Mesenchymal stem cells from Shwachman-Diamond syndrome patients display normal functions and do not contribute to hematological defects

Blood Cancer Journal

Volumn 2, Issue 10, 2012, Pages

  Andre V ^a   Longoni, D ^b   Bresolin, S ^c   Cappuzzello, C ^a   Dander, E ^a   Galbiati, M ^a   Bugarin, C ^a   Meglio, A D ^c   Nicolis, E ^d   Maserati, E ^e   Serafini, M ^f   Warren, A J ^g   Te Kronnie, G ^c   Cazzaniga, G ^a   Sainati, L ^c   Cipolli, M ^d   Biondi, A ^b   D'Amico, G ^a  

^a UNIVERSITY OF MILANO BICOCCA   (Italy)

^b SAN GERARDO HOSPITAL   (Italy)

^c UNIVERSITY OF PADOVA   (Italy)

^d UNIVERSITY HOSPITAL OF VERONA   (Italy)

^e UNIVERSITY OF INSUBRIA   (Italy)

^f DULBECCO TELETHON INSTITUTE   (Italy)

^g MRC LABORATORY OF MOLECULAR BIOLOGY   (United Kingdom)

Author keywords

bone marrow failure; mesenchymal stem cells; SBDS; Shwachman Diamond syndrome

Indexed keywords

CD34 ANTIGEN; CELL SURFACE MARKER; INTERLEUKIN 6;

ACUTE GRANULOCYTIC LEUKEMIA; ADOLESCENT; ADULT; APOPTOSIS; ARTICLE; CELL DIFFERENTIATION; CELL FUNCTION; CELL GROWTH; CELL LINEAGE; CELL STRUCTURE; CELL SURVIVAL; CHILD; CLINICAL ARTICLE; COCULTURE; CONTROLLED STUDY; CYTOKINE PRODUCTION; FEMALE; GENE MUTATION; HEMATOPOIETIC STEM CELL; HUMAN; HUMAN CELL; KARYOTYPE; LYMPHOCYTE PROLIFERATION; MALE; MESENCHYMAL STEM CELL; MICROENVIRONMENT; MITOSIS INHIBITION; MYELODYSPLASTIC SYNDROME; NEUTROPHIL; PROTEIN EXPRESSION; SHWACHMAN SYNDROME;

EID: 84871067796     PISSN: None     EISSN: 20445385     Source Type: Journal    
DOI: 10.1038/bcj.2012.40     Document Type: Article

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