Unfolded Protein Response and Activated Degradative Pathways Regulation in GNE Myopathy

PLoS ONE

Volumn 8, Issue 3, 2013, Pages

  Li, Honghao ^a,b   Chen, Qi ^c   Liu, Fuchen ^a   Zhang, Xuemei ^d   Li, Wei ^a   Liu, Shuping ^a   Zhao, Yuying ^a   Gong, Yaoqin ^e   Yan, Chuanzhu ^a,e  

^a SHANDONG UNIVERSITY   (China)

^b SHANDONG PROVINCIAL HOSPITAL AFFILIATED TO SHANDONG UNIVERSITY   (China)

^c YANTAI YUHUANGDING HOSPITAL   (China)

^d Key Laboratory of Cardiovascular Proteomics of Shandong Province   (China)

^e SHANDONG UNIVERSITY   (China)

Author keywords

[No Author keywords available]

Indexed keywords

AMYLOID PRECURSOR PROTEIN; CALNEXIN; CALRETICULIN; GLUCOSE REGULATED PROTEIN 78; GLUCOSE REGULATED PROTEIN 94; PROTEASOME; TAU PROTEIN; UBIQUITIN; URIDINE DIPHOSPHATE N ACETYLGLUCOSAMINE 2 EPIMERASE; VALOSIN CONTAINING PROTEIN; ADENOSINE TRIPHOSPHATASE; CDC48 PROTEIN; CELL CYCLE PROTEIN; CHAPERONE; ENDOPLASMIN; HEAT SHOCK PROTEIN; MEMBRANE PROTEIN; MOLECULAR CHAPERONE GRP78; MULTIENZYME COMPLEX; UDP-N-ACETYLGLUCOSAMINE 2-EPIMERASE - N-ACETYLMANNOSAMINE KINASE;

ARTICLE; AUTOPHAGY; CLINICAL ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM ASSOCIATED DEGRADATION; ENDOPLASMIC RETICULUM STRESS; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOFLUORESCENCE; MORPHOLOGY; MUSCLE; MYOPATHY; PATHOGENESIS; PROTEIN AGGREGATION; PROTEIN CLEAVAGE; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN PHOSPHORYLATION; QUANTITATIVE ANALYSIS; REAL TIME POLYMERASE CHAIN REACTION; SIGNAL TRANSDUCTION; UBIQUITIB PROTEASOME SYSTEM; UBIQUITINATION; UNFOLDED PROTEIN RESPONSE; UPREGULATION; URIDINE DIPHOSPHATE N ACETYLGLUCOSAMINE 2 EPIMERASE MYOPATHY; ADULT; BIOPSY; CASE CONTROL STUDY; ENDOPLASMIC RETICULUM; ENZYMOLOGY; FEMALE; GENE EXPRESSION REGULATION; MALE; METABOLISM; MUSCLE DISEASE; PATHOLOGY; PHOSPHORYLATION; YOUNG ADULT;

ADENOSINE TRIPHOSPHATASES; ADULT; AMYLOID BETA-PROTEIN PRECURSOR; BIOPSY; CALNEXIN; CALRETICULIN; CASE-CONTROL STUDIES; CELL CYCLE PROTEINS; ENDOPLASMIC RETICULUM; FEMALE; GENE EXPRESSION REGULATION, ENZYMOLOGIC; HEAT-SHOCK PROTEINS; HUMANS; MALE; MEMBRANE GLYCOPROTEINS; MOLECULAR CHAPERONES; MULTIENZYME COMPLEXES; MUSCLES; MUSCULAR DISEASES; PHOSPHORYLATION; PROTEASOME ENDOPEPTIDASE COMPLEX; UNFOLDED PROTEIN RESPONSE; YOUNG ADULT; ANIMALS; CELL LINE; DROSOPHILA; GAUCHER DISEASE; GLUCOSYLCERAMIDASE;

EID: 84874612520     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0058116     Document Type: Article

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