Congenital heart disease and heterotaxy: Upper gastrointestinal fluoroscopy can be misleading and surgery in an asymptomatic patient is not beneficial

Journal of Pediatric Surgery

Volumn 48, Issue 1, 2013, Pages 164-169

  Papillon, Stephanie ^a   Goodhue, Catherine J ^a   Zmora, Osnat ^a   Sharma, Shalini S ^b   Wells, Winfield J ^a   Ford, Henri R ^a   Upperman, Jeffrey S ^a   Wang, Kasper S ^a   Bushman, Gerald A ^a   Kim, Richard ^a   Pierce, James R ^a  

^a CHILDREN S HOSPITAL LOS ANGELES   (United States)

^b UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

Author keywords

Asplenia; Heterotaxy; Isomerism; Ladd's procedure; Malrotation; Polysplenia

Indexed keywords

ACCESSORY SPLEEN; ARTICLE; ASPLENIA; CONGENITAL HEART DISEASE; DUODENOJEJUNAL MALPOSITION; FEMALE; FLUOROSCOPY; HETEROTAXY SYNDROME; HUMAN; INTESTINE OBSTRUCTION; INTESTINE VOLVULUS; MAJOR CLINICAL STUDY; MALE; MEDICAL RECORD REVIEW; PRIORITY JOURNAL; SCREENING; SMALL INTESTINE DISEASE; UPPER GASTROINTESTINAL FLUOROSCOPY;

ASYMPTOMATIC DISEASES; FEMALE; FLUOROSCOPY; FOLLOW-UP STUDIES; HETEROTAXY SYNDROME; HUMANS; INFANT, NEWBORN; INTESTINAL OBSTRUCTION; INTESTINAL VOLVULUS; LOGISTIC MODELS; MALE; MULTIVARIATE ANALYSIS; POSTOPERATIVE COMPLICATIONS; REOPERATION; RETROSPECTIVE STUDIES; RISK ASSESSMENT; TREATMENT OUTCOME;

EID: 84872370117     PISSN: 00223468     EISSN: 15315037     Source Type: Journal    
DOI: 10.1016/j.jpedsurg.2012.10.033     Document Type: Article

References (17)

1. D.W. Polhemus, and W.B. Schafer Congenital absence of the spleen; syndrome with atrioventricularis and situs inversus; case reports and review of the literature Pediatrics 9 1952 696 708
2. B.I. Ivemark Implications of agenesis of the spleen on the pathogenesis of conotruncus anomalies in childhood; an analysis of the heart malformations in the splenic agenesis syndrome, with fourteen new cases Acta Paediatr Suppl 44 1995 7 110
3. K. Maclean, and S. Dunwoodie Breaking symmetry: a clinical overview of left-right patterning Clin Genet 65 2004 441 457
4. J.P. Jacobs, R.H. Anderson, and P.M. Weinberg The nomenclature, definition and classification of cardiac structures in the setting of heterotaxy Cardiol Young 17 Suppl. 2 2007 1 28
5. V. Rose, T. Izukawa, and C. Moes Syndromes of asplenia and polysplenia: a review of cardiac and non-cardiac malformations in 60 cases with special reference to diagnosis and prognosis Br Heart J 37 1975 840 852
6. I.A. Yurlov, V.P. Podzolkov, and M.M. Zelenikin Experience with bidirectional cavopulmonary anastomosis and modified Fontan operation in patients with single ventricle and concomitant visceral heterotaxy Interact Cardiovasc Thorac Surg 12 2011 563 568
7. Swisher M, Jonas R, Tian X, et al.: Increased postoperative and respiratory complications in patients with congenital heart disease associated with heterotaxy. J Thorac Cardiovasc Surg 2011;141:637-644, 644.e631-633.
8. T.W. Prendiville, L.L. Barton, and W.R. Thompson Heterotaxy syndrome: defining contemporary disease trends Pediatr Cardiol 31 2010 1052 1058
9. K. Green, F.F. Buchvald, and J.K. Marthin Ventilation inhomogeneity in children with primary ciliary dyskinesia Thorax 67 2012 49 53
10. D.C. Yu, R.R. Thiagarajan, and P.C. Laussen Outcomes after the Ladd procedure in patients with heterotaxy syndrome, congenital heart disease, and intestinal malrotation J Pediatr Surg 44 2009 1089 1095 [discussion 1095]
11. D.B. Tashjian, B. Weeks, and M. Brueckner Outcomes after a Ladd procedure for intestinal malrotation with heterotaxia J Pediatr Surg 42 2007 528 531
12. B. Ferdman, L. States, and J.W. Gaynor Abnormalities of intestinal rotation in patients with congenital heart disease and the heterotaxy syndrome Congenit Heart Dis 2 2007 12 18
13. S.H. Borenstein, and J.C. Langer Heterotaxia syndromes and their abdominal manifestations Curr Opin Pediatr 18 2006 294 297
14. D.C. Little, and S.D. Smith Malrotation G.W. Holcomb, J.P. Murphy, Ashcraft's pediatric surgery 2010 PA, Saunders Philadelphia 416 424
15. M. Choi, S.H. Borenstein, and L. Hornberger Heterotaxia syndrome: the role of screening for intestinal rotation abnormalities Arch Dis Child 90 2005 813 815
16. J.R. Mehall, J.C. Chandler, and R.L. Mehall Management of typical and atypical intestinal malrotation J Pediatr Surg 37 2002 1169 1172
17. M.R. McVay, E.R. Kokoska, and R.J. Jackson Jack Barney Award. The changing spectrum of intestinal malrotation: diagnosis and management Am J Surg 194 2007 712 717 [discussion 718-719]