Fat and carbohydrate metabolism during exercise in late-onset Pompe disease

Molecular Genetics and Metabolism

Volumn 107, Issue 3, 2012, Pages 462-468

  Preisler, Nicolai ^a   Laforet, Pascal ^b   Madsen, Karen Lindhardt ^a   Hansen, Regitze Sølling ^a   Lukacs, Zoltan ^c   Ørngreen, Mette Cathrine ^a   Lacour, Arnaud ^d   Vissing, John ^a  

^a UNIVERSITY OF COPENHAGEN   (Denmark)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^c UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

^d LILLE UNIVERSITY HOSPITAL   (France)

Author keywords

Exercise; Glycogen; Glycogen storage disease type II; Metabolic myopathy; Skeletal muscle metabolism; Stable isotopes

Indexed keywords

GLUCAN 1,4 ALPHA GLUCOSIDASE; PALMITIC ACID;

ADULT; ARTICLE; CALORIMETRY; CARBOHYDRATE METABOLISM; CLINICAL ARTICLE; CONTROLLED STUDY; ENERGY METABOLISM; EXERCISE TEST; EXERCISE TOLERANCE; FEMALE; GLUCOSE INFUSION; GLYCOGEN STORAGE DISEASE TYPE 2; GLYCOGENOLYSIS; HEART RATE; HUMAN; ISOTOPE ANALYSIS; LIPID METABOLISM; MALE; MUSCLE ATROPHY; MUSCLE WEAKNESS; OXIDATION; PRIORITY JOURNAL; SKELETAL MUSCLE; WORK CAPACITY;

AGE OF ONSET; ALPHA-GLUCOSIDASES; CALORIMETRY, INDIRECT; CASE-CONTROL STUDIES; EXERCISE; FATTY ACIDS; FEMALE; GLUCOSE; GLYCOGEN; GLYCOGEN STORAGE DISEASE TYPE II; GLYCOGENOLYSIS; HUMANS; INFUSIONS, INTRAVENOUS; ISOTOPE LABELING; MALE; MUSCLE WEAKNESS; MUSCLE, SKELETAL; OXYGEN CONSUMPTION; PHYSICAL EXERTION;

EID: 84867902106     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.08.019     Document Type: Article

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