Aggressive fatal case of autoimmune hemorrhaphilia resulting from anti-Factor XIII antibodies

Blood Coagulation and Fibrinolysis

Volumn 24, Issue 1, 2013, Pages 85-89

  Sugiyama, Hiroyuki ^a   Uesugi, Hiroko ^a   Suzuki, Satoshi ^a   Tanaka, Kenji ^a   Souri, Masayoshi ^b   Ichinose, Akitada ^b  

^a Saiseikai Noe Hospital   (Japan)

^b YAMAGATA UNIVERSITY   (Japan)

Author keywords

autoantibody; autoimmune disease; factor XIII deficiency; fatal bleeding disorder; point of care test

Indexed keywords

BLOOD CLOTTING FACTOR 13; BLOOD CLOTTING FACTOR 13 ANTIBODY; CEFTRIAXONE; FRESH FROZEN PLASMA; HEMOGLOBIN; PREDNISOLONE; PROTEIN ANTIBODY; UNCLASSIFIED DRUG;

ABDOMINAL WALL MUSCULATURE; AGED; ARTICLE; AUTOIMMUNE DISEASE; AUTOIMMUNE HEMORRHAPHILIA BLOOD CLOTTING FACTOR 13; BLEEDING DISORDER; CASE REPORT; CONTINUOUS HEMODIAFILTRATION; DEATH; EPISTAXIS; FEMALE; GINGIVA BLEEDING; HEMATOMA; HUMAN; HUMAN TISSUE; PLASMAPHERESIS; PRIORITY JOURNAL;

AGED; ANTI-BACTERIAL AGENTS; AUTOANTIBODIES; AUTOIMMUNE DISEASES; CEFTRIAXONE; DELAYED DIAGNOSIS; DISEASE PROGRESSION; EPISTAXIS; FACTOR XIII; FACTOR XIII DEFICIENCY; FATAL OUTCOME; FEMALE; GINGIVAL HEMORRHAGE; HEMATOMA; HEMODIAFILTRATION; HEMOPERITONEUM; HEMORRHAGIC DISORDERS; HUMANS; NEUROSYPHILIS; PARTIAL THROMBOPLASTIN TIME; PLASMA EXCHANGE;

EID: 84871807326     PISSN: 09575235     EISSN: 14735733     Source Type: Journal    
DOI: 10.1097/MBC.0b013e328358e8e7     Document Type: Article

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