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Volumn 98, Issue 5, 2013, Pages 667-674

Principles of care for the diagnosis and treatment of von Willebrand disease

Author keywords

[No Author keywords available]

Indexed keywords

ALLOANTIBODY; AMINOCAPROIC ACID; BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR 8 CONCENTRATE; BLOOD CLOTTING FACTOR 8 PLUS VON WILLEBRAND FACTOR; DESMOPRESSIN; EMOSINT; ESTROGEN; FACTOR 8Y; FANHDI; GESTAGEN; GRIFOLS; HEPATITIS A VACCINE; HEPATITIS B VACCINE; IRON; LEVONORGESTREL; LOW MOLECULAR WEIGHT HEPARIN; ORAL CONTRACEPTIVE AGENT; RECOMBINANT BLOOD CLOTTING FACTOR 8; RISTOCETIN; THROMBOCYTE CONCENTRATE; TRANEXAMIC ACID; UNCLASSIFIED DRUG; VON WILLEBRAND FACTOR; WILFACTIN;

EID: 84877026971     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2012.077263     Document Type: Review
Times cited : (170)

References (61)
  • 1
    • 0023164845 scopus 로고
    • Epidemiological investigation of the prevalence of von Willebrand's disease
    • Rodeghiero F, Castaman G, Dini E. Epidemiological investigation of the prevalence of von Willebrand's disease. Blood. 1987;69(2):454-9.
    • (1987) Blood , vol.69 , Issue.2 , pp. 454-459
    • Rodeghiero, F.1    Castaman, G.2    Dini, E.3
  • 2
    • 0032823229 scopus 로고    scopus 로고
    • Inconsistency of association between type 1 von Willebrand disease phenotype and genotype in families identified in an epidemiological investigation
    • Castaman G, Eikenboom JCJ, Bertina RM, Rodeghiero F. Inconsistency of association between type 1 von Willebrand disease phenotype and genotype in families identified in an epidemiological investigation. Thromb Haemost. 1999;82(3):1065-70.
    • (1999) Thromb Haemost , vol.82 , Issue.3 , pp. 1065-1070
    • Castaman, G.1    Eikenboom, J.C.J.2    Bertina, R.M.3    Rodeghiero, F.4
  • 3
    • 67149132162 scopus 로고    scopus 로고
    • Von Willebrand factor to the rescue
    • De Meyer SF, Deckmyn H, Vanhoorelbeke K. von Willebrand factor to the rescue. Blood. 2009;113(21):5049-57.
    • (2009) Blood , vol.113 , Issue.21 , pp. 5049-5057
    • de Meyer, S.F.1    Deckmyn, H.2    Vanhoorelbeke, K.3
  • 4
    • 3943048700 scopus 로고    scopus 로고
    • Treatment of von Willebrand's Disease
    • Mannucci PM. Treatment of von Willebrand's Disease. N Engl J Med. 2004; 351(7):683-94.
    • (2004) N Engl J Med , vol.351 , Issue.7 , pp. 683-694
    • Mannucci, P.M.1
  • 5
    • 2342625955 scopus 로고    scopus 로고
    • Management of von Willebrand disease: A guideline from the UK Haemophilia Centre Doctors' Organization
    • Pasi KJ, Collins PW, Keeling DM, Brown SA, Cumming AM, Dolan GC, et al. Management of von Willebrand disease: a guideline from the UK Haemophilia Centre Doctors' Organization. Haemophilia. 2004; 10(3):218-31.
    • (2004) Haemophilia , vol.10 , Issue.3 , pp. 218-231
    • Pasi, K.J.1    Collins, P.W.2    Keeling, D.M.3    Brown, S.A.4    Cumming, A.M.5    Dolan, G.C.6
  • 6
    • 33748802581 scopus 로고    scopus 로고
    • Update on the pathophysiology and classification of von Willebrand disease: A report of the Subcommittee on von Willebrand Factor
    • Sadler JE, Budde U, Eikenboom JC, Favaloro EJ, Hill FG, Holmberg L, et al. Update on the pathophysiology and classification of von Willebrand disease: a report of the Subcommittee on von Willebrand Factor. J Thromb Haemost. 2006;4(10):2103-14.
    • (2006) J Thromb Haemost , vol.4 , Issue.10 , pp. 2103-2114
    • Sadler, J.E.1    Budde, U.2    Eikenboom, J.C.3    Favaloro, E.J.4    Hill, F.G.5    Holmberg, L.6
  • 7
    • 83055187115 scopus 로고    scopus 로고
    • Von Willebrand disease (VWD): Evidencebased diagnosis and management guidelines, the National Heart, Lung, and Blood Institute (NHLBI) Expert Panel report (USA)
    • Nichols WL, Hultin MB, James AH, Manco- Johnson MJ, Montgomery RR, Ortel TL, et al. von Willebrand disease (VWD): evidencebased diagnosis and management guidelines, the National Heart, Lung, and Blood Institute (NHLBI) Expert Panel report (USA). Haemophilia. 2008;14(2):171-232.
    • (2008) Haemophilia , vol.14 , Issue.2 , pp. 171-232
    • Nichols, W.L.1    Hultin, M.B.2    James, A.H.3    Manco-Johnson, M.J.4    Montgomery, R.R.5    Ortel, T.L.6
  • 8
    • 66849141406 scopus 로고    scopus 로고
    • How I treat von Willebrand disease
    • Rodeghiero F, Castaman G, Tosetto A. How I treat von Willebrand disease. Blood. 2009; 114(6):1158-65.
    • (2009) Blood , vol.114 , Issue.6 , pp. 1158-1165
    • Rodeghiero, F.1    Castaman, G.2    Tosetto, A.3
  • 9
    • 66349136610 scopus 로고    scopus 로고
    • Evidence-based recommendations on the treatment of von Willebrand disease in Italy
    • Mannucci PM, Franchini M, Castaman G, Federici AB. Evidence-based recommendations on the treatment of von Willebrand disease in Italy. Blood Transf. 2009:7(2):117-26.
    • (2009) Blood Transf , vol.7 , Issue.2 , pp. 117-126
    • Mannucci, P.M.1    Franchini, M.2    Castaman, G.3    Federici, A.B.4
  • 11
    • 0019206797 scopus 로고
    • Application of indicators, predictors and diagnostic indices in coagulation disorders. I. Evaluation of a self-administered questionnaire with binary questions
    • Wahlberg T, Blomback M, Hall P, Axelsson G. Application of indicators, predictors and diagnostic indices in coagulation disorders. I. Evaluation of a self-administered questionnaire with binary questions. Methods Infect Med. 1980;19(4):194-200.
    • (1980) Methods Infect Med , vol.19 , Issue.4 , pp. 194-200
    • Wahlberg, T.1    Blomback, M.2    Hall, P.3    Axelsson, G.4
  • 13
    • 29244439008 scopus 로고    scopus 로고
    • The discriminant power of bleeding history for the diagnosis of type 1 von Willebrand disease: An international, multicenter study
    • Rodeghiero F, Castaman G, Tosetto A, Batlle J, Baudo F, Cappelletti A, et al. The discriminant power of bleeding history for the diagnosis of type 1 von Willebrand disease: an international, multicenter study. J Thromb Haemost. 2005;3(12):2619-26.
    • (2005) J Thromb Haemost , vol.3 , Issue.12 , pp. 2619-2626
    • Rodeghiero, F.1    Castaman, G.2    Tosetto, A.3    Batlle, J.4    Baudo, F.5    Cappelletti, A.6
  • 14
    • 43249098361 scopus 로고    scopus 로고
    • Evidence-based diagnosis of type 1 von Willebrand disease: A Bayes theorem approach
    • Tosetto A, Castaman G, Rodeghiero F. Evidence-based diagnosis of type 1 von Willebrand disease: a Bayes theorem approach. Blood. 2008;111(8):3998-4003.
    • (2008) Blood , vol.111 , Issue.8 , pp. 3998-4003
    • Tosetto, A.1    Castaman, G.2    Rodeghiero, F.3
  • 15
    • 43149083497 scopus 로고    scopus 로고
    • Bleeding scores in inherited bleeding disorders: Clinical or research tools?
    • Tosetto A, Rodeghiero F, Castaman G. Bleeding scores in inherited bleeding disorders: clinical or research tools? Haemophilia. 2008;14(3):415-22.
    • (2008) Haemophilia , vol.14 , Issue.3 , pp. 415-422
    • Tosetto, A.1    Rodeghiero, F.2    Castaman, G.3
  • 16
    • 77956493323 scopus 로고    scopus 로고
    • ISTH/SSC bleeding assessment tool: A standardized questionnaire and a proposal for a new bleeding score for inherited bleeding disorders
    • Rodeghiero F, Tosetto A, Abshire T, Arnold DM, Coller B, James P, et al. ISTH/SSC bleeding assessment tool: a standardized questionnaire and a proposal for a new bleeding score for inherited bleeding disorders. J Thromb Haemost. 2010;8(9):2063-5.
    • (2010) J Thromb Haemost , vol.8 , Issue.9 , pp. 2063-2065
    • Rodeghiero, F.1    Tosetto, A.2    Abshire, T.3    Arnold, D.M.4    Coller, B.5    James, P.6
  • 17
    • 33644977050 scopus 로고    scopus 로고
    • A quantitative analysis of bleeding symptoms in type 1 von Willebrand disease: Results from a multicenter European study (MCMDM-1 VWD)
    • Tosetto A, Rodeghiero F, Castaman G, Goodeve A, Federici AB, Budde U, et al. A quantitative analysis of bleeding symptoms in type 1 von Willebrand disease: results from a multicenter European study (MCMDM-1 VWD). J Thromb Haemost. 2006;4(4):766-73.
    • (2006) J Thromb Haemost , vol.4 , Issue.4 , pp. 766-773
    • Tosetto, A.1    Rodeghiero, F.2    Castaman, G.3    Goodeve, A.4    Federici, A.B.5    Budde, U.6
  • 18
    • 33845967766 scopus 로고    scopus 로고
    • Phenotype and genotype of a cohort of families historically diagnosed with type 1 von Willebrand disease in the European study, Molecular and Clinical Markers for the Diagnosis and Management of Type 1 von Willebrand Disease (MCMDM-1VWD)
    • Goodeve A, Eikenboom J, Castaman G, Rodeghiero F, Federici AB, Batlle J, et al. Phenotype and genotype of a cohort of families historically diagnosed with type 1 von Willebrand disease in the European study, Molecular and Clinical Markers for the Diagnosis and Management of Type 1 von Willebrand Disease (MCMDM-1VWD). Blood. 2007;109(1):112-21.
    • (2007) Blood , vol.109 , Issue.1 , pp. 112-121
    • Goodeve, A.1    Eikenboom, J.2    Castaman, G.3    Rodeghiero, F.4    Federici, A.B.5    Batlle, J.6
  • 19
    • 77953800564 scopus 로고    scopus 로고
    • Quantitation of bleeding symptoms in children with von Willebrand disease: Use of a standardized pediatric bleeding questionnaire
    • Biss TT, Blanchette VS, Clark SD, Bowman M, Wakefield CD, Silva M, et al. Quantitation of bleeding symptoms in children with von Willebrand disease: use of a standardized pediatric bleeding questionnaire. J Thromb Haemost. 2010;8(6):950-6.
    • (2010) J Thromb Haemost , vol.8 , Issue.6 , pp. 950-956
    • Biss, T.T.1    Blanchette, V.S.2    Clark, S.D.3    Bowman, M.4    Wakefield, C.D.5    Silva, M.6
  • 20
    • 79955396907 scopus 로고    scopus 로고
    • Bleeding tendency and efficacy of anti-haemorrhagic treatments in patients with type 1 von Willebrand disease and increased von Willebrand factor clearance
    • Castaman G, Tosetto A, Federici AB, Rodeghiero F. Bleeding tendency and efficacy of anti-haemorrhagic treatments in patients with type 1 von Willebrand disease and increased von Willebrand factor clearance. Thromb Haemost. 2011;105(4):647-54.
    • (2011) Thromb Haemost , vol.105 , Issue.4 , pp. 647-654
    • Castaman, G.1    Tosetto, A.2    Federici, A.B.3    Rodeghiero, F.4
  • 21
    • 84859169124 scopus 로고    scopus 로고
    • Different bleeding risk in type 2 A and 2 M Von Willebrand disease: A two-year prospective study in 107 patients
    • Castaman G, Federici AB, Tosetto A, La Marca S, Stufano F, Mannucci PM, et al. Different bleeding risk in type 2 A and 2 M Von Willebrand disease: a two-year prospective study in 107 patients. J Thromb Haemost. 2012;10(4):632-8.
    • (2012) J Thromb Haemost , vol.10 , Issue.4 , pp. 632-638
    • Castaman, G.1    Federici, A.B.2    Tosetto, A.3    la Marca, S.4    Stufano, F.5    Mannucci, P.M.6
  • 22
    • 0026011654 scopus 로고
    • Human von Willebrand factor gene and pseudogene: Structural analysis and differentiation by polymerase chain reaction
    • Mancuso DJ, Tuley EA, Westfield LA et al. Human von Willebrand factor gene and pseudogene: structural analysis and differentiation by polymerase chain reaction. Biochemistry 1991;30(1):253-69.
    • (1991) Biochemistry , vol.30 , Issue.1 , pp. 253-269
    • Mancuso, D.J.1    Tuley, E.A.2    Westfield, L.A.3
  • 23
    • 77952581903 scopus 로고    scopus 로고
    • The genetic basis of von Willebrand disease
    • Goodeve A. The genetic basis of von Willebrand disease. Blood Rev. 2010;24(3): 123-34.
    • (2010) Blood Rev , vol.24 , Issue.3 , pp. 123-134
    • Goodeve, A.1
  • 24
    • 51249102362 scopus 로고    scopus 로고
    • The molecular analysis of von Willebrand disease: A guideline from the UK Haemophilia Centre Doctors' Organisation Haemophilia Genetics Laboratory Network
    • Keeney S, Bowen D, Cumming A, Enayat S, Goodeve A, Hill F. The molecular analysis of von Willebrand disease: a guideline from the UK Haemophilia Centre Doctors' Organisation Haemophilia Genetics Laboratory Network. Haemophilia. 2008; 14(4):1099-11.
    • (2008) Haemophilia , vol.14 , Issue.4 , pp. 1099-1111
    • Keeney, S.1    Bowen, D.2    Cumming, A.3    Enayat, S.4    Goodeve, A.5    Hill, F.6
  • 25
    • 84877020937 scopus 로고    scopus 로고
    • Laboratory diagnosis of von Willebrand disease: The phenotype
    • Federici AB, Lee CA, Berntorp EE, Lillicrap D, Montgomery RR, Oxford, UK; Wiley-Blackwell
    • Budde U, Favaloro EJ. Laboratory diagnosis of von Willebrand disease: the phenotype. In Federici AB, Lee CA, Berntorp EE, Lillicrap D, Montgomery RR (eds). Von Willebrand disease. Oxford, UK; Wiley-Blackwell, 2011, 100-13.
    • (2011) Von Willebrand Disease , pp. 100-113
    • Budde, U.1    Favaloro, E.J.2
  • 26
    • 0024420764 scopus 로고
    • Consistency of responses to repeated DDAVP infusions in patients with von Willebrand's disease and hemophilia A
    • Rodeghiero F, Castaman G, Di Bona E, Ruggeri M. Consistency of responses to repeated DDAVP infusions in patients with von Willebrand's disease and hemophilia A. Blood. 1989;74(6):1997-2000.
    • (1989) Blood , vol.74 , Issue.6 , pp. 1997-2000
    • Rodeghiero, F.1    Castaman, G.2    Di Bona, E.3    Ruggeri, M.4
  • 27
    • 12144289138 scopus 로고    scopus 로고
    • Biologic response to desmopressin in patients with severe type 1 and type 2 von Willebrand disease: Results of a multicenter European study
    • Federici AB, Mazurier C, Berntorp E, Lee CA, Scharrer I, Goudemand J, et al. Biologic response to desmopressin in patients with severe type 1 and type 2 von Willebrand disease: results of a multicenter European study. Blood. 2004 (6);103: 2032-8.
    • (2004) Blood , vol.103 , Issue.6 , pp. 2032-2038
    • Federici, A.B.1    Mazurier, C.2    Berntorp, E.3    Lee, C.A.4    Scharrer, I.5    Goudemand, J.6
  • 28
    • 43549097149 scopus 로고    scopus 로고
    • Response to desmopressin is influenced by the genotype and phenotype in type 1 von Willebrand disease (VWD): Results from the European Study MCMDM-1VWD
    • Castaman G, Lethagen S, Federici AB, Tosetto A, Goodeve A, Budde U, et al. Response to desmopressin is influenced by the genotype and phenotype in type 1 von Willebrand disease (VWD): results from the European Study MCMDM-1VWD. Blood. 2008(7);111: 3531-9.
    • (2008) Blood , vol.111 , Issue.7 , pp. 3531-3539
    • Castaman, G.1    Lethagen, S.2    Federici, A.B.3    Tosetto, A.4    Goodeve, A.5    Budde, U.6
  • 29
    • 67849111584 scopus 로고    scopus 로고
    • Reduced von Willebrand factor survival in von Willebrand disease: Pathophysiologic and clinical relevance
    • Castaman G, Tosetto A, Rodeghiero F. Reduced von Willebrand factor survival in von Willebrand disease: pathophysiologic and clinical relevance. J Thomb Haemost. 2009;7:(Suppl 1):71-4.
    • (2009) J Thomb Haemost , vol.7 , Issue.SUPPL. 1 , pp. 71-74
    • Castaman, G.1    Tosetto, A.2    Rodeghiero, F.3
  • 30
    • 0029967568 scopus 로고    scopus 로고
    • Desmopressin and type II B von Willebrand disease
    • Castaman G, Rodeghiero F. Desmopressin and type II B von Willebrand disease. Hemophilia. 1996;2(2):73-6.
    • (1996) Hemophilia , vol.2 , Issue.2 , pp. 73-76
    • Castaman, G.1    Rodeghiero, F.2
  • 31
    • 60249092963 scopus 로고    scopus 로고
    • Clinical and molecular predictors of thrombocytopenia and risk of bleeding in patients with von Willebrand disease type 2B: A cohort study of 67 patients
    • Federici AB, Mannucci PM, Castaman G, Baronciani L, Bucciarelli P, Canciani MT, et al. Clinical and molecular predictors of thrombocytopenia and risk of bleeding in patients with von Willebrand disease type 2B: a cohort study of 67 patients. Blood. 2009;113(5):526-34.
    • (2009) Blood , vol.113 , Issue.5 , pp. 526-534
    • Federici, A.B.1    Mannucci, P.M.2    Castaman, G.3    Baronciani, L.4    Bucciarelli, P.5    Canciani, M.T.6
  • 32
    • 0026713114 scopus 로고
    • Patterns of development of tachyphylaxis in patients with haemophilia and von Willebrand disease after repeated doses of desmopressin (DDAVP)
    • Mannucci PM, Bettega D, Cattaneo M. Patterns of development of tachyphylaxis in patients with haemophilia and von Willebrand disease after repeated doses of desmopressin (DDAVP). Br J Haematol. 1992;82(1):87-93.
    • (1992) Br J Haematol , vol.82 , Issue.1 , pp. 87-93
    • Mannucci, P.M.1    Bettega, D.2    Cattaneo, M.3
  • 33
    • 0024410234 scopus 로고
    • Hyponatremia and seizures in young children given DDAVP
    • Smith TJ, Gill JC, Ambruso DR, Hathaway WE. Hyponatremia and seizures in young children given DDAVP. Am J Hematol. 1989; 31(3):199-202.
    • (1989) Am J Hematol , vol.31 , Issue.3 , pp. 199-202
    • Smith, T.J.1    Gill, J.C.2    Ambruso, D.R.3    Hathaway, W.E.4
  • 34
    • 0023835090 scopus 로고
    • Myocardial infarction in a patient with hemophilia treated with DDAVP
    • Bond L, Bevan D. Myocardial infarction in a patient with hemophilia treated with DDAVP. N Eng J Med. 1988;318(2):121.
    • (1988) N Eng J Med , vol.318 , Issue.2 , pp. 121
    • Bond, L.1    Bevan, D.2
  • 35
    • 0023875934 scopus 로고
    • Thrombosis following desmopressin for uremic bleeding
    • Byrnes JJ, Larcada A, Moake JL. Thrombosis following desmopressin for uremic bleeding. Am J Hematol. 1988;28(1):63-5.
    • (1988) Am J Hematol , vol.28 , Issue.1 , pp. 63-65
    • Byrnes, J.J.1    Larcada, A.2    Moake, J.L.3
  • 36
    • 17044373272 scopus 로고    scopus 로고
    • Use of desmopressin (DDAVP) during early pregnancy in factor VIII-deficient women
    • Mannucci PM. Use of desmopressin (DDAVP) during early pregnancy in factor VIII-deficient women. Blood. 2005; 105(8):3382.
    • (2005) Blood , vol.105 , Issue.8 , pp. 3382
    • Mannucci, P.M.1
  • 37
    • 77953210923 scopus 로고    scopus 로고
    • Pregnancy and delivery in women with von Willebrand's disease and different von Willebrand factor mutations
    • Castaman G, Tosetto A, Rodeghiero F. Pregnancy and delivery in women with von Willebrand's disease and different von Willebrand factor mutations. Haematologica. 2010; 95(6) 963-9.
    • (2010) Haematologica , vol.95 , Issue.6 , pp. 963-969
    • Castaman, G.1    Tosetto, A.2    Rodeghiero, F.3
  • 38
    • 0141955859 scopus 로고    scopus 로고
    • Immunization of patients with bleeding disorders
    • Makris M, Conlon CP, Watson HG. Immunization of patients with bleeding disorders. Haemophilia. 2003;9(5):541-6.
    • (2003) Haemophilia , vol.9 , Issue.5 , pp. 541-546
    • Makris, M.1    Conlon, C.P.2    Watson, H.G.3
  • 40
    • 66949168185 scopus 로고    scopus 로고
    • The safety of plasma-derived von Willebrand/factor VIII concentrates in the management of inherited von Willebrand disease
    • Federici AB. The safety of plasma-derived von Willebrand/factor VIII concentrates in the management of inherited von Willebrand disease. Expert Opin Drug Saf. 2009(2); 8: 203-10.
    • (2009) Expert Opin Drug Saf , vol.8 , Issue.2 , pp. 203-210
    • Federici, A.B.1
  • 41
    • 84877028333 scopus 로고    scopus 로고
    • The use of plasma- derived concentrates
    • Federici AB, Lee CA, Berntorp EE, Lillicrap D, Mongomery RR., Oxford, UK; Wiley-Blackwell
    • Mannucci PM, Franchini M. The use of plasma- derived concentrates. In: Federici AB, Lee CA, Berntorp EE, Lillicrap D, Mongomery RR. Von Willebrand disease. Oxford, UK; Wiley-Blackwell, 2011:200-6.
    • (2011) Von Willebrand Disease , pp. 200-206
    • Mannucci, P.M.1    Franchini, M.2
  • 42
    • 79959792971 scopus 로고    scopus 로고
    • Treatment of von Willebrand disease with FVIII/VWF concentrates
    • Castaman G. Treatment of von Willebrand disease with FVIII/VWF concentrates. Blood Transf. 2011;9(Suppl 2):s9-s13.
    • (2011) Blood Transf , vol.9 , Issue.SUPPL. 2
    • Castaman, G.1
  • 43
    • 28444472737 scopus 로고    scopus 로고
    • Pharmacokinetic studies on Wilfactin, a von Willebrand factor concentrate with a low factor VIII content treated with three virusinactivation/ removal methods
    • Goudemand J, Scharrer I, Berntorp E, Lee CA, Borel-Derlon A, Stieltjes N, et al. Pharmacokinetic studies on Wilfactin, a von Willebrand factor concentrate with a low factor VIII content treated with three virusinactivation/ removal methods. J Thromb Haemost. 2005;3(10):2219-27.
    • (2005) J Thromb Haemost , vol.3 , Issue.10 , pp. 2219-2227
    • Goudemand, J.1    Scharrer, I.2    Berntorp, E.3    Lee, C.A.4    Borel-Derlon, A.5    Stieltjes, N.6
  • 44
    • 34250169072 scopus 로고    scopus 로고
    • Treatment of severe von Willebrand disease with a high-purity von Willebrand factor concentrate (Wilfactin): A prospective study of 50 patients
    • Borel-Derlon A, Federici AB, Roussel-Robert V, Goudemand J, Lee CA, Scharrer I, et al. Treatment of severe von Willebrand disease with a high-purity von Willebrand factor concentrate (Wilfactin): a prospective study of 50 patients. J Thromb Haemost. 2007; 5(6):1115-24.
    • (2007) J Thromb Haemost , vol.5 , Issue.6 , pp. 1115-1124
    • Borel-Derlon, A.1    Federici, A.B.2    Roussel-Robert, V.3    Goudemand, J.4    Lee, C.A.5    Scharrer, I.6
  • 45
    • 0036713595 scopus 로고    scopus 로고
    • Venous thrombosis following the use of intermediate purity FVIII concentrate to treat patients with von Willebrand's disease
    • Makris M, Colvin B, Gupta V, Shields ML, Smith MP. Venous thrombosis following the use of intermediate purity FVIII concentrate to treat patients with von Willebrand's disease. Thromb Haemost. 2002;88(3):387-8.
    • (2002) Thromb Haemost , vol.88 , Issue.3 , pp. 387-388
    • Makris, M.1    Colvin, B.2    Gupta, V.3    Shields, M.L.4    Smith, M.P.5
  • 46
    • 0036712293 scopus 로고    scopus 로고
    • Venous thromboembolism in von Willebrand disease
    • Mannucci PM. Venous thromboembolism in von Willebrand disease. Thromb Haemost. 2002;88(3):378-9.
    • (2002) Thromb Haemost , vol.88 , Issue.3 , pp. 378-379
    • Mannucci, P.M.1
  • 47
    • 19944364505 scopus 로고    scopus 로고
    • Long-term prophylaxis in von Willebrand disease
    • Berntorp E, Petrini P. Long-term prophylaxis in von Willebrand disease. Blood Coag Fibrinol. 2005;16(Suppl 1):S23-6.
    • (2005) Blood Coag Fibrinol , vol.16 , Issue.SUPPL. 1
    • Berntorp, E.1    Petrini, P.2
  • 48
    • 37149005797 scopus 로고    scopus 로고
    • Highly purified VWF/FVIII concentrates in the treatment and prophylaxis of von Willebrand disease. The PRO.WILL study
    • Federici AB. Highly purified VWF/FVIII concentrates in the treatment and prophylaxis of von Willebrand disease. The PRO.WILL study. Haemophilia. 2007;13(Suppl 5):15-24.
    • (2007) Haemophilia , vol.13 , Issue.SUPPL. 5 , pp. 15-24
    • Federici, A.B.1
  • 49
    • 84870998006 scopus 로고    scopus 로고
    • Prophylaxis in severe forms of von Willebrand's disease: Results from the von Willebrand disease prophylaxis network (VWD PN)
    • Abshire TC, Federici AB, Alvarez MT, Bowen J, Carcao MD, Cox Gill J, et al. Prophylaxis in severe forms of von Willebrand's disease: results from the von Willebrand disease prophylaxis network (VWD PN). Haemophilia. 2013;19(1):76-81.
    • (2013) Haemophilia , vol.19 , Issue.1 , pp. 76-81
    • Abshire, T.C.1    Federici, A.B.2    Alvarez, M.T.3    Bowen, J.4    Carcao, M.D.5    Cox Gill, J.6
  • 50
    • 0023469711 scopus 로고
    • Lifethreatening reaction to factor VIII concentrate in a patient with severe von Willebrand disease and alloantibodies to von Willebrand factor
    • Mannucci PM, Tamaro G, Narchi G, Candotti G, Federici A, Altieri D, et al. Lifethreatening reaction to factor VIII concentrate in a patient with severe von Willebrand disease and alloantibodies to von Willebrand factor. Eur J Hematol. 1987;39(5):467-70.
    • (1987) Eur J Hematol , vol.39 , Issue.5 , pp. 467-470
    • Mannucci, P.M.1    Tamaro, G.2    Narchi, G.3    Candotti, G.4    Federici, A.5    Altieri, D.6
  • 51
    • 79955643645 scopus 로고    scopus 로고
    • Common large partial VWF gene deletion does not cause alloantibody formation in the Hungarian type 3 von Willebrand disease population
    • Mohl A, Boda Z, Jager R, Losonczy H, Marosi A, Masszi T, et al. Common large partial VWF gene deletion does not cause alloantibody formation in the Hungarian type 3 von Willebrand disease population. J Thromb Haemost. 2011;9(5):945-52.
    • (2011) J Thromb Haemost , vol.9 , Issue.5 , pp. 945-952
    • Mohl, A.1    Boda, Z.2    Jager, R.3    Losonczy, H.4    Marosi, A.5    Masszi, T.6
  • 52
    • 0029872095 scopus 로고    scopus 로고
    • Use of recombinant factor VIIa (NovoSeven) in the treatment of two patients with type III von Willebrand's disease and an inhibitor against von Willebrand factor
    • Ciavarella N, Schiavoni M, Valenzano E, Mangini F, Inchingolo F. Use of recombinant factor VIIa (NovoSeven) in the treatment of two patients with type III von Willebrand's disease and an inhibitor against von Willebrand factor. Haemostasis. 1996;26 (Suppl 1):10-4.
    • (1996) Haemostasis , vol.26 , Issue.SUPPL. 1 , pp. 10-14
    • Ciavarella, N.1    Schiavoni, M.2    Valenzano, E.3    Mangini, F.4    Inchingolo, F.5
  • 53
    • 43149111831 scopus 로고    scopus 로고
    • Treatment for patients with type 3 von Willebrand disease and alloantibodies: A case report
    • Franchini M, Gandini G, Giuffrida A, De Gironcoli M, Federici AB. Treatment for patients with type 3 von Willebrand disease and alloantibodies: a case report. Haemophilia. 2008;14(3):645-6.
    • (2008) Haemophilia , vol.14 , Issue.3 , pp. 645-646
    • Franchini, M.1    Gandini, G.2    Giuffrida, A.3    de Gironcoli, M.4    Federici, A.B.5
  • 54
    • 0025878651 scopus 로고
    • Hemostatic effect of normal platelet transfusion in severe von Willebrand disease patients
    • Castillo R, Monteagudo J, Escolar G, Ordinas A, Magallón M, Martín Villar J. Hemostatic effect of normal platelet transfusion in severe von Willebrand disease patients. Blood. 1991;77(9):1901-5.
    • (1991) Blood , vol.77 , Issue.9 , pp. 1901-1905
    • Castillo, R.1    Monteagudo, J.2    Escolar, G.3    Ordinas, A.4    Magallón, M.5    Martín Villar, J.6
  • 55
    • 0032560732 scopus 로고    scopus 로고
    • Hemostatic drugs
    • Mannucci PM. Hemostatic drugs. N Eng J Med. 1998;339(4):245-53.
    • (1998) N Eng J Med , vol.339 , Issue.4 , pp. 245-253
    • Mannucci, P.M.1
  • 58
    • 10844220754 scopus 로고    scopus 로고
    • The use of levonorgestrel-releasing intrauterine system for treatment of menorrhagia in women with inherited bleeding disorders
    • Kingman CE, Kadir RA, Lee CA, Economides DL. The use of levonorgestrel-releasing intrauterine system for treatment of menorrhagia in women with inherited bleeding disorders. Br J Obstet Gynaecol. 2004;111(12): 1425-8.
    • (2004) Br J Obstet Gynaecol , vol.111 , Issue.12 , pp. 1425-1428
    • Kingman, C.E.1    Kadir, R.A.2    Lee, C.A.3    Economides, D.L.4
  • 59
    • 0032515596 scopus 로고    scopus 로고
    • Frequency of inherited bleeding disorders in women with menorrhagia
    • Kadir RA, Economides DL, Sabin CA, Owens D, Lee CA. Frequency of inherited bleeding disorders in women with menorrhagia. Lancet. 1998,351(9101):485-9.
    • (1998) Lancet , vol.351 , Issue.9101 , pp. 485-489
    • Kadir, R.A.1    Economides, D.L.2    Sabin, C.A.3    Owens, D.4    Lee, C.A.5
  • 60
    • 0023610642 scopus 로고
    • Von Willebrand's disease presenting as thrombocytopenia during pregnancy
    • Giles AR, Hoogendoorn H, Benford K. Type IIB von Willebrand's disease presenting as thrombocytopenia during pregnancy. Br J Haematol. 1987;67(3):349-53.
    • (1987) Br J Haematol , vol.67 , Issue.3 , pp. 349-353
    • Giles, A.R.1    Hoogendoorn, H.2    Benford, K.3    Type, I.I.B.4
  • 61
    • 34249929900 scopus 로고    scopus 로고
    • Evaluation of the clinical safety of desmopressin during pregnancy in women with a low plasmatic von Willebrand factor level and bleeding history
    • Sánchez-Luceros A, Meschengieser SS, Turdó K, Arizó A, Woods AI, Casais P, et al. Evaluation of the clinical safety of desmopressin during pregnancy in women with a low plasmatic von Willebrand factor level and bleeding history. Thromb Res. 2007; 120(3):387-90.
    • (2007) Thromb Res , vol.120 , Issue.3 , pp. 387-390
    • Sánchez-Luceros, A.1    Meschengieser, S.S.2    Turdó, K.3    Arizó, A.4    Woods, A.I.5    Casais, P.6


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