Placental stem cell correction of murine intermediate maple syrup urine disease

Hepatology

Volumn 57, Issue 3, 2013, Pages 1017-1023

  Skvorak, Kristen J ^a   Dorko, Kenneth ^a   Marongiu, Fabio ^a   Tahan, Veysel ^a   Hansel, Marc C ^a   Gramignoli, Roberto ^b   Gibson, K Michael ^c   Strom, Stephen C ^b  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b KAROLINSKA INSTITUTE   (Sweden)

^c MICHIGAN TECHNOLOGICAL UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

2 OXOISOVALERATE DEHYDROGENASE (LIPOAMIDE); ALLOISOLEUCINE; ISOLEUCINE; LEUCINE; VALINE;

AMNION CELL; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BODY WEIGHT; CELL SURVIVAL; CONTROLLED STUDY; DISEASE MODEL; ENGRAFTMENT; ENZYME ACTIVITY; HUMAN; HUMAN TISSUE; MAPLE SYRUP URINE DISEASE; MOUSE; NONHUMAN; PLACENTAL STEM CELL CORRECTION; PRIORITY JOURNAL; STEM CELL TRANSPLANTATION;

3-METHYL-2-OXOBUTANOATE DEHYDROGENASE (LIPOAMIDE); AMINO ACIDS, BRANCHED-CHAIN; AMNION; ANIMALS; ANIMALS, NEWBORN; BODY WEIGHT; BRAIN; CELL DIFFERENTIATION; DISEASE MODELS, ANIMAL; EPITHELIAL CELLS; FEMALE; HEPATOCYTES; HUMANS; MAPLE SYRUP URINE DISEASE; MICE; MICE, MUTANT STRAINS; PLACENTA; PREGNANCY; STEM CELL TRANSPLANTATION; TRANSPLANTATION, HETEROLOGOUS;

EID: 84874481902     PISSN: 02709139     EISSN: 15273350     Source Type: Journal    
DOI: 10.1002/hep.26150     Document Type: Article

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