Altered regional cardiac wall mechanics are associated with differential cardiomyocyte calcium handling due to nebulette mutations in preclinical inherited dilated cardiomyopathy

Journal of Molecular and Cellular Cardiology

Volumn 60, Issue 1, 2013, Pages 151-160

  Maiellaro Rafferty, K ^a   Wansapura, J P ^a   Mendsaikhan, U ^a   Osinska, H ^a   James, J F ^a   Taylor, M D ^a   Robbins, J ^a   Kranias, E G ^b   Towbin, J A ^a   Purevjav, E ^a  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^b UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

Cardiac magnetic resonance imaging; Connexin43; Desmin; Dilated cardiomyopathy; Nebulette; Sarcomere

Indexed keywords

ALPHA ACTININ; CONNEXIN 43; DESMIN; ISOPRENALINE; NEBULETTE; NEBULIN; TROPONIN I; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CALCIUM HOMEOSTASIS; CALCIUM MOBILIZATION; CARDIOVASCULAR MAGNETIC RESONANCE; CELL ISOLATION; CELL SEPARATION; CELL ULTRASTRUCTURE; CONGESTIVE CARDIOMYOPATHY; CONTROLLED STUDY; DISEASE ASSOCIATION; EX VIVO STUDY; GENE; GENE EXPRESSION REGULATION; GENE MUTATION; HEART MUSCLE CELL; HEART MUSCLE CONTRACTILITY; HEART STRESS; HEART VENTRICLE WALL MOTION; IN VIVO STUDY; MALE; MOLECULAR DYNAMICS; MOUSE; NEBL GENE; NONHUMAN; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; SARCOMERE;

ACTININ; ANIMALS; CALCIUM SIGNALING; CARDIOMEGALY; CYTOSKELETAL PROTEINS; HEART DEFECTS, CONGENITAL; LIM DOMAIN PROTEINS; MICE; MICE, TRANSGENIC; MUTATION; MYOCARDIAL CONTRACTION; MYOCARDIUM; MYOCYTES, CARDIAC; SARCOMERES;

ANIMALIA; MUS; MUS MUSCULUS;

EID: 84877817517     PISSN: 00222828     EISSN: 10958584     Source Type: Journal    
DOI: 10.1016/j.yjmcc.2013.04.021     Document Type: Article

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