Thrombotic thrombocytopenic purpura in IgG4-related disease with severe deficiency of ADAMTS-13 activity and IgG4 autoantibody against ADAMTS-13

Arthritis Care and Research

Volumn 63, Issue 8, 2011, Pages 1209-1212

  Saeki, Takako ^a   Ito, Tomoyuki ^a   Youkou, Akira ^b   Ishiguro, Hajime ^a   Sato, Naoko ^a   Yamazaki, Hajime ^a   Koike, Tadashi ^a   Kourakata, Hiroyo ^c   Ferrari, Silvia ^d   Scheiflinger, Friedrich ^d   Narita, Ichiei ^b  

^a NAGAOKA RED CROSS HOSPITAL   (Japan)

^b NIIGATA UNIVERSITY GRADUATE SCHOOL OF MEDICAL AND DENTAL SCIENCES   (Japan)

^c Saiseikai Sanjo Hospital   (Japan)

^d Baxter Innovations   (Austria)

Author keywords

[No Author keywords available]

Indexed keywords

AUTOANTIBODY; BILIRUBIN; D DIMER; ENZYME ANTIBODY; FERRITIN; IMMUNOGLOBULIN G; IMMUNOGLOBULIN G ANTIBODY; IMMUNOGLOBULIN G4; IMMUNOGLOBULIN G4 AUTOANTIBODY; LACTATE DEHYDROGENASE; PREDNISOLONE; SOLUBLE INTERLEUKIN 2 RECEPTOR; UNCLASSIFIED DRUG; VON WILLEBRAND FACTOR CLEAVING PROTEINASE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE ANTIBODY;

ADULT; ANEMIA; ANTIBODY TITER; ARTICLE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; DIAGNOSTIC VALUE; DISEASE SEVERITY; DRUG DOSE REDUCTION; ENZYME ACTIVITY; ENZYME DEFICIENCY; HEMOGLOBIN BLOOD LEVEL; HUMAN; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN G4 RELATED LUNG DISEASE; IMMUNOHISTOCHEMISTRY; LEUKOCYTE COUNT; LUNG DISEASE; MALE; PETECHIA; STEROID THERAPY; THROMBOCYTE COUNT; THROMBOTIC THROMBOCYTOPENIC PURPURA; TREATMENT RESPONSE;

ADAM PROTEINS; AUTOANTIBODIES; AUTOIMMUNE DISEASES; HUMANS; IMMUNOGLOBULIN G; MALE; MIDDLE AGED; PURPURA, THROMBOTIC THROMBOCYTOPENIC; SEVERITY OF ILLNESS INDEX; TREATMENT OUTCOME;

EID: 84860389606     PISSN: 21514658     EISSN: 15290131     Source Type: Journal    
DOI: 10.1002/acr.20484     Document Type: Article

References (14)

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