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Volumn 156, Issue 1, 1997, Pages

Dietary treatment in late-onset acid maltase deficiency

Author keywords

Acid maltase deficiency; Alanine; Diet; Glycogen storage disease; Stable isotope

Indexed keywords

ALANINE; CARBON 13; GLUCAN 1,4 ALPHA GLUCOSIDASE; GLUCOSE; ISOTOPE; LEUCINE;

EID: 0030759860     PISSN: 09439676     EISSN: None     Source Type: Journal    
DOI: 10.1007/pl00014270     Document Type: Article
Times cited : (23)

References (9)
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    • Protein, glucose kinetics in juvenile and adult patients with Glycogen Storage Disease Type II
    • Bodamer OAF, Leonard JV, Halliday D (1995) Protein, glucose kinetics in juvenile and adult patients with Glycogen Storage Disease Type II. Monatsschr Kinderheilkd 143:909
    • (1995) Monatsschr Kinderheilkd , vol.143 , pp. 909
    • Bodamer, O.A.F.1    Leonard, J.V.2    Halliday, D.3
  • 3
    • 24044549553 scopus 로고
    • Biochemical aspect of glycogen deposition disease
    • Cori GT (1957) Biochemical aspect of glycogen deposition disease. Mod Probl Paediatr 3:344-358
    • (1957) Mod Probl Paediatr , vol.3 , pp. 344-358
    • Cori, G.T.1
  • 6
    • 0001448360 scopus 로고
    • Glycogen storage disease type II: Acid α-glucosidase (acid maltase) deficiency
    • Scriver CR, Beaudet AL, Sly WS, Valle D (eds) McGraw Hill, New York
    • Hirschhorn R (1995) Glycogen storage disease type II: acid α-glucosidase (acid maltase) deficiency. In: Scriver CR, Beaudet AL, Sly WS, Valle D (eds) The metabolic and molecular bases of inherited disease, vol. II. McGraw Hill, New York, pp 2443-2464
    • (1995) The Metabolic and Molecular Bases of Inherited Disease , vol.2 , pp. 2443-2464
    • Hirschhorn, R.1
  • 7
    • 0022446103 scopus 로고
    • Acid maltase deficiency: A case study and review of the pathophysiological changes and proposed therapeutic measures
    • Isaacs H, Savage N, Badenhorst M, Whistler T (1986) Acid maltase deficiency: a case study and review of the pathophysiological changes and proposed therapeutic measures. J Neurol Neurosurg Psychiatry 49:1011-1018
    • (1986) J Neurol Neurosurg Psychiatry , vol.49 , pp. 1011-1018
    • Isaacs, H.1    Savage, N.2    Badenhorst, M.3    Whistler, T.4
  • 8
    • 0027515831 scopus 로고
    • In vivo measurement of changes in body composition: Description of methods and their validation against 12-d continuous whole body calorimetry
    • Jebb SA, Murgatroyd PR, Goldberg GR, Prentice AM, Coward WA (1993) In vivo measurement of changes in body composition: description of methods and their validation against 12-d continuous whole body calorimetry. Am J Clin Nutr 58(4): 455-462
    • (1993) Am J Clin Nutr , vol.58 , Issue.4 , pp. 455-462
    • Jebb, S.A.1    Murgatroyd, P.R.2    Goldberg, G.R.3    Prentice, A.M.4    Coward, W.A.5
  • 9
    • 0022456674 scopus 로고
    • Acid maltase deficiency in an adult. Evidence for improvement in respiratory function with high-protein dietary therapy
    • Margolis ML, Hill AR (1986) Acid maltase deficiency in an adult. Evidence for improvement in respiratory function with high-protein dietary therapy. Am Rev Respir Dis 143(2): 328-331
    • (1986) Am Rev Respir Dis , vol.143 , Issue.2 , pp. 328-331
    • Margolis, M.L.1    Hill, A.R.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.