Massive splenic infarction in an adolescent with hemoglobin S-HPFH

Pediatric Blood and Cancer

Volumn 60, Issue 7, 2013, Pages

  Whyte, Donna ^a   Forget, Bernard ^a   Chui, David H K ^b   Luo, Hong yuan ^b   Pashankar, Farzana ^a  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b BOSTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Children; Sickle cell disease; Splenic infarction

Indexed keywords

AZITHROMYCIN; CEFTRIAXONE;

ABDOMINAL PAIN; ABNORMAL RESPIRATORY SOUND; ADULT; ARTICLE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; COUGHING; DISEASE DURATION; DISEASE EXACERBATION; ECHOGRAPHY; FEVER; FINE NEEDLE ASPIRATION BIOPSY; HEMATOLOGIC DISEASE; HEMOGLOBIN SICKLE HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN; HOSPITAL READMISSION; HUMAN; LENGTH OF STAY; MALE; PRIORITY JOURNAL; REPEAT PROCEDURE; SPLEEN INFARCTION; TACHYCARDIA; TACHYPNEA; THORAX PAIN; THORAX RADIOGRAPHY;

EID: 84878238604     PISSN: 15455009     EISSN: 15455017     Source Type: Journal    
DOI: 10.1002/pbc.24444     Document Type: Article

References (17)

1. Forget BG. Molecular basis of hereditary persistence of fetal hemoglobin. Ann N Y Acad Sci 1998; 850: 38-44.
2. Murray N, Serjeant BE, Serjeant GR. Sickle cell-hereditary persistence of fetal haemoglobin and its differentiation from other sickle cell syndromes. Br J Haematol 1988; 69: 89-92.
3. Charache S, Conley CL. Hereditary persistence of fetal hemoglobin. Ann N Y Acad Sci 1969; 165: 37-41.
4. Conley CL, Weatherall DJ, Richardson SN, et al. Hereditary persistence of fetal hemoglobin: A study of 79 affected persons in 15 negro families in Baltimore. Blood 1963; 21: 261.
5. Ngo DA, Aygun B, Akinsheye I, et al. Fetal haemoglobin levels and haematological characteristics of compound heterozygotes for haemoglobin S and deletional hereditary persistence of fetal haemoglobin. Br J Haematol 2012; 156: 259-264.
6. Konotey-Ahulu FID. Effect of environment on sickle cell disease in West Africa: Epidemiologic and clinical considerations. In: Abramson H, Bertles J, Wethers DL, editors. Sickle cell disease. St. Louis: Mosby; 1973. p 20.
7. Jacob GF, Raper AB. Hereditary persistence of foetal haemoglobin production, and its interaction with the sickle-cell trait. Bri J Haematol 1958; 4: 138-149.
8. Jama AH, Salem AH, Dabbous IA. Massive splenic infarction in Saudi patients with sickle cell anemia: A unique manifestation. Am J Hematol 2002; 69: 205-209.
9. Al-Salem AH. Indications and complications of splenectomy for children with sickle cell disease. J Pediatr Surg 2006; 41: 1909-1915.
10. Berry RA, Odumakinde EA, Lewis JP. Massive splenic infarction in doubly abnormal heterozygous sickling disorders: A new complication of acute splenic sequestration syndrome. West J Med 1991; 155: 531-532.
11. Fishbone G, Nunez D, Jr., Leon R, et al. Massive splenic infarction in sickle cell-hemoglobin C disease angiographic findings. Am J Roentgenol 1977; 129: 927-928.
12. Ouyang DL, Kohrt HE, Garza D, et al. Massive splenic infarct in a collegiate football player with hemoglobin SC disease. Clin J Sports Med 2008; 18: 89-91.
13. Cooley JC, Peterson WL, Engel CE, et al. Clinical triad of massive splenic infarction, sicklemia trait, and high altitude flying. JAMA 1954; 154: 111-113.
14. Conn HO. Sickle-cell trait and splenic infarction associated with high altitude flying. NEJM 1954; 251: 417-420.
15. Shalev O, Boylen AL, Levene C, et al. Sickle cell trait in a white Jewish family presenting as splenic infarction at high altitude. Am J Hematol 1988; 27: 46-48.
16. Gitlin SD, Thompson CB. Non-altitude-related splenic infarction in a patient with sickle cell trait. Am J Med 1989; 87: 697-698.
17. Tso ACY, Roper DR, Wong CL, et al. Splenic infarction in a patient with sickle cell trait and hereditary spherocytosis. Am J Hematol. 2011; 86: 695-696.