Fat and carbohydrate metabolism during exercise in phosphoglucomutase type 1 deficiency

Journal of Clinical Endocrinology and Metabolism

Volumn 98, Issue 7, 2013, Pages

  Preisler, Nicolai ^a   Laforêt, Pascal ^b   Echaniz Laguna, Andoni ^c   Ørngreen, Mette C ^a   Lonsdorfer Wolf, Evelyne ^d   Doutreleau, Stephane ^d   Geny, Bernard ^d   Stojkovic, Tanya ^b   Piraud, Monique ^e   Petit, François M ^f   Vissing, John ^a  

^a UNIVERSITY OF COPENHAGEN   (Denmark)

^b ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

^c UNIVERSITY HOSPITAL OF STRASBOURG   (France)

^d UNIVERSITÉ DE STRASBOURG   (France)

^e HOSPICES CIVILS DE LYON   (France)

^f HÔPITAL ANTOINE BÉCLÈRE   (France)

Author keywords

[No Author keywords available]

Indexed keywords

GLUCOSE; LACTIC ACID; PALMITIC ACID; PHOSPHOGLUCOMUTASE;

ADULT; ARTICLE; BICYCLE ERGOMETRY; CALORIMETRY; CARBOHYDRATE METABOLISM; CASE REPORT; CONTROLLED STUDY; ENZYME DEFICIENCY; EXERCISE; EXERCISE TOLERANCE; EXHAUSTION; EXPERIMENTAL STUDY; FATTY ACID METABOLISM; GLUCOSE BLOOD LEVEL; GLUCOSE INFUSION; GLUCOSE OXIDATION; GLYCOLYSIS; HEART RATE; HORMONE RESPONSE; HUMAN; HYPOGLYCEMIA; INTERVENTION STUDY; INTRAVENOUS GLUCOSE TOLERANCE TEST; LACTATE BLOOD LEVEL; LIPID METABOLISM; MALE; OXYGEN CONSUMPTION; PHOSPHOGLUCOMUTASE TYPE 1 DEFICIENCY; PRIORITY JOURNAL; WORK CAPACITY;

ADULT; BICYCLING; CARBOHYDRATE METABOLISM; EXERCISE TEST; EXERCISE TOLERANCE; GLUCOSE; GLYCOGEN STORAGE DISEASE; HEART RATE; HUMANS; HYPOGLYCEMIA; INFUSIONS, INTRAVENOUS; LACTIC ACID; LIPID METABOLISM; MALE; MOTOR ACTIVITY; MUSCLE, SKELETAL; MUSCULAR DISEASES; OXYGEN CONSUMPTION; SEVERITY OF ILLNESS INDEX;

EID: 84879927138     PISSN: 0021972X     EISSN: 19457197     Source Type: Journal    
DOI: 10.1210/jc.2013-1651     Document Type: Article

References (15)

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