Acquired hemophilia a associated with IgG4-related lung disease in a patient with autoimmune pancreatitis

Internal Medicine

Volumn 51, Issue 22, 2012, Pages 3151-3154

  Sugino, Keishi ^a   Gocho, Kyoko ^a   Ishida, Fumiaki ^a   Kikuchi, Naoshi ^a   Hirota, Nao ^a   Sato, Keita ^a   Sano, Go ^a   Isobe, Kazutoshi ^a   Sakamoto, Susumu ^a   Takai, Yujiro ^a   Hata, Yoshinobu ^a   Shibuya, Kazutoshi ^a   Uekusa, Toshimasa ^b   Kurosaki, Atsuko ^c   Homma, Sakae ^a  

^a TOHO UNIVERSITY OMORI MEDICAL CENTER   (Japan)

^b KANTO ROSAI HOSPITAL   (Japan)

^c TORANOMON HOSPITAL   (Japan)

Author keywords

Acquired hemophilia A; Autoimmune pancreatitis; IgG4 related disease; IgG4 related lung disease

Indexed keywords

BLOOD CLOTTING FACTOR 8; IMMUNOGLOBULIN E; IMMUNOGLOBULIN G; IMMUNOGLOBULIN G4; PREDNISOLONE; RECOMBINANT BLOOD CLOTTING FACTOR 7A;

AGED; ANEMIA; ARTERITIS; ARTICLE; AUTOIMMUNE PANCREATITIS; CASE REPORT; CELL INFILTRATION; COMPUTER ASSISTED TOMOGRAPHY; CORTICOSTEROID THERAPY; DISEASE ASSOCIATION; DRUG DOSE REDUCTION; FIBROSIS; HEMATOMA; HEMOPHILIA A; HUMAN; HUMAN TISSUE; IMMUNOGLOBULIN G4 RELATED LUNG DISEASE; IMMUNOHISTOCHEMISTRY; INFLAMMATION; LIMB SWELLING; LUNG BIOPSY; LUNG DISEASE; MALE; MULTIPLE PULMONARY NODULES; PHLEBITIS; PROTEIN BLOOD LEVEL; PROTHROMBIN TIME; THORAX RADIOGRAPHY; VIDEO ASSISTED THORACOSCOPIC SURGERY;

AGED; AUTOIMMUNE DISEASES; HEMOPHILIA A; HUMANS; IMMUNOGLOBULIN G; LUNG DISEASES; MALE; PANCREATITIS; PARTIAL THROMBOPLASTIN TIME;

EID: 84869740915     PISSN: 09182918     EISSN: 13497235     Source Type: Journal    
DOI: 10.2169/internalmedicine.51.8133     Document Type: Article

References (8)

1. Hamano H, Kawa S, Horiuchi A, et al. High serum IgG4 concentrations in patients with sclerosing pancreatitis. N Engl J Med 344: 732-738, 2001.
2. Umehara H, Okazaki K, Masaki Y, et al. Comprehensive diagnostic criteria for IgG4-related disease (IgG4-RD), 2011. Mod Rheumatol 22: 21-30, 2012.
3. Zen Y, Fujii T, Harada K, et al. Th2 and regulatory immune reactions are increased in immunoglobulin G4-related sclerosing pancreatitis and cholangitis. Hepatology 45: 1538-1546, 2007.
4. Kessler CM. Acquired factor VIII autoantibody inhibitors: current concepts and potential therapeutic strategies for the future. Haematologica 85: 57-61, 2000.
5. Boggio LN, Green D. Acquired hemophilia. Rev Clin Exp Hematol 5: 389-404, 2001.
6. Matsumoto T, Shima M, Fukuda K, et al. Immunological characterization of factor VIII autoantibodies in patients with acquired hemophilia A in the presence or absence of underlying disease. Thromb Res 104: 381-388, 2001.
7. Saeki T, Ito T, Youkou A, et al. Thrombotic thrombocytopenic purpura in IgG4-related disease with severe deficiency of ADAMTS-13 activity and IgG4 autoantibody against ADAMTS-Arthritis Care Res 63: 1209-1212, 2011.
8. Astermark J, Oldenburg J, Pavlova A, Berntorp E, Lefvert AK. Polymorphisms in the IL10 but not in the IL1beta and IL4 genes are associated with inhibitor development in patients with hemophilia A. Blood 107: 3167-3172, 2006.