-
1
-
-
84878115619
-
-
Cystic Fibrosis Trust, Date last accessed: April 23,. Date last updated: December 14, 2011
-
Cystic Fibrosis Trust. UK CF Registry Annual data report 2010. www.cysticfibrosis.org.uk/media/108230/ CR_Annual_Data_Report_2010_Dec_11.pdf Date last accessed: April 23, 2012. Date last updated: December 14, 2011.
-
(2012)
UK CF Registry Annual data report 2010
-
-
-
2
-
-
79955008735
-
Targeting lung attacks
-
FitzGerald JM. Targeting lung attacks. Thorax 2011; 66: 365-366.
-
(2011)
Thorax
, vol.66
, pp. 365-366
-
-
FitzGerald, J.M.1
-
3
-
-
0034998451
-
Defining an exacerbation of pulmonary disease in cystic fibrosis
-
Dakin C, Henry RL, Field P, et al. Defining an exacerbation of pulmonary disease in cystic fibrosis. Pediatr Pulmonol 2001; 31: 436-442.
-
(2001)
Pediatr Pulmonol
, vol.31
, pp. 436-442
-
-
Dakin, C.1
Henry, R.L.2
Field, P.3
-
4
-
-
34748903941
-
-
5th Edn. Cystic Fibrosis Foundation, Date last accessed April 23, 2012
-
Cunningham JC, Taussig LM. An Introduction to Cystic Fibrosis for Patients and Families. 5th Edn. Cystic Fibrosis Foundation, 2003. www.cff.org/uploadedfiles/treatments/cfcareguidelines/diagnosis/an-introduction-to-cf-for-patientsand-families.pdf Date last accessed April 23, 2012.
-
(2003)
An Introduction to Cystic Fibrosis for Patients and Families
-
-
Cunningham, J.C.1
Taussig, L.M.2
-
5
-
-
0141816759
-
Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: A randomized controlled trial
-
Saiman L, Marshall BC, Mayer-Hamblett N, et al. Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial. JAMA 2003; 290: 1749-1756.
-
(2003)
JAMA
, vol.290
, pp. 1749-1756
-
-
Saiman, L.1
Marshall, B.C.2
Mayer-Hamblett, N.3
-
6
-
-
0033531143
-
Intermittent administration of inhaled tobramycin in patients with cystic fibrosis
-
Cystic Fibrosis Inhaled Tobramycin Study Group
-
Ramsey BW, Pepe MS, Quan JM, et al. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group. N Engl J Med 1999; 340: 23-30.
-
(1999)
N Engl J Med
, vol.340
, pp. 23-30
-
-
Ramsey, B.W.1
Pepe, M.S.2
Quan, J.M.3
-
7
-
-
80051796005
-
Approach to treating cystic fibrosis pulmonary exacerbations varies widely across US CF care centers
-
Kraynack NC, Gothard MD, Falletta LM, et al. Approach to treating cystic fibrosis pulmonary exacerbations varies widely across US CF care centers. Pediatr Pulmonol 2011; 46: 870-881.
-
(2011)
Pediatr Pulmonol
, vol.46
, pp. 870-881
-
-
Kraynack, N.C.1
Gothard, M.D.2
Falletta, L.M.3
-
8
-
-
0028129568
-
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
-
The Pulmozyme Study Group
-
Fuchs HJ, Borowitz DS, Christiansen DH, et al. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group. N Engl J Med 1994; 331: 637-642.
-
(1994)
N Engl J Med
, vol.331
, pp. 637-642
-
-
Fuchs, H.J.1
Borowitz, D.S.2
Christiansen, D.H.3
-
9
-
-
30944466084
-
A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
-
Elkins MR, Robinson M, Rose BR, et al. A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. N Engl J Med 2006; 354: 229-240.
-
(2006)
N Engl J Med
, vol.354
, pp. 229-240
-
-
Elkins, M.R.1
Robinson, M.2
Rose, B.R.3
-
10
-
-
67349204479
-
Early anti-pseudomonal acquisition in young patients with cystic fibrosis: Rationale and design of the EPIC clinical trial and observational study
-
Treggiari MM, Rosenfeld M, Mayer-Hamblett N, et al. Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study. Contemp Clin Trials 2009; 30: 256-268.
-
(2009)
Contemp Clin Trials
, vol.30
, pp. 256-268
-
-
Treggiari, M.M.1
Rosenfeld, M.2
Mayer-Hamblett, N.3
-
12
-
-
84879417125
-
Pulmonary exacerbations in cystic fibrosis: Young children with characteristic signs and symptoms
-
[In press DOI: 10.1002/ppul.22658]
-
Regelmann WE, Schechter MS, Wagener JS, et al. Pulmonary exacerbations in cystic fibrosis: young children with characteristic signs and symptoms. Pediatr Pulmonol 2012 [In press DOI: 10.1002/ppul.22658].
-
(2012)
Pediatr Pulmonol
-
-
Regelmann, W.E.1
Schechter, M.S.2
Wagener, J.S.3
-
13
-
-
79958077769
-
Pulmonary exacerbation: Towards a definition for use in clinical trials. Report from the EuroCareCF Working Group on outcome parameters in clinical trials
-
Bilton D, Canny G, Conway S, et al. Pulmonary exacerbation: towards a definition for use in clinical trials. Report from the EuroCareCF Working Group on outcome parameters in clinical trials. J Cyst Fibros 2011; 10: Suppl. 2, S79-S81.
-
(2011)
J Cyst Fibros
, vol.10
, Issue.SUPPL. 2
-
-
Bilton, D.1
Canny, G.2
Conway, S.3
-
14
-
-
70350446684
-
Cystic fibrosis pulmonary guidelines: Treatment of pulmonary exacerbations
-
Flume PA, Mogayzel PJ Jr, Robinson KA, et al. Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations. Am J Respir Crit Care Med 2009; 180: 802-808.
-
(2009)
Am J Respir Crit Care Med
, vol.180
, pp. 802-808
-
-
Flume, P.A.1
Mogayzel Jr., P.J.2
Robinson, K.A.3
-
15
-
-
0032972209
-
Oxidative stress during acute respiratory exacerbations in cystic fibrosis
-
McGrath LT, Mallon P, Dowey L, et al. Oxidative stress during acute respiratory exacerbations in cystic fibrosis. Thorax 1999; 54: 518-523.
-
(1999)
Thorax
, vol.54
, pp. 518-523
-
-
McGrath, L.T.1
Mallon, P.2
Dowey, L.3
-
16
-
-
34547731349
-
The effect of treatment of cystic fibrosis pulmonary exacerbations on airways and systemic inflammation
-
Downey DG, Brockbank S, Martin SL, et al. The effect of treatment of cystic fibrosis pulmonary exacerbations on airways and systemic inflammation. Pediatr Pulmonol 2007; 42: 729-735.
-
(2007)
Pediatr Pulmonol
, vol.42
, pp. 729-735
-
-
Downey, D.G.1
Brockbank, S.2
Martin, S.L.3
-
17
-
-
84860600969
-
Effect of acute exacerbations on skeletal muscle strength and physical activity in cystic fibrosis
-
Wieboldt J, Atallah L, Kelly JL, et al. Effect of acute exacerbations on skeletal muscle strength and physical activity in cystic fibrosis. J Cyst Fibros 2012; 11: 209-215.
-
(2012)
J Cyst Fibros
, vol.11
, pp. 209-215
-
-
Wieboldt, J.1
Atallah, L.2
Kelly, J.L.3
-
18
-
-
69549105799
-
Serum matrix metalloproteinases in adult CF patients: Relation to pulmonary exacerbation
-
Roderfeld M, Rath T, Schulz R, et al. Serum matrix metalloproteinases in adult CF patients: relation to pulmonary exacerbation. J Cyst Fibros 2009; 8: 338-347.
-
(2009)
J Cyst Fibros
, vol.8
, pp. 338-347
-
-
Roderfeld, M.1
Rath, T.2
Schulz, R.3
-
19
-
-
33845687299
-
Oxidative stress and lipid-derived inflammatory mediators during acute exacerbations of cystic fibrosis
-
Reid DW, Misso N, Aggarwal S, et al. Oxidative stress and lipid-derived inflammatory mediators during acute exacerbations of cystic fibrosis. Respirology 2007; 12: 63-69.
-
(2007)
Respirology
, vol.12
, pp. 63-69
-
-
Reid, D.W.1
Misso, N.2
Aggarwal, S.3
-
20
-
-
54249153391
-
Biomarkers in exhaled breath condensate indicate presence and severity of cystic fibrosis in children
-
Robroeks CM, Rosias PP, van Vliet D, et al. Biomarkers in exhaled breath condensate indicate presence and severity of cystic fibrosis in children. Pediatr Allergy Immunol 2008; 19: 652-659.
-
(2008)
Pediatr Allergy Immunol
, vol.19
, pp. 652-659
-
-
Robroeks, C.M.1
Rosias, P.P.2
van Vliet, D.3
-
21
-
-
28344446191
-
Biomarkers of neutrophilic inflammation in exhaled air of cystic fibrosis children with bacterial airway infections
-
Bodini A, D'Orazio C, Peroni D, et al. Biomarkers of neutrophilic inflammation in exhaled air of cystic fibrosis children with bacterial airway infections. Pediatr Pulmonol 2005; 40: 494-499.
-
(2005)
Pediatr Pulmonol
, vol.40
, pp. 494-499
-
-
Bodini, A.1
D'Orazio, C.2
Peroni, D.3
-
22
-
-
34948827980
-
IL-8 and pH values in exhaled condensate after antibiotics in cystic fibrosis children
-
Bodini A, D'Orazio C, Peroni DG, et al. IL-8 and pH values in exhaled condensate after antibiotics in cystic fibrosis children. Int J Immunopathol Pharmacol 2007; 20: 467-472.
-
(2007)
Int J Immunopathol Pharmacol
, vol.20
, pp. 467-472
-
-
Bodini, A.1
D'Orazio, C.2
Peroni, D.G.3
-
23
-
-
84865101337
-
Urinary desmosine: A biomarker of structural lung injury during CF pulmonary exacerbation
-
Laguna TA, Wagner BD, Starcher B, et al. Urinary desmosine: a biomarker of structural lung injury during CF pulmonary exacerbation. Pediatr Pulmonol 2012; 47: 856-863.
-
(2012)
Pediatr Pulmonol
, vol.47
, pp. 856-863
-
-
Laguna, T.A.1
Wagner, B.D.2
Starcher, B.3
-
24
-
-
0035865730
-
Predictive 5-year survivorship model of cystic fibrosis
-
Liou TG, Adler FR, Fitzsimmons SC, et al. Predictive 5-year survivorship model of cystic fibrosis. Am J Epidemiol 2001; 153: 345-352.
-
(2001)
Am J Epidemiol
, vol.153
, pp. 345-352
-
-
Liou, T.G.1
Adler, F.R.2
Fitzsimmons, S.C.3
-
25
-
-
78649759755
-
Cystic fibrosis and survival to 40 years: A case-control study
-
Simmonds NJ, Macneill SJ, Cullinan P, et al. Cystic fibrosis and survival to 40 years: a case-control study. Eur Respir J 2010; 36: 1277-1283.
-
(2010)
Eur Respir J
, vol.36
, pp. 1277-1283
-
-
Simmonds, N.J.1
McNeill, S.J.2
Cullinan, P.3
-
26
-
-
0036152764
-
Impact of recent pulmonary exacerbations on quality of life in patients with cystic fibrosis
-
Britto MT, Kotagal UR, Hornung RW, et al. Impact of recent pulmonary exacerbations on quality of life in patients with cystic fibrosis. Chest 2002; 121: 64-72.
-
(2002)
Chest
, vol.121
, pp. 64-72
-
-
Britto, M.T.1
Kotagal, U.R.2
Hornung, R.W.3
-
27
-
-
21544475912
-
The effect of infective exacerbations on sleep and neurobehavioral function in cystic fibrosis
-
Dobbin CJ, Bartlett D, Melehan K, et al. The effect of infective exacerbations on sleep and neurobehavioral function in cystic fibrosis. Am J Respir Crit Care Med 2005; 172: 99-104.
-
(2005)
Am J Respir Crit Care Med
, vol.172
, pp. 99-104
-
-
Dobbin, C.J.1
Bartlett, D.2
Melehan, K.3
-
28
-
-
0026693732
-
A cost description of an adult cystic fibrosis unit and cost analyses of different categories of patients
-
Robson M, Abbott J, Webb K, et al. A cost description of an adult cystic fibrosis unit and cost analyses of different categories of patients. Thorax 1992; 47: 684-689.
-
(1992)
Thorax
, vol.47
, pp. 684-689
-
-
Robson, M.1
Abbott, J.2
Webb, K.3
-
29
-
-
85044704751
-
The cost of medical care for patients with cystic fibrosis in a health maintenance organization
-
Lieu TA, Ray GT, Farmer G, et al. The cost of medical care for patients with cystic fibrosis in a health maintenance organization. Pediatrics 1999; 103: e72.
-
(1999)
Pediatrics
, vol.103
-
-
Lieu, T.A.1
Ray, G.T.2
Farmer, G.3
-
30
-
-
70349507503
-
Healthcare expenditures for privately insured people with cystic fibrosis
-
Ouyang L, Grosse SD, Amendah DD, et al. Healthcare expenditures for privately insured people with cystic fibrosis. Pediatr Pulmonol 2009; 44: 989-996.
-
(2009)
Pediatr Pulmonol
, vol.44
, pp. 989-996
-
-
Ouyang, L.1
Grosse, S.D.2
Amendah, D.D.3
-
31
-
-
80355127141
-
Inhaled dry powder mannitol in cystic fibrosis: An efficacy and safety study
-
Bilton D, Robinson P, Cooper P, et al. Inhaled dry powder mannitol in cystic fibrosis: an efficacy and safety study. Eur Respir J 2011; 38: 1071-1080.
-
(2011)
Eur Respir J
, vol.38
, pp. 1071-1080
-
-
Bilton, D.1
Robinson, P.2
Cooper, P.3
-
32
-
-
30344460714
-
Computed tomography correlates with pulmonary exacerbations in children with cystic fibrosis
-
Brody AS, Sucharew H, Campbell JD, et al. Computed tomography correlates with pulmonary exacerbations in children with cystic fibrosis. Am J Respir Crit Care Med 2005; 172: 1128-1132.
-
(2005)
Am J Respir Crit Care Med
, vol.172
, pp. 1128-1132
-
-
Brody, A.S.1
Sucharew, H.2
Campbell, J.D.3
-
33
-
-
33646578187
-
Objective measurement of cough during pulmonary exacerbations in adults with cystic fibrosis
-
Smith JA, Owen EC, Jones AM, et al. Objective measurement of cough during pulmonary exacerbations in adults with cystic fibrosis. Thorax 2006; 61: 425-429.
-
(2006)
Thorax
, vol.61
, pp. 425-429
-
-
Smith, J.A.1
Owen, E.C.2
Jones, A.M.3
-
34
-
-
71749105530
-
Association of socioeconomic status with the use of chronic therapies and healthcare utilization in children with cystic fibrosis
-
Schechter MS, McColley SA, Silva S, et al. Association of socioeconomic status with the use of chronic therapies and healthcare utilization in children with cystic fibrosis. J Pediatr 2009; 155: 634-639.
-
(2009)
J Pediatr
, vol.155
, pp. 634-639
-
-
Schechter, M.S.1
McColley, S.A.2
Silva, S.3
-
35
-
-
1642529559
-
Effect of ambient air pollution on pulmonary exacerbations and lung function in cystic fibrosis
-
Goss CH, Newsom SA, Schildcrout JS, et al. Effect of ambient air pollution on pulmonary exacerbations and lung function in cystic fibrosis. Am J Respir Crit Care Med 2004; 169: 816-821.
-
(2004)
Am J Respir Crit Care Med
, vol.169
, pp. 816-821
-
-
Goss, C.H.1
Newsom, S.A.2
Schildcrout, J.S.3
-
36
-
-
34447530328
-
Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis
-
Konstan MW, Morgan WJ, Butler SM, et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151: 134-139.
-
(2007)
J Pediatr
, vol.151
, pp. 134-139
-
-
Konstan, M.W.1
Morgan, W.J.2
Butler, S.M.3
-
37
-
-
79952753579
-
Pulmonary exacerbations are associated with subsequent FEV1 decline in both adults and children with cystic fibrosis
-
Sanders DB, Bittner RC, Rosenfeld M, et al. Pulmonary exacerbations are associated with subsequent FEV1 decline in both adults and children with cystic fibrosis. Pediatr Pulmonol 2011; 46: 393-400.
-
(2011)
Pediatr Pulmonol
, vol.46
, pp. 393-400
-
-
Sanders, D.B.1
Bittner, R.C.2
Rosenfeld, M.3
-
38
-
-
77957694293
-
Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation
-
Sanders DB, Bittner RC, Rosenfeld M, et al. Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation. Am J Respir Crit Care Med 2010; 182: 627-632.
-
(2010)
Am J Respir Crit Care Med
, vol.182
, pp. 627-632
-
-
Sanders, D.B.1
Bittner, R.C.2
Rosenfeld, M.3
-
39
-
-
79959852127
-
Bronchoscopy in cystic fibrosis infants diagnosed by newborn screening
-
Stafler P, Davies JC, Balfour-Lynn IM, et al. Bronchoscopy in cystic fibrosis infants diagnosed by newborn screening. Pediatr Pulmonol 2011; 46: 696-700.
-
(2011)
Pediatr Pulmonol
, vol.46
, pp. 696-700
-
-
Stafler, P.1
Davies, J.C.2
Balfour-Lynn, I.M.3
-
40
-
-
80051572617
-
Infection, inflammation, and lung function decline in infants with cystic fibrosis
-
Pillarisetti N, Williamson E, Linnane B, et al. Infection, inflammation, and lung function decline in infants with cystic fibrosis. Am J Respir Crit Care Med 2011; 184: 75-81.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 75-81
-
-
Pillarisetti, N.1
Williamson, E.2
Linnane, B.3
-
41
-
-
84862776813
-
Progression of early structural lung disease in young children with cystic fibrosis assessed using CT
-
Mott LS, Park J, Murray CP, et al. Progression of early structural lung disease in young children with cystic fibrosis assessed using CT. Thorax 2012; 67: 509-516.
-
(2012)
Thorax
, vol.67
, pp. 509-516
-
-
Mott, L.S.1
Park, J.2
Murray, C.P.3
-
42
-
-
84866070431
-
Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening
-
Hoo AF, Thia LP, Nguyen TT, et al. Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening. Thorax 2012; 67: 874-881.
-
(2012)
Thorax
, vol.67
, pp. 874-881
-
-
Hoo, A.F.1
Thia, L.P.2
Nguyen, T.T.3
-
43
-
-
79960151730
-
Effect of bronchoalveolar lavage-directed therapy on Pseudomonas aeruginosa infection and structural lung injury in children with cystic fibrosis: A randomized trial
-
Wainwright CE, Vidmar S, Armstrong DS, et al. Effect of bronchoalveolar lavage-directed therapy on Pseudomonas aeruginosa infection and structural lung injury in children with cystic fibrosis: a randomized trial. JAMA 2011; 306: 163-171.
-
(2011)
JAMA
, vol.306
, pp. 163-171
-
-
Wainwright, C.E.1
Vidmar, S.2
Armstrong, D.S.3
-
44
-
-
46749111127
-
The role of respiratory viruses in cystic fibrosis
-
Wat D, Gelder C, Hibbitts S, et al. The role of respiratory viruses in cystic fibrosis. J Cyst Fibros 2008; 7: 320-328.
-
(2008)
J Cyst Fibros
, vol.7
, pp. 320-328
-
-
Wat, D.1
Gelder, C.2
Hibbitts, S.3
-
45
-
-
84866177155
-
Role of respiratory viruses in pulmonary exacerbations in children with cystic fibrosis
-
Asner S, Waters V, Solomon M, et al. Role of respiratory viruses in pulmonary exacerbations in children with cystic fibrosis. J Cyst Fibros 2012; 11: 433-439.
-
(2012)
J Cyst Fibros
, vol.11
, pp. 433-439
-
-
Asner, S.1
Waters, V.2
Solomon, M.3
-
46
-
-
77950824214
-
Influenza-associated cystic fibrosis pulmonary exacerbations
-
Ortiz JR, Neuzil KM, Victor JC, et al. Influenza-associated cystic fibrosis pulmonary exacerbations. Chest 2010; 137: 852-860.
-
(2010)
Chest
, vol.137
, pp. 852-860
-
-
Ortiz, J.R.1
Neuzil, K.M.2
Victor, J.C.3
-
47
-
-
80052478907
-
Impact of the A (H1N1) pandemic influenza (season 2009-2010) on patients with cystic fibrosis
-
Viviani L, Assael BM, Kerem E. Impact of the A (H1N1) pandemic influenza (season 2009-2010) on patients with cystic fibrosis. J Cyst Fibrosis 2011; 10: 370-376.
-
(2011)
J Cyst Fibrosis
, vol.10
, pp. 370-376
-
-
Viviani, L.1
Assael, B.M.2
Kerem, E.3
-
48
-
-
79953002944
-
Rhinovirus infection liberates planktonic bacteria from biofilm and increases chemokine responses in cystic fibrosis airway epithelial cells
-
Chattoraj SS, Ganesan S, Jones AM, et al. Rhinovirus infection liberates planktonic bacteria from biofilm and increases chemokine responses in cystic fibrosis airway epithelial cells. Thorax 2011; 66: 333-339.
-
(2011)
Thorax
, vol.66
, pp. 333-339
-
-
Chattoraj, S.S.1
Ganesan, S.2
Jones, A.M.3
-
49
-
-
84856707861
-
Lack of an exaggerated inflammatory response on virus infection in cystic fibrosis
-
Kieninger E, Vareille M, Kopf BS, et al. Lack of an exaggerated inflammatory response on virus infection in cystic fibrosis. Eur Respir J 2012; 39: 297-304.
-
(2012)
Eur Respir J
, vol.39
, pp. 297-304
-
-
Kieninger, E.1
Vareille, M.2
Kopf, B.S.3
-
50
-
-
77953312034
-
Pulmonary exacerbations in cystic fibrosis with negative bacterial cultures
-
Zemanick ET, Wagner BD, Harris JK, et al. Pulmonary exacerbations in cystic fibrosis with negative bacterial cultures. Pediatr Pulmonol 2010; 45: 569-577.
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 569-577
-
-
Zemanick, E.T.1
Wagner, B.D.2
Harris, J.K.3
-
51
-
-
0035129011
-
Methicillin resistant Staphylococcus aureus (MRSA) infection in cystic fibrosis
-
Miall LS, McGinley NT, Brownlee KG, et al. Methicillin resistant Staphylococcus aureus (MRSA) infection in cystic fibrosis. Arch Dis Child 2001; 84: 160-162.
-
(2001)
Arch Dis Child
, vol.84
, pp. 160-162
-
-
Miall, L.S.1
McGinley, N.T.2
Brownlee, K.G.3
-
52
-
-
18844373631
-
How much do Pseudomonas biofilms contribute to symptoms of pulmonary exacerbation in cystic fibrosis?
-
Van Devanter DR, Van Dalfsen JM. How much do Pseudomonas biofilms contribute to symptoms of pulmonary exacerbation in cystic fibrosis? Pediatr Pulmonol 2005; 39: 504-506.
-
(2005)
Pediatr Pulmonol
, vol.39
, pp. 504-506
-
-
van Devanter, D.R.1
van Dalfsen, J.M.2
-
53
-
-
12144288633
-
Adult cystic fibrosis exacerbations and new strains of Pseudomonas aeruginosa
-
Aaron SD, Ramotar K, Ferris W, et al. Adult cystic fibrosis exacerbations and new strains of Pseudomonas aeruginosa. Am J Respir Crit Care Med 2004; 169: 811-815.
-
(2004)
Am J Respir Crit Care Med
, vol.169
, pp. 811-815
-
-
Aaron, S.D.1
Ramotar, K.2
Ferris, W.3
-
54
-
-
0023912397
-
Sputum changes associated with therapy for endobronchial exacerbation in cystic fibrosis
-
Smith AL, Redding G, Doershuk C, et al. Sputum changes associated with therapy for endobronchial exacerbation in cystic fibrosis. J Pediatr 1988; 112: 547-554.
-
(1988)
J Pediatr
, vol.112
, pp. 547-554
-
-
Smith, A.L.1
Redding, G.2
Doershuk, C.3
-
55
-
-
0025230752
-
Reduction of sputum Pseudomonas aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do bronchodilators and chest physiotherapy alone
-
Regelmann WE, Elliott GR, Warwick WJ, et al. Reduction of sputum Pseudomonas aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do bronchodilators and chest physiotherapy alone. Am Rev Respir Dis 1990; 141: 914-921.
-
(1990)
Am Rev Respir Dis
, vol.141
, pp. 914-921
-
-
Regelmann, W.E.1
Elliott, G.R.2
Warwick, W.J.3
-
56
-
-
80052450195
-
Does bacterial density in cystic fibrosis sputum increase prior to pulmonary exacerbation?
-
Stressmann FA, Rogers GB, Marsh P, et al. Does bacterial density in cystic fibrosis sputum increase prior to pulmonary exacerbation? J Cyst Fibros 2011; 10: 357-365.
-
(2011)
J Cyst Fibros
, vol.10
, pp. 357-365
-
-
Stressmann, F.A.1
Rogers, G.B.2
Marsh, P.3
-
57
-
-
84869120178
-
Treatment of lung infection in patients with cystic fibrosis: Current and future strategies
-
Döring G, Flume P, Heijerman H, et al. Treatment of lung infection in patients with cystic fibrosis: current and future strategies. J Cyst Fibros 2012; 11: 461-479.
-
(2012)
J Cyst Fibros
, vol.11
, pp. 461-479
-
-
Döring, G.1
Flume, P.2
Heijerman, H.3
-
58
-
-
33847050904
-
An official ATS/IDSA statement: Diagnosis, treatment, and prevention of nontuberculous mycobacterial diseases
-
Griffith DE, Aksamit T, Brown-Elliott BA, et al. An official ATS/IDSA statement: diagnosis, treatment, and prevention of nontuberculous mycobacterial diseases. Am J Respir Crit Care Med 2007; 175: 367-416.
-
(2007)
Am J Respir Crit Care Med
, vol.175
, pp. 367-416
-
-
Griffith, D.E.1
Aksamit, T.2
Brown-Elliott, B.A.3
-
60
-
-
76749097178
-
Chronic Mycobacterium abscessus infection and lung function decline in cystic fibrosis
-
Esther CR Jr, Esserman DA, Gilligan P, et al. Chronic Mycobacterium abscessus infection and lung function decline in cystic fibrosis. J Cyst Fibrosis 2010; 9: 117-123.
-
(2010)
J Cyst Fibrosis
, vol.9
, pp. 117-123
-
-
Esther Jr., C.R.1
Esserman, D.A.2
Gilligan, P.3
-
61
-
-
0003541888
-
-
Report of the UK Cystic Fibrosis Trust Antibiotic Working Group. 3rd Edn. London, Cystic Fibrosis Trust
-
Cystic Fibrosis Trust. Antibiotic treatment for cystic fibrosis. Report of the UK Cystic Fibrosis Trust Antibiotic Working Group. 3rd Edn. London, Cystic Fibrosis Trust, 2009.
-
(2009)
Antibiotic treatment for cystic fibrosis
-
-
Trust, C.F.1
-
62
-
-
59349114291
-
Diagnosing allergic bronchopulmonary aspergillosis in children with cystic fibrosis
-
Thia LP, Balfour Lynn IM. Diagnosing allergic bronchopulmonary aspergillosis in children with cystic fibrosis. Paediatr Respir Rev 2009; 10: 37-42.
-
(2009)
Paediatr Respir Rev
, vol.10
, pp. 37-42
-
-
Thia, L.P.1
Balfour Lynn, I.M.2
-
63
-
-
33746324245
-
Aspergillus bronchitis in cystic fibrosis
-
Shoseyov D, Brownlee KG, Conway SP, et al. Aspergillus bronchitis in cystic fibrosis. Chest 2006; 130: 222-226.
-
(2006)
Chest
, vol.130
, pp. 222-226
-
-
Shoseyov, D.1
Brownlee, K.G.2
Conway, S.P.3
-
64
-
-
77957868732
-
Sputum Candida albicans presages FEV1 decline and hospitaltreated exacerbations in cystic fibrosis
-
Chotirmall SH, O'Donoghue E, Bennett K, et al. Sputum Candida albicans presages FEV1 decline and hospitaltreated exacerbations in cystic fibrosis. Chest 2010; 138: 1186-1195.
-
(2010)
Chest
, vol.138
, pp. 1186-1195
-
-
Chotirmall, S.H.1
O'Donoghue, E.2
Bennett, K.3
-
65
-
-
39049142717
-
Exacerbations in cystic fibrosis: 3-Management
-
Smyth A, Elborn JS. Exacerbations in cystic fibrosis: 3-Management. Thorax 2008; 63: 180-184.
-
(2008)
Thorax
, vol.63
, pp. 180-184
-
-
Smyth, A.1
Elborn, J.S.2
-
66
-
-
0019961926
-
Antibiotic treatment of Staphylococcus aureus infection in cystic brosis
-
Szaff M, Høiby N. Antibiotic treatment of Staphylococcus aureus infection in cystic brosis. Acta Paediatr Scand 1982; 71: 821-826.
-
(1982)
Acta Paediatr Scand
, vol.71
, pp. 821-826
-
-
Szaff, M.1
Høiby, N.2
-
67
-
-
0021263330
-
Antibiotic treatment of Haemophilus inuenzae and Haemophilus parainuenzae infections in patients with cystic fibrosis
-
Pressler T, Szaff M, Høiby N. Antibiotic treatment of Haemophilus inuenzae and Haemophilus parainuenzae infections in patients with cystic fibrosis. Acta Paediatr Scand 1984; 73: 541-547.
-
(1984)
Acta Paediatr Scand
, vol.73
, pp. 541-547
-
-
Pressler, T.1
Szaff, M.2
Høiby, N.3
-
69
-
-
84155164716
-
Oral antimicrobial use in outpatient cystic fibrosis pulmonary exacerbation management: A single-center experience
-
Briggs EC, Nguyen T, Wall MA, et al. Oral antimicrobial use in outpatient cystic fibrosis pulmonary exacerbation management: a single-center experience. Clin Respir J 2012; 6: 56-64.
-
(2012)
Clin Respir J
, vol.6
, pp. 56-64
-
-
Briggs, E.C.1
Nguyen, T.2
Wall, M.A.3
-
71
-
-
0037252230
-
Factors influencing outcomes in cystic fibrosis: A center-based analysis
-
Johnson C, Butler SM, Konstan MW, et al. Factors influencing outcomes in cystic fibrosis: a center-based analysis. Chest 2003; 123: 20-27.
-
(2003)
Chest
, vol.123
, pp. 20-27
-
-
Johnson, C.1
Butler, S.M.2
Konstan, M.W.3
-
72
-
-
68049115348
-
A review of the home intravenous antibiotic service available to children with cystic fibrosis
-
Gilchrist FJ, Lenney W. A review of the home intravenous antibiotic service available to children with cystic fibrosis. Arch Dis Child 2009; 94: 647.
-
(2009)
Arch Dis Child
, vol.94
, pp. 647
-
-
Gilchrist, F.J.1
Lenney, W.2
-
73
-
-
0030878965
-
Effectiveness of home versus hospital care in the routine treatment of cystic fibrosis
-
Bosworth DG, Nielson DW. Effectiveness of home versus hospital care in the routine treatment of cystic fibrosis. Pediatr Pulmonol 1997; 24: 42-47.
-
(1997)
Pediatr Pulmonol
, vol.24
, pp. 42-47
-
-
Bosworth, D.G.1
Nielson, D.W.2
-
74
-
-
1542719752
-
Long term clinical outcome and hospital intravenous antibiotic treatment in adults with cystic fibrosis
-
Thornton J, Elliott R, Tully MP, et al. Long term clinical outcome and hospital intravenous antibiotic treatment in adults with cystic fibrosis. Thorax 2004; 59: 242-246.
-
(2004)
Thorax
, vol.59
, pp. 242-246
-
-
Thornton, J.1
Elliott, R.2
Tully, M.P.3
-
75
-
-
50849086144
-
Effectiveness of home treatment for patients with cystic fibrosis: The intravenous administration of antibiotics to treat respiratory infections
-
Termoz A, Touzet S, Bourdy S, et al. Effectiveness of home treatment for patients with cystic fibrosis: the intravenous administration of antibiotics to treat respiratory infections. Pediatr Pulmonol 2008; 43: 908-915.
-
(2008)
Pediatr Pulmonol
, vol.43
, pp. 908-915
-
-
Termoz, A.1
Touzet, S.2
Bourdy, S.3
-
76
-
-
33746656304
-
Home versus hospital intravenous antibiotic therapy for acute pulmonary exacerbations in children with cystic fibrosis
-
Nazer D, Abdulhamid I, Thomas R, et al. Home versus hospital intravenous antibiotic therapy for acute pulmonary exacerbations in children with cystic fibrosis. Pediatr Pulmonol 2006; 41: 744-749.
-
(2006)
Pediatr Pulmonol
, vol.41
, pp. 744-749
-
-
Nazer, D.1
Abdulhamid, I.2
Thomas, R.3
-
77
-
-
78349264246
-
Location and duration of treatment of cystic fibrosis respiratory exacerbations do not affect outcomes
-
Collaco JM, Green DM, Cutting GR, et al. Location and duration of treatment of cystic fibrosis respiratory exacerbations do not affect outcomes. Am J Respir Crit Care Med 2010; 182: 1137-1143.
-
(2010)
Am J Respir Crit Care Med
, vol.182
, pp. 1137-1143
-
-
Collaco, J.M.1
Green, D.M.2
Cutting, G.R.3
-
78
-
-
0036840718
-
Single and combination antibiotic susceptibilities of planktonic, adherent, and biofilm-grown Pseudomonas aeruginosa isolates cultured from sputa of adults with cystic fibrosis
-
Aaron SD, Ferris W, Ramotar K, et al. Single and combination antibiotic susceptibilities of planktonic, adherent, and biofilm-grown Pseudomonas aeruginosa isolates cultured from sputa of adults with cystic fibrosis. J Clin Microbiol 2002; 40: 4172-4179.
-
(2002)
J Clin Microbiol
, vol.40
, pp. 4172-4179
-
-
Aaron, S.D.1
Ferris, W.2
Ramotar, K.3
-
79
-
-
84862501656
-
Results of antibiotic susceptibility testing do not influence clinical outcome in children with cystic fibrosis
-
Hurley MN, Ariff AH, Bertenshaw C, et al. Results of antibiotic susceptibility testing do not influence clinical outcome in children with cystic fibrosis. J Cyst Fibros 2012; 11: 288-292.
-
(2012)
J Cyst Fibros
, vol.11
, pp. 288-292
-
-
Hurley, M.N.1
Ariff, A.H.2
Bertenshaw, C.3
-
80
-
-
84861313371
-
Once-daily versus multiple-daily dosing with intravenous aminoglycosides for cystic fibrosis
-
Smyth AR, Bhatt J. Once-daily versus multiple-daily dosing with intravenous aminoglycosides for cystic fibrosis. Cochrane Database Syst Rev 2012; 2: CD002009.
-
(2012)
Cochrane Database Syst Rev
, vol.2
-
-
Smyth, A.R.1
Bhatt, J.2
-
81
-
-
77953805526
-
Duration of intravenous antibiotic treatment for respiratory exacerbations in children with cystic fibrosis
-
Brown SM, Balfour-Lynn IM. Duration of intravenous antibiotic treatment for respiratory exacerbations in children with cystic fibrosis. Arch Dis Child 2010; 95: 568.
-
(2010)
Arch Dis Child
, vol.95
, pp. 568
-
-
Brown, S.M.1
Balfour-Lynn, I.M.2
-
82
-
-
79952263651
-
Duration of intravenous antibiotic therapy in people with cystic fibrosis
-
Plummer A, Wildman M. Duration of intravenous antibiotic therapy in people with cystic fibrosis. Cochrane Database Syst Rev 2011; 1: CD006682.
-
(2011)
Cochrane Database Syst Rev
, vol.1
-
-
Plummer, A.1
Wildman, M.2
-
83
-
-
84856731944
-
Incidence and risk factors for pulmonary exacerbation treatment failures in cystic fibrosis patients chronically infected with Pseudomonas aeruginosa
-
Parkins MD, Rendall JC, Elborn JS. Incidence and risk factors for pulmonary exacerbation treatment failures in cystic fibrosis patients chronically infected with Pseudomonas aeruginosa. Chest 2012; 141: 485-493.
-
(2012)
Chest
, vol.141
, pp. 485-493
-
-
Parkins, M.D.1
Rendall, J.C.2
Elborn, J.S.3
-
84
-
-
77951249356
-
Neuraminidase inhibitors for the treatment of influenza infection in people with cystic fibrosis
-
Jagannath VA, Asokan GV, Fedorowicz Z, et al. Neuraminidase inhibitors for the treatment of influenza infection in people with cystic fibrosis. Cochrane Database Syst Rev 2010; 3: CD008139.
-
(2010)
Cochrane Database Syst Rev
, vol.3
-
-
Jagannath, V.A.1
Asokan, G.V.2
Fedorowicz, Z.3
-
85
-
-
80355128127
-
Why, when and how to propose noninvasive ventilation in cystic fibrosis?
-
Fauroux B. Why, when and how to propose noninvasive ventilation in cystic fibrosis? Minerva Anestesiol 2011; 77: 1108-1114.
-
(2011)
Minerva Anestesiol
, vol.77
, pp. 1108-1114
-
-
Fauroux, B.1
-
86
-
-
30944452384
-
Mucus clearance and lung function in cystic fibrosis with hypertonic saline
-
Donaldson SH, Bennett WD, Zeman KL, et al. Mucus clearance and lung function in cystic fibrosis with hypertonic saline. N Engl J Med 2006; 354: 241-250.
-
(2006)
N Engl J Med
, vol.354
, pp. 241-250
-
-
Donaldson, S.H.1
Bennett, W.D.2
Zeman, K.L.3
-
87
-
-
77950787429
-
Inhaled mannitol improves the hydration and surface properties of sputum in patients with cystic fibrosis
-
Daviskas E, Anderson SD, Jaques A, et al. Inhaled mannitol improves the hydration and surface properties of sputum in patients with cystic fibrosis. Chest 2010; 137: 861-868.
-
(2010)
Chest
, vol.137
, pp. 861-868
-
-
Daviskas, E.1
Anderson, S.D.2
Jaques, A.3
-
88
-
-
79957957677
-
Nebulized hypertonic saline decreases IL-8 in sputum of patients with cystic fibrosis
-
Reeves EP, Williamson M, O'Neill SJ, et al. Nebulized hypertonic saline decreases IL-8 in sputum of patients with cystic fibrosis. Am J Respir Crit Care Med 2011; 183: 1517-1523.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1517-1523
-
-
Reeves, E.P.1
Williamson, M.2
O'Neill, S.J.3
-
89
-
-
77951988740
-
Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function
-
Amin R, Subbarao P, Jabar A, et al. Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function. Thorax 2010; 65: 379-383.
-
(2010)
Thorax
, vol.65
, pp. 379-383
-
-
Amin, R.1
Subbarao, P.2
Jabar, A.3
-
91
-
-
8944262191
-
Aerosolized recombinant human DNase in hospitalized cystic fibrosis patients with acute pulmonary exacerbations
-
Wilmott RW, Amin RS, Colin AA, et al. Aerosolized recombinant human DNase in hospitalized cystic fibrosis patients with acute pulmonary exacerbations. Am J Respir Crit Care Med 1996; 153: 1914-1917.
-
(1996)
Am J Respir Crit Care Med
, vol.153
, pp. 1914-1917
-
-
Wilmott, R.W.1
Amin, R.S.2
Colin, A.A.3
-
92
-
-
0035010507
-
Bronchoscopically administered recombinant human DNase for lobar atelectasis in cystic fibrosis
-
Slattery DM, Waltz DA, Denham B, et al. Bronchoscopically administered recombinant human DNase for lobar atelectasis in cystic fibrosis. Pediatr Pulmonol 2001; 31: 383-388.
-
(2001)
Pediatr Pulmonol
, vol.31
, pp. 383-388
-
-
Slattery, D.M.1
Waltz, D.A.2
Denham, B.3
-
93
-
-
0032783588
-
Diagnosis, screening and management of cystic fibrosis related diabetes mellitus: A consensus conference report
-
Moran A, Hardin D, Rodman D, et al. Diagnosis, screening and management of cystic fibrosis related diabetes mellitus: a consensus conference report. Diabetes Res Clin Pract 1999; 45: 61-73.
-
(1999)
Diabetes Res Clin Pract
, vol.45
, pp. 61-73
-
-
Moran, A.1
Hardin, D.2
Rodman, D.3
-
94
-
-
0141956255
-
Allergic bronchopulmonary aspergillosis in cystic fibrosis-state of the art: Cystic Fibrosis Foundation Consensus Conference
-
Stevens DA, Moss RB, Kurup VP, et al. Allergic bronchopulmonary aspergillosis in cystic fibrosis-state of the art: Cystic Fibrosis Foundation Consensus Conference. Clin Infect Dis 2003; 37: Suppl. 3, S225-S264.
-
(2003)
Clin Infect Dis
, vol.37
, Issue.SUPPL. 3
-
-
Stevens, D.A.1
Moss, R.B.2
Kurup, V.P.3
-
95
-
-
0031808362
-
Enhanced bioavailability of itraconazole in hydroxypropyl-bcyclodextrin solution versus capsules in healthy volunteers
-
Barone JA, Moskovitz BL, Guarnieri J, et al. Enhanced bioavailability of itraconazole in hydroxypropyl-bcyclodextrin solution versus capsules in healthy volunteers. Antimicrob Agents Chemother 1998; 42: 1862-1865.
-
(1998)
Antimicrob Agents Chemother
, vol.42
, pp. 1862-1865
-
-
Barone, J.A.1
Moskovitz, B.L.2
Guarnieri, J.3
-
96
-
-
79953834427
-
Increased oral bioavailability of itraconazole and its active metabolite, 7-hydroxyitraconazole, when coadministered with a vitamin C beverage in healthy participants
-
Bae SK, Park SJ, Shim EJ, et al. Increased oral bioavailability of itraconazole and its active metabolite, 7-hydroxyitraconazole, when coadministered with a vitamin C beverage in healthy participants. J Clin Pharmacol 2011; 51: 444-451.
-
(2011)
J Clin Pharmacol
, vol.51
, pp. 444-451
-
-
Bae, S.K.1
Park, S.J.2
Shim, E.J.3
-
97
-
-
84878364537
-
Subtherapeutic itraconazole and voriconazole levels in children with cystic fibrosis
-
Bentley S, Gupta A, Balfour-Lynn IM. Subtherapeutic itraconazole and voriconazole levels in children with cystic fibrosis. J Cyst Fibros 2013; 12: 418-419.
-
(2013)
J Cyst Fibros
, vol.12
, pp. 418-419
-
-
Bentley, S.1
Gupta, A.2
Balfour-Lynn, I.M.3
-
98
-
-
29544437697
-
Voriconazole therapy in children with cystic fibrosis
-
Hilliard T, Edwards S, Buchdahl R, et al. Voriconazole therapy in children with cystic fibrosis. J Cyst Fibros 2005; 4: 215-220.
-
(2005)
J Cyst Fibros
, vol.4
, pp. 215-220
-
-
Hilliard, T.1
Edwards, S.2
Buchdahl, R.3
-
99
-
-
65349170114
-
Voriconazole in the treatment of allergic bronchopulmonary aspergillosis in cystic fibrosis
-
Glackin L, Leen G, Elnazir B, et al. Voriconazole in the treatment of allergic bronchopulmonary aspergillosis in cystic fibrosis. Ir Med J 2009; 102: 29.
-
(2009)
Ir Med J
, vol.102
, pp. 29
-
-
Glackin, L.1
Leen, G.2
Elnazir, B.3
-
100
-
-
84860331468
-
High frequency of voriconazole-related phototoxicity in cystic fibrosis patients
-
Rondeau S, Couderc L, Dominique S, et al. High frequency of voriconazole-related phototoxicity in cystic fibrosis patients. Eur Respir J 2012; 39: 782-784.
-
(2012)
Eur Respir J
, vol.39
, pp. 782-784
-
-
Rondeau, S.1
Couderc, L.2
Dominique, S.3
-
101
-
-
83355169572
-
Phototoxicity and photocarcinogenesis associated with voriconazole
-
Epaulard O, Leccia MT, Blanche S, et al. Phototoxicity and photocarcinogenesis associated with voriconazole. Med Mal Infect 2011; 41: 639-645.
-
(2011)
Med Mal Infect
, vol.41
, pp. 639-645
-
-
Epaulard, O.1
Leccia, M.T.2
Blanche, S.3
-
102
-
-
42949155761
-
Nebulised corticosteroid and amphotericin B: An alternative treatment for ABPA?
-
Laoudi Y, Paolini JB, Grimfed A, et al. Nebulised corticosteroid and amphotericin B: an alternative treatment for ABPA? Eur Respir J 2008; 31: 908-909.
-
(2008)
Eur Respir J
, vol.31
, pp. 908-909
-
-
Laoudi, Y.1
Paolini, J.B.2
Grimfed, A.3
-
103
-
-
84860452929
-
Efficacy of nebulised liposomal amphotericin B in the attack and maintenance treatment of ABPA
-
Godet C, Meurice JC, Roblot F, et al. Efficacy of nebulised liposomal amphotericin B in the attack and maintenance treatment of ABPA. Eur Respir J 2012; 39: 1261-1263.
-
(2012)
Eur Respir J
, vol.39
, pp. 1261-1263
-
-
Godet, C.1
Meurice, J.C.2
Roblot, F.3
-
105
-
-
77957195625
-
Controlled trial of cycled antibiotic prophylaxis to prevent initial Pseudomonas aeruginosa infection in children with cystic fibrosis
-
Tramper-Stranders GA, Wolfs TF, van Haren Noman S, et al. Controlled trial of cycled antibiotic prophylaxis to prevent initial Pseudomonas aeruginosa infection in children with cystic fibrosis. Thorax 2010; 65: 915-920.
-
(2010)
Thorax
, vol.65
, pp. 915-920
-
-
Tramper-Stranders, G.A.1
Wolfs, T.F.2
van Haren Noman, S.3
-
106
-
-
77950126962
-
Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis
-
Langton Hewer SC, Smyth AR. Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis. Cochrane Database Syst Rev 2009; 4: CD004197.
-
(2009)
Cochrane Database Syst Rev
, vol.4
-
-
Langton Hewer, S.C.1
Smyth, A.R.2
-
107
-
-
80052511405
-
Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis
-
Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, et al. Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis. Arch Pediatr Adolesc Med 2011; 165: 847-856.
-
(2011)
Arch Pediatr Adolesc Med
, vol.165
, pp. 847-856
-
-
Treggiari, M.M.1
Retsch-Bogart, G.2
Mayer-Hamblett, N.3
-
108
-
-
84855892151
-
Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis
-
Mayer-Hamblett N, Kronmal RA, Gibson RL, et al. Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis. Pediatr Pulmonol 2012; 47: 125-134.
-
(2012)
Pediatr Pulmonol
, vol.47
, pp. 125-134
-
-
Mayer-Hamblett, N.1
Kronmal, R.A.2
Gibson, R.L.3
-
109
-
-
79960204922
-
Infection prevention and control in cystic fibrosis
-
Saiman L. Infection prevention and control in cystic fibrosis. Curr Opin Infect Dis 2011; 24: 390-395.
-
(2011)
Curr Opin Infect Dis
, vol.24
, pp. 390-395
-
-
Saiman, L.1
-
110
-
-
77950112873
-
Vaccines for preventing influenza in people with cystic fibrosis
-
Dharmaraj P, Smyth RL. Vaccines for preventing influenza in people with cystic fibrosis. Cochrane Database Syst Rev 2009; 4: CD001753.
-
(2009)
Cochrane Database Syst Rev
, vol.4
-
-
Dharmaraj, P.1
Smyth, R.L.2
-
111
-
-
77956905085
-
Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening
-
Sermet-Gaudelus I, Mayell SJ, Southern KW, et al. Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening. J Cyst Fibros 2010; 9: 323-329.
-
(2010)
J Cyst Fibros
, vol.9
, pp. 323-329
-
-
Sermet-Gaudelus, I.1
Mayell, S.J.2
Southern, K.W.3
-
112
-
-
0036157901
-
Long-term benefits of inhaled tobramycin in adolescent patients with cystic fibrosis
-
Moss RB. Long-term benefits of inhaled tobramycin in adolescent patients with cystic fibrosis. Chest 2002; 121: 55-63.
-
(2002)
Chest
, vol.121
, pp. 55-63
-
-
Moss, R.B.1
-
113
-
-
0035666058
-
A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities
-
Quan JM, Tiddens HA, Sy JP, et al. A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities. J Pediatr 2001; 139: 813-820.
-
(2001)
J Pediatr
, vol.139
, pp. 813-820
-
-
Quan, J.M.1
Tiddens, H.A.2
Sy, J.P.3
-
114
-
-
44949151079
-
Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis
-
Lands LC, Stanojevic S. Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis. Cochrane Database Syst Rev 2007; 4: CD001505.
-
(2007)
Cochrane Database Syst Rev
, vol.4
-
-
Lands, L.C.1
Stanojevic, S.2
-
116
-
-
77951887288
-
Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: A randomized controlled trial
-
Saiman L, Anstead M, Mayer-Hamblett N, et al. Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial. JAMA 2010; 303: 1707-1715.
-
(2010)
JAMA
, vol.303
, pp. 1707-1715
-
-
Saiman, L.1
Anstead, M.2
Mayer-Hamblett, N.3
-
117
-
-
84861892411
-
Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: The ISIS randomized controlled trial
-
Rosenfeld M, Ratjen F, Brumback L, et al. Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial. JAMA 2012; 307: 2269-2277.
-
(2012)
JAMA
, vol.307
, pp. 2269-2277
-
-
Rosenfeld, M.1
Ratjen, F.2
Brumback, L.3
-
118
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
Ramsey BW, Davies J, McElvaney NG, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011; 365: 1663-1672.
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
-
119
-
-
34249878976
-
A multicenter, randomized, double-blind, placebo-controlled trial to evaluate the metabolic and respiratory effects of growth hormone in children with cystic fibrosis
-
Schnabel D, Grasemann C, Staab D, et al. A multicenter, randomized, double-blind, placebo-controlled trial to evaluate the metabolic and respiratory effects of growth hormone in children with cystic fibrosis. Pediatrics 2007; 119: e1230-e1238.
-
(2007)
Pediatrics
, vol.119
-
-
Schnabel, D.1
Grasemann, C.2
Staab, D.3
-
121
-
-
36248953255
-
Cystic fibrosis pulmonary guidelines: Chronic medications for maintenance of lung health
-
Flume PA, O'Sullivan BP, Robinson KA, et al. Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med 2007; 176: 957-969.
-
(2007)
Am J Respir Crit Care Med
, vol.176
, pp. 957-969
-
-
Flume, P.A.1
O'Sullivan, B.P.2
Robinson, K.A.3
-
122
-
-
34547773123
-
Exacerbations in cystic fibrosis: 2. prevention
-
Bell SC, Robinson PJ. Exacerbations in cystic fibrosis: 2. prevention. Thorax 2007; 62: 723-732.
-
(2007)
Thorax
, vol.62
, pp. 723-732
-
-
Bell, S.C.1
Robinson, P.J.2
-
123
-
-
50849131275
-
Shifting patterns of inhaled antibiotic use in cystic fibrosis
-
Moskowitz SM, Silva SJ, Mayer-Hamblett N, et al. Shifting patterns of inhaled antibiotic use in cystic fibrosis. Pediatr Pulmonol 2008; 43: 874-881.
-
(2008)
Pediatr Pulmonol
, vol.43
, pp. 874-881
-
-
Moskowitz, S.M.1
Silva, S.J.2
Mayer-Hamblett, N.3
|