Glycoform-Selective Prion Formation in Sporadic and Familial Forms of Prion Disease

PLoS ONE

Volumn 8, Issue 3, 2013, Pages

  Xiao, Xiangzhu ^a   Yuan, Jue ^a   Haïk, Stéphane ^b   Cali, Ignazio ^a   Zhan, Yian ^a,g   Moudjou, Mohammed ^c   Li, Baiya ^a   Laplanche, Jean Louis ^d   Laude, Hubert ^c   Langeveld, Jan ^e   Gambetti, Pierluigi ^a   Kitamoto, Tetsuyuki ^f   Kong, Qingzhong ^a   Brandel, Jean Philippe ^b   Cobb, Brian A ^a   Petersen, Robert B ^a   Zou, Wen Quan ^a,g,h  

^a CASE WESTERN RESERVE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b SORBONNE UNIVERSITÉ   (France)

^c INRA Institut National de la Recherche Agronomique   (France)

^d HÔPITAL LARIBOISIÈRE   (France)

^e WAGENINGEN UNIVERSITY   (Netherlands)

^f TOHOKU UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^g NANCHANG UNIVERSITY   (China)

^h CHINESE CENTER FOR DISEASE CONTROL AND PREVENTION   (China)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCAN; PRION PROTEIN; PROTEINASE K; VALINE;

ARTICLE; BIOCHEMICAL COMPOSITION; CELL LYSATE; CELL SURFACE; CLINICAL ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; FAMILIAL CREUTZFELDT JAKOB DISEASE; HUMAN; HUMAN CELL; HUMAN TISSUE; MOLECULAR DYNAMICS; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN LOCALIZATION; SIGNAL TRANSDUCTION; SPORADIC CREUTZFELDT JAKOB DISEASE;

BRAIN; CELL LINE; CELL MEMBRANE; CREUTZFELDT-JAKOB SYNDROME; ENDOPEPTIDASE K; ENDOPLASMIC RETICULUM; GLYCOSYLATION; HUMANS; POLYSACCHARIDES; PRION DISEASES; PRIONS; PROTEOLYSIS; VALINE;

EID: 84875088471     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0058786     Document Type: Article

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