Mitochondrial function is impaired in yeast and human cellular models of Shwachman Diamond syndrome

Biochemical and Biophysical Research Communications

Volumn 437, Issue 1, 2013, Pages 29-34

  Henson, Adrianna L ^a   Moore, Joseph B ^a   Alard, Pascale ^b   Wattenberg, Max M ^a   Liu, Johnson M ^c   Ellis, Steven R ^a  

^a UNIVERSITY OF LOUISVILLE   (United States)

^b University of Louisville School of Medicine   (United States)

^c Feinstein Institute of Medical Research   (United States)

Author keywords

Bone marrow failure; Mitochondria; Ribosome; Translation

Indexed keywords

ANION CHANNEL; PORIN; PROTEIN; PROTEIN SDO1; REACTIVE OXYGEN METABOLITE; UNCLASSIFIED DRUG; VOLTAGE DEPENDENT ANION CHANNEL 1;

APOPTOSIS; ARTICLE; CARBON SOURCE; CHEMOTAXIS; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOSIS SPINDLE; MYELODYSPLASTIC SYNDROME; NEUTROPENIA; NONHUMAN; OUTER MEMBRANE; OXYGEN CONSUMPTION; PANCREAS INSUFFICIENCY; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN SYNTHESIS; RIBOSOME; SEQUENCE ANALYSIS; SHWACHMAN SYNDROME; YEAST CELL;

BONE MARROW FAILURE; MITOCHONDRIA; RIBOSOME; TRANSLATION;

BONE MARROW DISEASES; CARBON; CELL LINE; EXOCRINE PANCREATIC INSUFFICIENCY; FERMENTATION; GENE KNOCKDOWN TECHNIQUES; HUMANS; LIPOMATOSIS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MITOCHONDRIA; MODELS, BIOLOGICAL; PROTEINS; PROTEOMICS; REACTIVE OXYGEN SPECIES; SACCHAROMYCES CEREVISIAE; SACCHAROMYCES CEREVISIAE PROTEINS;

MAMMALIA;

EID: 84880508268     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2013.06.028     Document Type: Article

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