Periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis syndrome is linked to dysregulated monocyte IL-1β production

Journal of Allergy and Clinical Immunology

Volumn 131, Issue 6, 2013, Pages 1635-1643

  Kolly, Laeticia ^a   Busso, Nathalie ^a   Von Scheven Gete, Annette ^a   Bagnoud, Nathaliane ^a   Moix, Isabelle ^c   Holzinger, Dirk ^b   Simon, Gregoire ^a   Ives, Annette ^a   Guarda, Greta ^d   So, Alexander ^a   Morris, Michael A ^c   Hofer, Michaël ^a  

^a LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

^b UNIVERSITY HOSPITAL MÜNSTER   (Germany)

^c GENEVA UNIVERSITY HOSPITALS   (Switzerland)

^d UNIVERSITY OF LAUSANNE   (Switzerland)

Author keywords

aphthous stomatitis; autoinflammatory disease; cervical adenitis syndrome; inflammasome; interleukine 1 ; Periodic fever; pharyngitis; recurrent fever

Indexed keywords

C REACTIVE PROTEIN; CALCIUM BINDING PROTEIN; CALGRANULIN A; CALGRANULIN B; CASPASE 3; CYTOKINE; GAMMA INTERFERON INDUCIBLE PROTEIN 10; INTERLEUKIN 1BETA; INTERLEUKIN 6; MONOCYTE CHEMOTACTIC PROTEIN 1; PREDNISONE; PROTEIN S100A12; SERUM AMYLOID A; STEROID; TUMOR NECROSIS FACTOR ALPHA; UNCLASSIFIED DRUG;

ADULT; AGED; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOKINE PRODUCTION; CYTOKINE RELEASE; DNA DETERMINATION; ERYTHROCYTE SEDIMENTATION RATE; FEMALE; FEVER; GENE; GENE EXPRESSION; GENE FREQUENCY; GENETIC POLYMORPHISM; GENETIC VARIABILITY; GENOTYPE; HUMAN; HUMAN CELL; MALE; MEFV GENE; MONOCYTE; MVK GENE; NEUTROPHIL COUNT; NLRP3 GENE; NUCLEOTIDE SEQUENCE; PATHOGENESIS; PERIPHERAL BLOOD MONONUCLEAR CELL; PFAPA SYNDROME; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; TNFRSF1A GENE; TREATMENT RESPONSE;

ADOLESCENT; ADULT; AGED; CHILD; FEMALE; FEVER; GENETIC VARIATION; HUMANS; INFLAMMATION; INFLAMMATION MEDIATORS; INTERLEUKIN 1 RECEPTOR ANTAGONIST PROTEIN; INTERLEUKIN-1BETA; LEUKOCYTE COUNT; LEUKOCYTES, MONONUCLEAR; LIPOPOLYSACCHARIDES; LYMPHADENITIS; MALE; MIDDLE AGED; MONOCYTES; NEUTROPHILS; PHARYNGITIS; STOMATITIS, APHTHOUS; SYNDROME; YOUNG ADULT;

EID: 84878562491     PISSN: 00916749     EISSN: 10976825     Source Type: Journal    
DOI: 10.1016/j.jaci.2012.07.043     Document Type: Article

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