Kaufman, S. J. et al. (1998). Mutations in the integrin alpha7 gene cause congenital myopathy. Nat. Genet. 19, 94-97.
-
(1998)
Nat. Genet.
, vol.19
, pp. 94-97
-
-
Hayashi, Y.K.1
Chou, F.L.2
Engvall, E.3
Ogawa, M.4
Matsuda, C.5
Hirabayashi, S.6
Yokochi, K.7
Ziober, B.L.8
Kramer, R.H.9
Kaufman, S.J.10
-
16
-
-
0030809116
-
Altered expression of the alpha7beta1 integrin in human and murine muscular dystrophies
-
Hodges, B. L., Hayashi, Y. K., Nonaka, I., Wang, W., Arahata, K. and Kaufman, S. J. (1997). Altered expression of the alpha7beta1 integrin in human and murine muscular dystrophies. J. Cell Sci. 110, 2873-2881.
-
(1997)
J. Cell Sci.
, vol.110
, pp. 2873-2881
-
-
Hodges, B.L.1
Hayashi, Y.K.2
Nonaka, I.3
Wang, W.4
Arahata, K.5
Kaufman, S.J.6
-
17
-
-
0023614188
-
Dystrophin: The protein product of the Duchenne muscular dystrophy locus
-
Hoffman, E. P., Brown, R. H., Jr and Kunkel, L. M. (1987). Dystrophin: the protein product of the Duchenne muscular dystrophy locus. Cell 51, 919-928.
-
(1987)
Cell
, vol.51
, pp. 919-928
-
-
Hoffman, E.P.1
Brown Jr., R.H.2
Kunkel, L.M.3
-
18
-
-
0023706738
-
Muscular dystrophy in a litter of golden retriever dogs
-
Kornegay, J. N., Tuler, S. M., Miller, D. M. and Levesque, D. C. (1988). Muscular dystrophy in a litter of golden retriever dogs. Muscle Nerve 11, 1056-1064.
-
(1988)
Muscle Nerve
, vol.11
, pp. 1056-1064
-
-
Kornegay, J.N.1
Tuler, S.M.2
Miller, D.M.3
Levesque, D.C.4
-
19
-
-
84857374252
-
Canine models of Duchenne muscular dystrophy and their use in therapeutic strategies
-
Kornegay, J. N., Bogan, J. R., Bogan, D. J., Childers, M. K., Li, J., Nghiem, P., Detwiler, D. A., Larsen, C. A., Grange, R. W., Bhavaraju-Sanka, R. K. et al. (2012). Canine models of Duchenne muscular dystrophy and their use in therapeutic strategies. Mamm. Genome 23, 85-108.
-
(2012)
Mamm. Genome
, vol.23
, pp. 85-108
-
-
Kornegay, J.N.1
Bogan, J.R.2
Bogan, D.J.3
Childers, M.K.4
Li, J.5
Nghiem, P.6
Detwiler, D.A.7
Larsen, C.A.8
Grange, R.W.9
Bhavaraju-Sanka, R.K.10
-
20
-
-
10044289327
-
Effects of prednisone in canine muscular dystrophy
-
Liu, J. M., Okamura, C. S., Bogan, D. J., Bogan, J. R., Childers, M. K. and Kornegay, J. N. (2004). Effects of prednisone in canine muscular dystrophy. Muscle Nerve 30, 767-773.
-
(2004)
Muscle Nerve
, vol.30
, pp. 767-773
-
-
Liu, J.M.1
Okamura, C.S.2
Bogan, D.J.3
Bogan, J.R.4
Childers, M.K.5
Kornegay, J.N.6
-
21
-
-
39349089905
-
Increasing alpha 7 beta 1-integrin promotes muscle cell proliferation, adhesion, and resistance to apoptosis without changing gene expression
-
Liu, J., Burkin, D. J. and Kaufman, S. J. (2008a). Increasing alpha 7 beta 1-integrin promotes muscle cell proliferation, adhesion, and resistance to apoptosis without changing gene expression. Am. J. Physiol. 294, C627-C640.
-
(2008)
Am. J. Physiol.
, vol.294
-
-
Liu, J.1
Burkin, D.J.2
Kaufman, S.J.3
-
22
-
-
58149102151
-
Genetically determined proteolytic cleavage modulates alpha7beta1 integrin function
-
Liu, J., Gurpur, P. B. and Kaufman, S. J. (2008b). Genetically determined proteolytic cleavage modulates alpha7beta1 integrin function. J. Biol. Chem. 283, 35668-35678.
-
(2008)
J. Biol. Chem.
, vol.283
, pp. 35668-35678
-
-
Liu, J.1
Gurpur, P.B.2
Kaufman, S.J.3
-
23
-
-
0029988437
-
Synaptic integrins in developing, adult, and mutant muscle: Selective association of alpha1, alpha7A, and alpha7B integrins with the neuromuscular junction
-
Martin, P. T., Kaufman, S. J., Kramer, R. H. and Sanes, J. R. (1996). Synaptic integrins in developing, adult, and mutant muscle: selective association of alpha1, alpha7A, and alpha7B integrins with the neuromuscular junction. Dev. Biol. 174, 125-139.
-
(1996)
Dev. Biol.
, vol.174
, pp. 125-139
-
-
Martin, P.T.1
Kaufman, S.J.2
Kramer, R.H.3
Sanes, J.R.4
-
24
-
-
61849088555
-
Correlation of dystrophin-glycoprotein complex and focal adhesion complex with myosin heavy chain isoforms in rat skeletal muscle
-
Masuda, S., Hayashi, T., Hashimoto, T. and Taguchi, S. (2009). Correlation of dystrophin-glycoprotein complex and focal adhesion complex with myosin heavy chain isoforms in rat skeletal muscle. Acta Physiol. (Oxf.) 195, 483-494.
-
(2009)
Acta Physiol. (Oxf.)
, vol.195
, pp. 483-494
-
-
Masuda, S.1
Hayashi, T.2
Hashimoto, T.3
Taguchi, S.4
-
25
-
-
0030724952
-
Absence of integrin alpha 7 causes a novel form of muscular dystrophy
-
Mayer, U., Saher, G., Fässler, R., Bornemann, A., Echtermeyer, F., von der Mark, H., Miosge, N., Pöschl, E. and von der Mark, K. (1997). Absence of integrin alpha 7 causes a novel form of muscular dystrophy. Nat. Genet. 17, 318-323.
-
(1997)
Nat. Genet.
, vol.17
, pp. 318-323
-
-
Mayer, U.1
Saher, G.2
Fässler, R.3
Bornemann, A.4
Echtermeyer, F.5
Von Der Mark, H.6
Miosge, N.7
Pöschl, E.8
Von Der Mark, K.9
-
26
-
-
0037311221
-
Early prednisone treatment in Duchenne muscular dystrophy
-
Merlini, L., Cicognani, A., Malaspina, E., Gennari, M., Gnudi, S., Talim, B. and Franzoni, E. (2003). Early prednisone treatment in Duchenne muscular dystrophy. Muscle Nerve 27, 222-227.
-
(2003)
Muscle Nerve
, vol.27
, pp. 222-227
-
-
Merlini, L.1
Cicognani, A.2
Malaspina, E.3
Gennari, M.4
Gnudi, S.5
Talim, B.6
Franzoni, E.7
-
27
-
-
0022496289
-
Isolation of candidate cDNAs for portions of the Duchenne muscular dystrophy gene
-
Monaco, A. P., Neve, R. L., Colletti-Feener, C., Bertelson, C. J., Kurnit, D. M. and Kunkel, L. M. (1986). Isolation of candidate cDNAs for portions of the Duchenne muscular dystrophy gene. Nature 323, 646-650.
-
(1986)
Nature
, vol.323
, pp. 646-650
-
-
Monaco, A.P.1
Neve, R.L.2
Colletti-Feener, C.3
Bertelson, C.J.4
Kurnit, D.M.5
Kunkel, L.M.6
-
28
-
-
79955618736
-
Current status of pharmaceutical and genetic therapeutic approaches to treat DMD
-
Pichavant, C., Aartsma-Rus, A., Clemens, P. R., Davies, K. E., Dickson, G., Takeda, S., Wilton, S. D., Wolff, J. A., Wooddell, C. I., Xiao, X. et al. (2011). Current status of pharmaceutical and genetic therapeutic approaches to treat DMD. Mol. Ther. 19, 830-840.
-
(2011)
Mol. Ther.
, vol.19
, pp. 830-840
-
-
Pichavant, C.1
Aartsma-Rus, A.2
Clemens, P.R.3
Davies, K.E.4
Dickson, G.5
Takeda, S.6
Wilton, S.D.7
Wolff, J.A.8
Wooddell, C.I.9
Xiao, X.10
-
29
-
-
0029555074
-
Deflazacort vs. Prednisone in Duchenne muscular dystrophy: Trends of an ongoing study
-
Reitter, B. (1995). Deflazacort vs. prednisone in Duchenne muscular dystrophy: trends of an ongoing study. Brain Dev. 17 Suppl., 39-43.
-
(1995)
Brain Dev.
, vol.17
, Issue.SUPPL.
, pp. 39-43
-
-
Reitter, B.1
-
30
-
-
33745493594
-
Severe muscular dystrophy in mice that lack dystrophin and alpha7 integrin
-
Rooney, J. E., Welser, J. V., Dechert, M. A., Flintoff-Dye, N. L., Kaufman, S. J. and Burkin, D. J. (2006). Severe muscular dystrophy in mice that lack dystrophin and alpha7 integrin. J. Cell Sci. 119, 2185-2195.
-
(2006)
J. Cell Sci.
, vol.119
, pp. 2185-2195
-
-
Rooney, J.E.1
Welser, J.V.2
Dechert, M.A.3
Flintoff-Dye, N.L.4
Kaufman, S.J.5
Burkin, D.J.6
-
31
-
-
66049117408
-
Laminin-111 protein therapy prevents muscle disease in the mdx mouse model for Duchenne muscular dystrophy
-
Rooney, J. E., Gurpur, P. B. and Burkin, D. J. (2009). Laminin-111 protein therapy prevents muscle disease in the mdx mouse model for Duchenne muscular dystrophy. Proc. Natl. Acad. Sci. USA 106, 7991-7996.
-
(2009)
Proc. Natl. Acad. Sci. USA
, vol.106
, pp. 7991-7996
-
-
Rooney, J.E.1
Gurpur, P.B.2
Burkin, D.J.3
-
32
-
-
84859258298
-
Glucocorticoid-treated mice are an inappropriate positive control for long-term preclinical studies in the mdx mouse
-
Sali, A., Guerron, A. D., Gordish-Dressman, H., Spurney, C. F., Iantorno, M., Hoffman, E. P. and Nagaraju, K. (2012). Glucocorticoid-treated mice are an inappropriate positive control for long-term preclinical studies in the mdx mouse. PLoS ONE 7, e34204.
-
(2012)
PLoS ONE
, vol.7
-
-
Sali, A.1
Guerron, A.D.2
Gordish-Dressman, H.3
Spurney, C.F.4
Iantorno, M.5
Hoffman, E.P.6
Nagaraju, K.7
-
33
-
-
0027787640
-
Expression of alpha 7 integrin cytoplasmic domains during skeletal muscle development: Alternate forms, conformational change, and homologies with serine/threonine kinases and tyrosine phosphatases
-
Song, W. K., Wang, W., Sato, H., Bielser, D. A. and Kaufman, S. J. (1993). Expression of alpha 7 integrin cytoplasmic domains during skeletal muscle development: alternate forms, conformational change, and homologies with serine/threonine kinases and tyrosine phosphatases. J. Cell Sci. 106, 1139-1152.
-
(1993)
J. Cell Sci.
, vol.106
, pp. 1139-1152
-
-
Song, W.K.1
Wang, W.2
Sato, H.3
Bielser, D.A.4
Kaufman, S.J.5
|