Heterotaxy syndrome: Defining contemporary disease trends

Pediatric Cardiology

Volumn 31, Issue 7, 2010, Pages 1052-1058

  Prendiville, Terence W ^a   Barton, Leslie L ^b   Thompson, William R ^a   Fink, Doran L ^a   Holmes, Kathryn W ^a  

^a JOHNS HOPKINS HOSPITAL   (United States)

^b UNIVERSITY OF ARIZONA COLLEGE OF MEDICINE   (United States)

Author keywords

Asplenia; Inferior vena cava; Malrotation; Polysplenia

Indexed keywords

AMOXICILLIN; ANTIBIOTIC AGENT; PENICILLIN G; PNEUMOCOCCUS VACCINE;

ACCESSORY SPLEEN; ANATOMY; ANTIBIOTIC PROPHYLAXIS; ARTICLE; ASPLENIA; CHILD; CLINICAL ARTICLE; ECHOCARDIOGRAPHY; FEMALE; FOLLOW UP; HETEROTAXY SYNDROME; HOSPITAL INFECTION; HUMAN; INCIDENCE; INFECTION RISK; INFERIOR CAVA VEIN; INTESTINE MALROTATION; MALE; MORTALITY; NONHUMAN; PNEUMOCOCCAL INFECTION; SEPSIS;

ABNORMALITIES, MULTIPLE; ADOLESCENT; CHILD; DEXTROCARDIA; FEMALE; GENETIC DISEASES, X-LINKED; HEART DEFECTS, CONGENITAL; HUMANS; MALE; RETROSPECTIVE STUDIES; RISK FACTORS; SEPSIS; SITUS INVERSUS; SPLEEN; SPLENIC DISEASES;

EID: 77957603760     PISSN: 01720643     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00246-010-9764-z     Document Type: Article

References (39)

1. R Abou Elella HK Najm H Balkhy L Bullard MS Kabbani 2010 Impact of bloodstream infection on the outcome of children undergoing cardiac surgery Pediatr Cardiol 31 483 489 10.1007/s00246-009-9624-x 20063161
2. PV Anagnostopoulos JM Pearl C Octave M Cohen A Gruessner E Wintering, et al. 2009 Improved current era outcomes in patients with heterotaxy syndromes Eur J Cardiothorac Surg 35 871 877 10.1016/j.ejcts.2008.12.018 19233677
3. A Azakie SL Merklinger WG Williams GS Van Arsdell JG Coles I Adatia 2001 Improving outcomes of the Fontan operation in children with atrial isomerism and heterotaxy syndromes Ann Thorac Surg 72 1636 16640 1:STN:280: DC%2BD3Mnns1arsQ%3D%3D 10.1016/S0003-4975(01)03039-9 11722057 (Pubitemid 33049776)
4. GM Barker SM O'Brien KF Welke ML Jacobs DK Benjamin Jr ED Peterson, et al. 2010 Major infection after pediatric cardiac surgery: a risk estimation model Ann Thorac Surg 89 843 850 10.1016/j.athoracsur.2009.11.048 20172141
5. PJ Bartz DJ Driscoll JA Dearani FJ Puga GK Danielson PW O'Leary, et al. 2006 Early and late results of the modified Fontan operation for heterotaxy syndrome: 30 years of experience in 142 patients J Am Coll Cardiol 48 2301 2305 10.1016/j.jacc.2006.07.053 17161263 (Pubitemid 44855420)
6. WD Biggar RA Ramirez V Rose 1981 Congenital asplenia: immunologic assessment and a clinical review of eight surviving patients Pediatrics 67 548 551 1:STN:280:DyaL3M3ks1GltA%3D%3D 7254976
7. RC Bone RA Balk FB Cerra RP Dellinger AM Fein WA Knaus, et al. 1992 Definitions for sepsis and organ failure and guidelines for the use of innovative therapies in sepsis. The ACCP/SCCM Consensus Conference Committee. American College of Chest Physicians/Society of Critical Care Medicine Chest 101 1644 1655 1:STN:280:DyaK383ovFeiuw%3D%3D 10.1378/chest.101.6.1644 1303622
8. DW Bratzler PM Houck 2005 Antimicrobial prophylaxis for surgery: an advisory statement from the National Surgical Infection Prevention Project Am J Surg 189 395 404 10.1016/j.amjsurg.2005.01.015 15820449 (Pubitemid 40488232)
9. A Brendolan MM Rosado R Carsetti L Selleri TN Dear 2007 Development and function of the mammalian spleen Bioessays 29 166 177 1:CAS:528: DC%2BD2sXitVCmsLg%3D 10.1002/bies.20528 17226804 (Pubitemid 46340251)
10. M Brueckner 2007 Heterotaxia, congenital heart disease, and primary ciliary dyskinesia Circulation 115 2793 2795 10.1161/CIRCULATIONAHA.107.699256 17548739 (Pubitemid 46869664)
11. YF Cheung VY Cheng AK Chau CS Chiu TC Yung MP Leung 2002 Outcome of infants with right atrial isomerism: is prognosis better with normal pulmonary venous drainage? Heart 87 146 152 1:STN:280:DC%2BD38%2FntVGisA%3D%3D 10.1136/heart.87.2.146 11796553
12. PJ Collignon 1994 Intravascular catheter associated sepsis: a common problem. The Australian study in intravascular catheter associated sepsis Med J Aust 161 374 378 1:STN:280:DyaK2czns1KltQ%3D%3D 8090116
13. MR Ditchfield JM Hutson 1998 Intestinal rotational abnormalities in polysplenia and asplenia syndromes Pediatr Radiol 28 303 306 1:STN:280:DyaK1c3jslOrsw%3D%3D 10.1007/s002470050358 9569265 (Pubitemid 28221132)
14. MP Dyke RP Martin PJ Berry 1991 Septicaemia and adrenal haemorrhage in congenital asplenia Arch Dis Child 66 636 637 1:STN:280:DyaK3M3kslymsw%3D%3D 10.1136/adc.66.5.636 2039257
15. MH Gaston JI Verter G Woods C Pegelow J Kelleher G Presbury, et al. 1986 Prophylaxis with oral penicillin in children with sickle cell anemia: a randomized trial N Engl J Med 314 1593 1599 1:STN:280:DyaL283jtVOhsA%3D%3D 10.1056/NEJM198606193142501 3086721
16. G Grisaru-Soen G Paret D Yahav V Boyko L Lerner-Geva 2009 Nosocomial infections in pediatric cardiovascular surgery patients: a 4-year survey Pediatr Crit Care Med 10 202 206 10.1097/PCC.0b013e31819a37c5 19188871
17. SS Huang VL Hinrichsen AE Stevenson SL Rifas-Shiman K Kleinman SI Pelton, et al. 2009 Continued impact of pneumococcal conjugate vaccine on carriage in young children Pediatrics 124 e1 e11 10.1542/peds.2008-3099 19564254
18. Jacobs JP, Anderson RH, Weinberg PM, Walters HL 3rd, Tchervenkov CI, Del Duca D, et al (2007) The nomenclature, definition and classification of cardiac structures in the setting of heterotaxy. Cardiol Young 17(Suppl)2:1-28
19. SJ Kim WH Kim HG Lim CH Lee JY Lee 2006 Improving results of the Fontan procedure in patients with heterotaxy syndrome Ann Thorac Surg 82 1245 1251 10.1016/j.athoracsur.2006.04.082 16996916 (Pubitemid 44425299)
20. KO Maher K VanDerElzen EL Bove RS Mosca CE Chenoweth TJ Kulik 2002 A retrospective review of three antibiotic prophylaxis regimens for pediatric cardiac surgical patients Ann Thorac Surg 74 1195 1200 10.1016/S0003-4975(02) 03893-6 12400768 (Pubitemid 35176746)
21. DC Melles S de Marie 2004 Prevention of infections in hyposplenic and asplenic patients: an update Neth J Med 62 45 52 1:STN:280: DC%2BD2c3ivVyjsg%3D%3D 15127830
22. B Mikoluc H Kayhty E Bernatowska R Motowski 2008 Immune response to the 7-valent pneumococcal conjugate vaccine in 30 asplenic children Eur J Clin Microbiol Infect Dis 27 923 928 1:CAS:528:DC%2BD1cXht1amsr%2FK 10.1007/s10096-008-0523-5 18584224
23. BH Nagel H Williams L Stewart J Paul O Stumper 2005 Splenic state in surviving patients with visceral heterotaxy Cardiol Young 15 469 473 10.1017/S1047951105211320 16164783 (Pubitemid 41630833)
24. Overturf GD (2000) American Academy of Pediatrics. Committee on Infectious Diseases. Technical report: prevention of pneumococcal infections, including the use of pneumococcal conjugate and polysaccharide vaccines and antibiotic prophylaxis. Pediatrics 106:367-376
25. Pickering LK, Baker CJ, Kimberlin DW, Long SS (2009) Red Book: 2009 Report of the Committee on Infectious Diseases, 28th ed. p 84
26. VE Price VS Blanchette EL Ford-Jones 2007 The prevention and management of infections in children with asplenia or hyposplenia Infect Dis Clin North Am 21 697 710 10.1016/j.idc.2007.07.002 17826619 (Pubitemid 47371197)
27. V Rose T Izukawa CA Moes 1975 Syndromes of asplenia and polysplenia. A review of cardiac and non-cardiac malformations in 60 cases with special reference to diagnosis and prognosis Br Heart J 37 840 852 1:STN:280: DyaE28%2FmtFykug%3D%3D 10.1136/hrt.37.8.840 1191445
28. M Ruscazio S Van Praagh AR Marrass G Catani S Iliceto R Van Praagh 1998 Interrupted inferior vena cava in asplenia syndrome and a review of the hereditary patterns of visceral situs abnormalities Am J Cardiol 81 111 1116 1:STN:280:DyaK1c7it1CmtA%3D%3D 10.1016/S0002-9149(97)00811-4 9462624 (Pubitemid 28046860)
29. GE Schutze EO Mason Jr WJ Barson KS Kim ER Wald LB Givner, et al. 2002 Invasive pneumococcal infections in children with asplenia Pediatr Infect Dis J 21 278 282 10.1097/00006454-200204000-00004 12075756 (Pubitemid 34326863)
30. DB Singer 1973 Postsplenectomy sepsis Perspect Paediatr Pathol 1 285 311 1:STN:280:DyaE2c7ltVWntA%3D%3D
31. F Smets A Bourgois C Vermylen B Brichard P Slacmuylders S Leyman, et al. 2007 Randomized revaccination with pneumococcal polysaccharide or conjugate vaccine in asplenic children previously vaccinated with polysaccharide vaccine Vaccine 25 5278 5282 1:CAS:528:DC%2BD2sXntF2rt7s%3D 10.1016/j.vaccine.2007.05. 014 17576024 (Pubitemid 46977540)
32. C Sox 2003 Health supervision for children with sickle cell disease Pediatrics 111 710 711 10.1542/peds.111.3.710 12612266 (Pubitemid 36330742)
33. D Spelman J Buttery A Daley D Isaacs I Jennens A Kakakios, et al. 2008 Guidelines for the prevention of sepsis in asplenic and hyposplenic patients Intern Med J 38 349 356 1:CAS:528:DC%2BD1cXmt1ensro%3D 10.1111/j.1445-5994.2007. 01579.x 18284463 (Pubitemid 351519485)
34. C Stamm I Friehs LF Duebener D Zurakowski JE Mayer Jr RA Jonas, et al. 2002 Improving results of the modified Fontan operation in patients with heterotaxy syndrome Ann Thorac Surg 74 1967 1977 10.1016/S0003-4975(02)04124-3 12643382 (Pubitemid 35440864)
35. DB Tashjian B Weeks M Brueckner RJ Touloukian 2007 Outcomes after a Ladd procedure for intestinal malrotation with heterotaxia J Pediatr Surg 42 528 531 10.1016/j.jpedsurg.2006.10.060 17336193
36. BS Ticho AM Goldstein R Van Praagh 2000 Extracardiac anomalies in the heterotaxy syndromes with focus on anomalies of midline-associated structures Am J Cardiol 85 729 734 1:STN:280:DC%2BD383lvFKjtQ%3D%3D 10.1016/S0002-9149(99) 00849-8 12000048 (Pubitemid 30133394)
37. JL Vincent DJ Bihari PM Suter HA Bruining J White MH Nicolas-Chanoin, et al. 1995 The prevalence of nosocomial infection in intensive care units in Europe. Results of the European prevalence of infection in intensive care (EPIC) study. EPIC international advisory committee JAMA 274 639 644 1:STN:280:DyaK2MzmsVWnuw%3D%3D 10.1001/jama.274.8.639 7637145
38. JD Waldman A Rosenthal AL Smith S Shurin AS Nadas 1977 Sepsis and congenital asplenia J Pediatr 90 555 559 1:STN:280:DyaE2s7itVKksA%3D%3D 10.1016/S0022-3476(77)80365-X 320299
39. MH Wu JK Wang HC Lue 2002 Sudden death in patients with right atrial isomerism (asplenism) after palliation J Pediatr 140 93 96 10.1067/mpd.2002. 120510 11815770 (Pubitemid 34117473)