Altered innate function of plasmacytoid dendritic cells restored by enzyme replacement therapy in Gaucher disease

Blood Cells, Molecules, and Diseases

Volumn 50, Issue 4, 2013, Pages 281-288

  Braudeau, Cécile ^a,b   Graveleau, Julie ^a   Rimbert, Marie ^a,b   Néel, Antoine ^a   Hamidou, Mohamed ^a,c   Grosbois, Bernard ^d   Besançon, Audrey ^a   Giraudet, Stéphanie ^a   Terrien, Caroline ^a   Josien, Régis ^a,b,c   Masseau, Agathe ^a  

^a NANTES UNIVERSITY HOSPITAL   (France)

^b Centre National de la Recherche Scientifique   (France)

^c UNIVERSITÉ DE NANTES   (France)

^d RENNES UNIVERSITY HOSPITAL   (France)

Author keywords

Dendritic cells; Gaucher disease; Memory T cells; Toll like receptor

Indexed keywords

CD4 ANTIGEN; CD45RO ANTIGEN; CYTOKINE; GAMMA INTERFERON; GLUCOSYLCERAMIDASE; GLUCOSYLCERAMIDE; GRANULOCYTE COLONY STIMULATING FACTOR; GRANULOCYTE MACROPHAGE COLONY STIMULATING FACTOR; IMIGLUCERASE; INTERLEUKIN 10; INTERLEUKIN 12; INTERLEUKIN 13; INTERLEUKIN 17; INTERLEUKIN 18; INTERLEUKIN 1BETA; INTERLEUKIN 2; INTERLEUKIN 3; INTERLEUKIN 4; INTERLEUKIN 5; INTERLEUKIN 6; INTERLEUKIN 7; INTERLEUKIN 8; MACROPHAGE INFLAMMATORY PROTEIN 1BETA; MONOCYTE CHEMOTACTIC PROTEIN 1; TALIGLUCERASE ALFA; TOLL LIKE RECEPTOR; TOLL LIKE RECEPTOR 9; TUMOR NECROSIS FACTOR ALPHA; UNINDEXED DRUG; VELAGLUCERASE ALFA;

ADULT; ARTICLE; B LYMPHOCYTE; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOKINE PRODUCTION; ENZYME REPLACEMENT; FEMALE; FLOW CYTOMETRY; GAUCHER DISEASE; HUMAN; HUMAN CELL; IMMUNOCOMPETENT CELL; INNATE IMMUNITY; MACROPHAGE; MALE; MONOCYTE; NATURAL KILLER CELL; PATHOLOGY; PLASMACYTOID DENDRITIC CELL; PRIORITY JOURNAL; T LYMPHOCYTE;

ADOLESCENT; ADULT; CHILD; CYTOKINES; DENDRITIC CELLS; ENZYME REPLACEMENT THERAPY; FEMALE; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; HUMANS; IMMUNITY, INNATE; IMMUNOLOGIC MEMORY; INFLAMMATION MEDIATORS; KILLER CELLS, NATURAL; LYMPHOCYTE COUNT; MALE; MIDDLE AGED; RECEPTORS, ANTIGEN, T-CELL, GAMMA-DELTA; T-LYMPHOCYTES; YOUNG ADULT;

EID: 84875534621     PISSN: 10799796     EISSN: 10960961     Source Type: Journal    
DOI: 10.1016/j.bcmd.2013.01.001     Document Type: Article

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